I-POEMS syndrome yinkinga yegazi ethinta izingxenye eziningi zomzimba futhi ibangela izimpawu eziningi. Lithinta kokubili amadoda nabesifazane futhi kuvame ukuqala ngemva kweminyaka yobudala engama-50, nakuba kungenzeka noma kunini. Ayaziwa ukuthi ingakanani i-POEMS syndrome eyenzekayo ngoba kunzima ukuyihlolisisa kahle. Isizathu asiziwa.
Izimpawu
Isichazamazwi se-POEMS simele:
- I-P - polyneuropathy, okusho izimpawu zesibindi njenge-numbness, ukulinganisa, kanye / noma ubuthakathaka bezandla nezinyawo
- O - i-organomegaly, okusho izitho ezikhulisiwe, ngokuvamile isibindi, i-spleen, noma i-lymph nodes. Amaphesenti angaba ngu-15 abantu abane-POEMS syndrome bane-Castleman isifo (i-lymph node disorder).
- E - endocrinopathy, okusho ukushintsha kokukhiqizwa kwehomoni. Izimpawu ezifana nesifo sikashukela , ukungabi namandla , ziyeke ukuhamba esikhathini ( amenorrhea ), amazinga aphansi wegciwane (hypothyroidism), kanye / noma ukuthuthukiswa kwebele kumadoda (gynecomastia) kungenzeka.
- I-M - i-gammopathy yama-monoclonal noma i-monoclonal plasma-disliferative disorder, kokubili okusho ukuthi amaseli we-protein angavamile egazi
- I-S - isikhumba sishintsha njengokwanda kwesikhumba sesikhumba (hyperpigmentation); ukwandisa izinwele zomzimba (hypertrichosis) ebusweni, emilenzeni nasesifuba; ukuqina kwesikhumba nokuqinisa, ukuvuvukala (i-edema) yemilenze nezinyawo, ukugcoba kwezipikili.
Abantu bangase bahlangane, ukukhathala, ama-aches kanye nezinhlungu ezijwayelekile, noma izinguquko embonweni, phakathi kwezinye izimpawu.
Ukuxilongwa
Ukuxilongwa kwe-POEMS syndrome kungenziwa ngokusekelwe kokuhlolwa kwesiguli kanye nomlando wakhe wezokwelapha. Izivivinyo zegazi ezifana nokubala okuphelele kwe-cell (CBC) kanye ne-serum proteinelectrophoresis zenziwa ukuze zibheke okungavamile, njengokuhlolwa komchamo. Izinga le-hormone ye-thyroid, amazinga e-blood glucose, namazinga e-estrogen egazini ahlolwe ukuze abone okungavamile.
I-bone marrow biopsy kanye / noma amathambo x-ray angenziwa ukuze kusize ekuxilongweni.
Umuntu ubhekwa ukuthi une-POEMS syndrome uma i- "P" (polyneuropathy) ne "M" (okungavamile amaprotheni egazi) ekhona kanye nezilonda ze-sclerotic (scarring) zesifo noma isifo se-Castleman. Abantu abaningi bazoba nezinye izimpawu ze-syndrome. Ngenxa yokuthi odokotela abaningi abajwayele ukuzwa i-POEMS syndrome, imiphumela engavamile yokuhlolwa kwegazi ngokuvamile iholela ekutheni i-myeloma eminingi ingabonakali kahle, noma izimpawu ze-polyneuropathy ziholela ekutheni i-diagnosis ye-polyneuropathy engavumelani nokudumala (CIDP) engapheli.
Ukwelapha
Ukwelashwa kwe-POEMS syndrome kuncike ekwelapheni kwesifo esiyingqayizivele se-cell cell. Iningi labantu lithola inhlanganisela yokwelapha okufana nalokhu:
- Ukwelashwa kwamafutha
- Imithi ye-corticosteroid njenge-prednisone
- I-Chemotherapy
- I-hormone esikhundleni samahomoni aphansi kakhulu
- Ukwelapha ngokomzimba
- Ukufakelwa kwe-bone marrow
Ochwepheshe njenge-neurologist (udokotela wesistimu wesifo), udokotela wegazi (udokotela wegazi), udokotela wezidakamizwa (udokotela wesikhumba), kanye ne-endocrinologist (udokotela we-hormone gland) ngokuvamile bahilelekile ekunakekeleni umuntu one-POEMS syndrome.
Imithombo:
Dispenzieri, Angela. "I-POEMS Syndrome." I-Hematology 2005 (2005): 360-367.
I-Dispenzieri, u-Angela, uRobert A. Kyle, uMartin Q. uLacy, uS. S. Vincent Rajkumar, uTerry M. Therneau, uDirk R. Larson, uFilip R. Greipp, uThomas E. Witzig, uRita Basu, uGuillermo A. Suarez, uRafael Fonseca, John A. Lust, & Morie A. Gertz. "I-POEMS syndrome: izincazelo nomphumela wesikhathi eside." I-Blood 101 (2003): 2496-2506.
"Izimpawu ze-POEMS Syndrome." Ukwelashwa kwe-POEMS Syndrome eMtholampilo yaseMayo. I-Mayo Clinic. 22 Meyi 2007
Chan, Joanna, & Wingfield Rehmus. "I-POEMS Syndrome." eMedicine. 15 Dec 2006. WebMD. 22 Meyi 2007