I-angioid streaks yinkinga ye-retinal ebonakala ngamaphule futhi ephazamisa embhedeni kaBruch, ingqimba engezansi ye- retina esiza ukondla futhi ukondla ungqimba obuningi be-photoreceptor. Isibungu sikaBruch singasakaza, sibone futhi siqale ukuphahlazeka. Imifantu ibonakala njengemigqa enamandla, enombala noma emigqumeni ephuma endaweni eseduze nerve ye-optic. Lezi ziphuzo zingabangela izinkinga ezihambisana nezifo ezifana ne- macular degeneration .
Ubani Osemngciphekweni Wama-Angioid Streaks?
Nakuba izitshalo ze-angioid zingenzeka ngaphandle kwesizathu se-systemic, amacala amaningi ahlotshaniswa nezifo zesikhumba esikhulayo. Kuze kube ngamaphesenti angu-50 abantu abanesisindo se-angioid bane-pseudoxanthoma elasticum, isifo se-Paget noma i-Ehlers-Danolos syndrome.
- I-Pseudoxanthoma elasticum (i-PXE) yisifo lapho i-calcium namaminerali aqoqwa khona ngamafutha e-elastic. Lokhu kungathinta isikhumba, amehlo, uhlelo lwesifo senhliziyo, kanye nesimiso sesisu. Izindwangu ezithintekayo ziyingxenye yezicubu ezixhumeneyo ezihlinzeka ngokuvumelana nezimo namandla emzimbeni wethu.
- Isifo se-Paget yisimo esibonakala ukukhubazeka kwethambo okubangelwa ukuphazanyiswa kwindlela yokuvuselelwa kwamathambo futhi ithambo liqala ukushintshwa ngesilinganiso esisheshayo kunokujwayelekile. Amathoni angakhula futhi abuthakathaka.
- I-Ehlers-Danlos syndrome yisifo esingavamile sofuzo oluphathelene ne-collagen emzimbeni wethu. Abantu abane-Ehlers-Danlos bangabhekana nezinkinga ezihlukahlukene zamehlo kufaka phakathi i-keratoconus, i-myopia ephakeme, imishini yokubuyisela kabusha, ukuhlukaniswa kwe-lens kanye nezintambo ze-angioid.
Kungani I-Angioid Ihlasela Imbangela Ukulahlekelwa Kombono?
Uma ama-breaks akhona ezingxenyeni eziphansi ze-retinal, izendlalelo zingasakwazi ukondla kahle amaseli we-photoreceptor. Lokhu kubangela ukuvuza kwamanzi kanye nokuntuleka kwe-oxygen. Amanetha angama-neovascular (i-mesh emihle yemithambo yegazi kanye nezicubu ezinamafutha) bese uqala ifomu.
Lawa manetha angabangela ukubola kwegazi nokukhwabanisa okukhulu. Lokhu kwakheka kufana nalokho okwenzeka ngezinye izikhathi nge-degular degeneration. Ukulahleka kombono okuphawulekayo kungenzeka.
Ukwelapha
Ngeshwa, akunakwenzeka ukwenza izintambo ze-angioid zihambe. Ukuhlolwa kwamehlo wonyaka kufanele kwenziwe ngumculi we-optometrist noma ophthalmologist jikelele ukuze ahlole ukuthuthukiswa kwamanetha angama-neovascular kanye nezinye izimpawu ezihambisanayo. Uma kwenzeka, uzothunyelwa kuchwepheshe we-retinal ukwelashwa, okungase kuhilele ukusetshenziswa kwelaser ukuyeka ukuqhubeka. Ukukhishwa kokuhlinzwa kwamanetha we-neovascular kuyindlela yokukhetha ukwelapha, kanye nokwelashwa kwe-photodynamic. Ngezinye izikhathi amanetha we-neovascular azovuza amanzi noma igazi. Kulokhu, izidakamizwa ezintsha ezibizwa ngokuthi i-antivascular endothelial antibodies zisetshenzisiwe futhi zibonise impumelelo enkulu. Ezinye iziguli zingase ziphathwe ngezidakamizwa zokulwa nezidakamizwa ze-endothelial growth (VEGF) futhi zibuye zibonise imiphumela emihle. Lezi zidakamizwa zijojowe ngqo emehlweni. Nakuba lezi zidakamizwa ezintsha zisebenza kahle, zivame ukujova ngokuphindaphindiwe njengoba i-neovascularization ivame ukuphindaphinda iziguli ezinezintambo ze-angioid.
Okufanele Ukwazi Ngama-Angioid Streaks
Abantu abanezinyosi ze-angioid banamehlo aphephile, bawabeka engozini ephakeme yokuqhekeka kwama-choroidal kanye ne-subretinal hemorrhage uma behlushwa amehlo.
Ngakho-ke, ukuvikelwa kweso kuyimfuneko. Amalensi wePolycarbonate kufanele abekwe njengoba ayilona lezinto ezingamelana nethonya. Izigqoko ezikhethekile zokuphepha kufanele zigqoke ngesikhathi semidlalo yokuxhumana.
Umthombo:
U-Alexander, uLarry J. Ukunakekelwa Okuyinhloko Kwesigaba Esiphansi, Edition Yesibili. Appleton & Lange, 1994, iphe 300-301.