I-Antiphospholipid syndrome (APS), eyaziwa nangokuthi 'igazi elinamathele,' liyisifo esizimele-umphumela wesistimu omzimba ukuguqula umzimba futhi ukuwuhlasela ngephutha. Endabeni ye-APS, umzimba wenza ama-antibodies abe amaprotheni ayo egazi.
I-Antiphospholipid syndrome ingenzeka kubantu abangenazo izifo ezihambisanayo. Lokhu kubizwa ngokuthi i-APS eyinhloko.
Lesi sifo singase senzeke ne- systemic lupus erythematosus (SLE) noma esinye isifo esizimele. Lokhu kubizwa ngokuthi i-APS yesibili.
Yeka ukuthi i-antiphospholipid syndrome kaningi kangakanani engakaziwa. Ama-anti-anti-APS angatholakala kubantu abaningi abangaba ngu-50% abane-lupus futhi ngo-1% kuya ku-5% wabantu bonke. I-Antiphospholipid syndrome ngokuvamile ivela encane kubantu abadala asebekhulile, kodwa ingaqala nganoma yisiphi isikhathi.
Izimpawu
Kanye nama-antibodies, umzimba uqala ukukhiqiza ama-blood clots. Ama-clots egazi angavimbela i-arteries kanye nemithanjeni, inqume ukunikezwa kwegazi engxenyeni yomzimba. Izimpawu okuhlangenwe nakho ngabanye zivela endaweni (s) kanye nemiphumela yezindwangu zegazi :
- Imifino noma imithanguzo yezingalo noma imilenze - Izembatho zingabangela ubuhlungu, ukuvuvukala, ukungafihli, ukumboza ezandleni noma ezinyaweni, noma emlenzeni ulonda. Uma ukunikezwa kwegazi kwaqedwa ngokuphelele kunxenye ethile, njengezwane, umuntu angase alahlekelwe yizwane.
- Imishanguzo yenhliziyo - Izingubo zingabangela ubuhlungu besifuba noma ukuhlasela kwenhliziyo . Umuntu angase abe nezinkinga zenhliziyo noma izinkinga zenhliziyo.
- Imikhumbi yegazi yesikhumba - Ama-clots angabangela izivunguvungu ( purpura ) noma i-blotchy, i-rash purplish ebizwa ngokuthi i-liveo reticularis.
- Imikhumbi yegazi ebuchosheni - I-clot eyanquma ukunikezwa kwegazi engxenyeni yobuchopho ibangela isifo . Umuntu onama-APS angase ahlangane nesifo sekhanda noma i- seizures .
- I-placenta ngesikhathi sokukhulelwa - Abesifazane abane-APS bangase babe nokulahlekelwa okungajwayelekile noma ukubeletha ngaphambi kwesikhathi.
Ifomu elibi kakhulu le-antiphospholipid syndrome, elibizwa ngokuthi i-APS eliyingozi, livela lapho izitho eziningi zangaphakathi zakha ama-clots wegazi esikhathini esiyizinsuku kuya kwamasonto.
Ukuxilongwa
Ukuxilongwa kwe-antiphospholipid syndrome kuncike ekuboniseni izimpawu nezibonakaliso, kanye nokuhlolwa kwama-laboratory. Uma umuntu eye enezigxobo zegazi emilenzeni ngaphandle kwanoma yimuphi omunye umphumela, isibonelo, i-APS ingase ibeke icala. Ukuhlolwa kwegazi kuma-anticardiolipin antibodies kungasiza ukuqinisekisa ukuxilongwa. Okunye imiphumela engavamile yokuhlolwa, njengamaplatelet wehla noma i- anemia , angase abe khona. Ukuskena kwe-computed tomography (CT) noma i-imagination magnetic resonance (MRI) ingaqinisekisa ukuthi kukhona ama-blood clots.
Ukwelapha
Ukwelashwa kwe-antiphospholipid syndrome kusekelwe ezimpawu zomuntu. I-APS enhlekelele idinga ukunakekelwa esibhedlela. Abanye abantu abanezinhlamvu zomzimba kodwa azikho izimpawu ze-APS zingase ziqalwe nge-aspirin yesilinganiso esiphansi nsuku zonke ukuze kusize ukunciphisa ingozi yezindwangu zegazi. Uma kutholakala i-clot yegazi, umuntu uqaliswa ngemithi ye-anticoagulant njenge-Coumadin (warfarin) noma i-Lovenox (enoxaparin).
Ngemithi kanye nokuguqula indlela yokuphila (njengokugwema isikhathi eside sokungasebenzi lapho ama-clots angakha khona emilenzeni), abantu abaningi abane-primary antiphospholipid syndrome bangadala impilo ejwayelekile, enempilo.
Labo abane-APS yesibili bangase babe nezinkinga ezengeziwe ngenxa yezimo zabo ezingezansi noma ezizimele.
Umthombo:
"Antiphospholipid Antibody Syndrome." Ama-Info Info. 15 Okthoba 2006. I-APS Foundation of America.