Isizathu Esincane Esingaziwa Sokulahlekelwa Ukuzwa
I-Mondini syndrome, eyaziwa nangokuthi i-Mondini dysplasia noma i-Mondini malformation, ichaza isimo lapho i-cochlea engaphelele khona, iphendukele eyodwa kuphela nengxenye esikhundleni sokuphenduka okujwayelekile okuphindwe kabili nengxenye. Lesi simo saqala ukuchazwa ngo-1791 udokotela uCarlo Mondini esihlokweni esithi "I-Anatomic Section of a Boy Born Deaf." Ukuhumusha okuvela kwisiLatini sokuqala salesi sihloko kwanyatheliswa ngo-1997.
Isihloko sokuqala sikaCarlo Mondini sine incazelo ecacile yenkinga ebizwa ngegama lakhe. Eminyakeni edlule, odokotela abathile baye basebenzisa leli gama ukuchaza ezinye izinto ezimbi ezingabonakali. Uma kuxoxwa ngezingqinamba ze-Mondini, kubalulekile ukuba ube nencazelo ecacile ye-cochlea nezinye izakhiwo zendlebe zangaphakathi njengoba igama elithi 'Mondini' lingase lidideke.
Izimbangela
Lokhu kuzalwa (okwamanje ekuzalweni) imbangela yokulahlekelwa kokuzwa. I-malini ye-Mondini iyenzeka uma kunokuphazanyiswa ekuthuthukiseni indlebe yangaphakathi phakathi nesonto lesikhombisa lokubeletha. Lokhu kungathinta okukodwa noma kokubili izindlebe futhi kungase kube yedwa noma kwenzeke nezinye izinkinga zezindlebe noma izinkinga. Ama-Syndromes aziwayo ukuthi ahlotshaniswa nokukhubazeka kwe-Mondini afaka i-Pendred Syndrome, i-DiGeorge Syndrome, i-Klippel Feil Syndrome, i-Fountain Syndrome, i-Wildervanck Syndrome, i-CHARGE syndrome, kanye nezinhlobo ezithile ze-chromosomal trisomies.
Kunezimo lapho ukukhubazeka kwe-Mondini kuxhunywe khona kumaphethini wefa le- autosomal elidumile futhi elizenzekelayo le- heritage kanye nokuthi kube yinto ehlukile.
Ukuxilongwa
Ukuxilongwa kwezimo ezimbi zeM Mondini kwenziwa ngezifundo ze-radiographic, njengezicabangela eziphezulu ze-CT zamathambo wesikhashana.
Ukuzwa Ukulahlekelwa Nokunakekelwa
Ukulahleka kokuzwa okuhambisana nokukhubazeka kwe-Mondini kungashintsha, nakuba ngokuvamile kuvamile. Kunconywa izinsiza zokuzwa lapho kunesisindo esanele sokuzwa ukuze kuzuze. Ezimweni lapho izinsiza zokuzwa zingasebenzi, ukufakelwa kwe-cochlear kwenziwe ngokuphumelelayo.
Okunye okucatshangwayo
Abantu abanokukhubazeka kwe-Mondini bangase babe engozini enkulu ye-meningitis. I-malformation ingase idale iphuzu lokungena elilula emzimbeni ozungeze ubuchopho nomgogodla. Ezimweni lapho kube khona iziqephu eziningi (noma eziphindaphindiwe) ze-meningitis, ukuhlinzwa ukuvala leli phuzu lokungena lingaboniswa.
I-Mondini malformation ingathinta futhi uhlelo lokulinganisela lwendlebe yangaphakathi. Izingane ezinokukhubazeka kwe-Mondini zingabonisa ukubambezeleka kokuthuthukiswa ekuthuthukiseni izimoto ngenxa yokunciphisa amavoti ebuchosheni kusukela ohlelweni lwabo lokulinganisela. Kwamanye amacala, izinkinga zokulinganisela zingase zingabonakali kuze kube umuntu omdala.
> Imithombo:
> Hain, T (2012). Mondini noMichel Izincazelo zezindlebe zangaphakathi. Ukuzivocavoca nokulinganisela.
> Bheka, W (1999). Iyini i-'Manini 'futhi Yenza Kanjani Ukuthi Igama Lenza Kanjani? I-American Journal ye-Neuroradiology.
> Mondini C. Minor imisebenzi kaCarlo > Mondini: > I-anatomic ingxenye yomfana ozelwe isithulu. Am J Otol 1997; 18: 288-293
> Mondini Dysplasia (2012). Ihhovisi Lezinkinga Zokugula Ezinzima.