I-syndrome eyaziwa njenge-posterior leukoencephalopathy syndrome, noma i-RPLS, isimo esingajwayelekile, esinjengobuhlungu esibangelwa ukuvuvukala ebuchosheni. I-leukoencephalopathy yangemva kokubuyela emuva ejwayelekile ihlotshaniswa nesiqephu somfutho wegazi ophezulu kakhulu . Noma kunjalo, i-syndrome ingase ikhule ngendlela engalindelekile ngaphambi kokuba ixazulule. Futhi, ngoba akukaze kuqinisekiswe ukuthi isigameko noma isiqephu esifana nesifo sokushaya isisu sizogcina sigcine, kubalulekile ukuthola usizo lwezokwelapha izimpawu zezinzwa.
Uma utshelwe ukuthi wena noma othandekayo uye waba nesifo se-leukoencephalopathy posterior, ungase ube nemibuzo embalwa ngakho.
Enye yezimpawu ze-RPLS yukuthi iguqulwa, okusho ukuthi lesi simo sesikhashana nokuthi izimpawu zayo kanye nokutholakala kwe-MRI kuphelile. Izifunda zobuchopho ezithintekayo yi-syndrome zikhona ngemuva kwengqondo. I-Leukoencephalopathy ichazwa njenge-clouding of consciousness, ukudideka, noma isimo sengqondo esishintshile ngenxa yesimo esithinta isifunda esikhulu sobuchopho. Endabeni ye-RPLS, yindaba emhlophe yobuchopho engathinteka kakhulu. Lesi simo yisifo. I-syndrome yinkimbinkimbi yezibonakaliso zesifo esivame ukuhlangana ndawonye noma nini lapho lesi sifo siphelela noma 'senza okuthile.'
I-RPLS iyisifo lapho isiqephu segazi eliphezulu senza ukuvuvukala okubuyiselwayo emlandweni omhlophe wezindawo zangasese zobuchopho, ngaleyo ndlela kuholela esimweni sengqondo esishintsha isikhathi eside.
Ukungafani kwe-RPLS
Njengoba kuvela, izimpawu ezibhekwe nalesi simo azicaci ngokucacile njengoba isichazamazwi saso sisho ukuthi, njengoba i-RPLS iboniswe ukuthi ibangele izimpawu ezihlukahlukene, zonke zazo zibe nobukhulu obukhulu bokuqina, nobude besikhathi. Okuvamile kakhulu kulawa, njengoba kubikwe ucwaningo oluthile, kufaka ukuhlukunyezwa kwe-encephalopathy (92%) (87%), ikhanda (54%) nezinkinga ezibukwayo (39%).
Kodwa akuzona zonke izimo ze-RPLS eziguqulwayo, ezihamba phambili, noma ezihlobene nokuvuvukala emcimbini omhlophe. Ngakho-ke cishe noma iyiphi indawo yobuchopho ingathinteka yi-RPLS, futhi ezinye izimpawu zesifo zingase zikhona.
Ukuxilongwa
Ukuxilongwa kwe-RPLS kwenziwa ngokusebenzisa ukunakekelwa ngokucophelela kwezokwelapha okuhlanganisa umlando oqaphele wezimpawu ezitholwa isiguli, ukuhlolwa kwegazi ngokomzimba, i-MRI yobuchopho, nokuba khona kwengcindezi ephakeme yegazi nxazonke zomcimbi. Kodwa-ke, ucwaningo olwenziwe ucwaningo lubonisa ukuthi abanye abantu bangase bahlushwa yi-RPLS lapho kukhona umfutho wegazi ovamile. Lokhu kungase kwenzeke esimweni esibizwa ngokuthi i-eclampsia, okuvame ukuhlotshaniswa nokukhulelwa kwesikhathi noma ukubeletha nokubeletha. I-encephalopathy ne-leukoencephalopathy nayo ingenzeka kubantu abasebenzisa imithi ethile.
Ngokuvamile, i-MRI yobuchopho beziguli ezine-RPLS ibonisa ukubukeka kwezindaba ezimhlophe zesifunda esilandelayo sobuchopho kuzo zombili izinhlangothi ezingakwesokunxele nangakwesokudla. Kodwa-ke, kwezinye izimo, i-RPLS ingafaka izindawo eziphambi kobuchopho noma ezinye izifunda zobuchopho, futhi zingase zibandakanye nodaba oluyimpunga. Ngaphezu kwalokho, amacala amaningi e-RPLS ashiye abasindile ngokulimala okungapheli kobuchopho, nakuba ezimweni eziningi isinqumo sokuvuvukala senzeka.
Ukuthuthukiswa kungagcinwa ngokujwayelekile nge-MRI yokulandela ubuchopho.
Ukwelapha
Ukwelashwa kwe-RPLS kubhekene nokugxila ngokuqinile ukucindezela kwegazi kanye namazinga asemzimbeni emzimbeni. Ukwengeza, ukuvimbela nokwelapha ukuhlukunyezwa kuyisici esibalulekile ekulawuleni okunzima kwalesi simo. Ukubheka izimpawu ezinjengezinsizwa kuyisici esibalulekile ekunqumeni izinguquko eziphuthumayo esimweni.
Isibikezelo
Ngokujwayelekile, izimpawu zixazulula ezinsukwini ezimbalwa kuya kwamasonto emva kokuqala kokuqala kwe-RPLS. Kodwa-ke, njengalawo wonke ama-episodes of stroke noma i-mini-stroke, kungenzeka ukuthi kube nezimpawu ezisele zokulimala komqondo.
Ihlelwe nguHeidi Moawad MD
Imithombo:
> Vivien H. Lee, MD; I-Eelco FM Wijdicks, MD; Edward M. Manno, MD; U-Alejandro A. Rabinstein, MD; I-Spectrum Clinic ye-Posterior Leukoencephalopathy Syndrome; Arch Neurol. 2008; 65 (2): 205-210.
> JP Mohr, uDennis W. Choi, uJames C. Grotta, uBryce Weir, uPhillip A. Wolf Stroke: Ukuguquka Kwamathambo, Ukuxilongwa, kanye Nokuphathwa Churchill Livingstone; Umagazini we-4 ( > 2004).