I-scleromalacia perforans yisimo esibucayi esibangelwa ukulahlekelwa umbono. I-scleromalacia perforans, eyaziwa nangokuthi i-necrotizing scleritis, yiyona ndlela enzima kakhulu ye-scleritis, ngezinye izikhathi eholela ekulahlekelweni kweso. Isimo ngokuvamile sihlotshaniswa nesifo sesistimu nokubandakanyeka kwezitho eziningi.
I-scleromalacia perforans ibonakaliswa ukucwiliswa okukhulu kwe-sclera yeso futhi ingahlukaniswa ngezigaba ezimbili, ngokuvuvukala ngaphandle kokuvuvukala.
Lolu hlobo lwe-scleritis luvame ukuhlotshaniswa nesifo samathambo esibi kakhulu.
Futhi eyaziwa njenge: Necrotizing scleritis
Kuyini i-Scleritis?
I-scleritis i-inflammation ye-sclera, isembozo sangaphandle esimhlophe saso. Imikhumbi yegazi ihamba ngaphesheya kwe-sclera futhi ingabandakanyeka ku-scleritis. I-scleritis ingaba yingozi emehlweni, okwenza ubuhlungu obukhulu nokulahlekelwa umbono kwabanye abantu. Nakuba i-scleritis ingase ibhekane nokuhlukunyezwa noma ukutheleleka, izimo eziningi ze-scleritis zihlotshaniswa nesifo esiyisisekelo se-system ezifana nesifo se-rheumatoid , i-ankylosing spondylitis, i-systemic lupus erythematosus, i-polyarteritis nodosa, i-granulomatosis ka-Wegener, i-herpes zoster virus, i-gout kanye ne-syphilis. Lezi zimo zenza ukuvuvukala okuvamile kuwo wonke umzimba.
Izinhlobo
I-Anterior scleritis , uhlobo oluvame kakhulu, luthinta ingxenye yangaphambili ye-sclera. Kunezinhlobo ezintathu ze-anterior scleritis:
- Ukusabalalisa i-scleritis yilona uhlobo oluvame kakhulu futhi lungaphathwa kalula. Lolu hlobo lubonisa ukubomvu okujwayelekile nokuvuvukala engxenyeni engaphambili yesklamu.
- I-sculitis ye-Nodular ine-nodules noma ama-bumps okuvame ukubhebhethekisa ukuthinta, ebusweni beso.
- I-Necrotizing scleritis (ebizwa nangokuthi i-scleromalcia perforans) iyindlela enzima kunazo zonke ye-anterior scleritis.
I-posterior scleritis yifomu engavamile kakhulu. Ithinta ingxenye yangasese yeso futhi ngokuvamile ayihlotshaniswa nesifo esibucayi sesistimu. Leli fomu lingabangela izinkinga ezifana ne-retinal detachment kanye ne-angle-closure glaucoma.
I-scleromalcia perforans ilandisa kuphela ngo-4% we-scleritis. Abantu ababhekene ne-scleromalcia perforans banezinhlungu ezinkulu. Ubuhlungu bukhulu kakhulu kunalokho iso elibonakalayo.
Izimpawu Nezibonakaliso
- ubomvu
- i-chemosis (ukuvuvukala okuhlangene)
- ijwabu leso livuvuka
- i-proptosis (iso eliphuma ngaphandle)
- Umbono wehlile
Ngaphezu kwalokho, odokotela bangabona:
- amafolda e-choroidal
- ukuphakama kwe-retinal
- ukuvuvukala kwe-optic disc
- ukuvuvukala kwe-macular
- amasosha wokutakula
Izinkinga
- Ukulahleka kombono
- Inani elikhulu njenge-astigmatism
- Anterior uveitis
- I-Cataract
- I-glaucoma
- I-globe perforation
Inkinga enkulu kunazo zonke ye-scleromalcia perforans iwuphawu lwe-globe iso. Uma lokhu kwenzeka, ungakwazi ngempela ukubona ngesikhala, ingxenye emhlophe yeso, futhi ubone izicubu ngaphansi. Uma kwenzeka lokhu, ukufakelwa kwe-scleral kuzobekwa ngokuqondile ku-sclera. Uhlobo lwesisindo esisetshenziselwa ukuhlanganiswa lungaba izicubu zokunikela. Kulesi simo, isiguli singase sidinge izidakamizwa ukuvimbela amasosha omzimba ukuvimbela ukwenqaba izicubu.
Ukwelashwa kwe-scleritis uma ufika kuleli phuzu kuyinselele. Odokotela abaningi bazozama i-steroids kanye nezidakamizwa ezingekho-steroidal ezilwa nokuvuvukala, kodwa kubonakala zingasebenzi kahle. Izidakamizwa ezikhethekile ze-immuno-modulatory zibonise isithembiso esithile.