Uhlobo Lwe-Arthritis Nefomu Ye-Vasculitis Eyisistimu
Isifo se-Kawasaki singenye yezinhlobo ezingaphezu kuka-100 ze-arthritis, ngokwe-Arthritis Foundation. Isifo se-Kawasaki siyindlela ye-vasculitis ehlelekile eyenziwa ezinganeni ezincane; I-80% yeziguli ze-Kawasaki zingaphansi kweminyaka emihlanu ubudala.
UTomasaku Kawasaki okokuqala wabona lesi sifo ngo-1967 eJapane. Ngaphambi kokuqokwa njengesifo se-Kawasaki, lesi simo saziwa ngokuthi i-lymph node syndrome.
Kubizwa nangokuthi isifo sikaKawasaki, i-Kawasaki's syndrome kanye ne-infantile polyarteritis.
Izimpawu
Isifo se-Kawasaki singase sihlotshaniswe nokuthuthukiswa kwe-arteritis ye-coronary (ukuvuvukala kwemithambo ye-coronary) nokubunjwa kwe-aneurysms. E-United States, isifo se-Kawasaki kubhekwa njengesizathu esiyinhloko sesifo senhliziyo esitholakalayo ezinganeni.
Isifo se-Kawasaki siphuthuma ngokushesha futhi siqhuba inkambo enobudlova esikhathini esingamasonto. Ngokujwayelekile, lesi simo sixazulula. Yize noma kunjalo, kunquma ukuthi kungaba nezinkinga zenhliziyo eminyakeni edlule.
Ezinye izimpawu ezihambisana nezifo ze-Kawasaki zihlanganisa:
- ama-spiking fever ahlala ezinsukwini eziyisihlanu noma ngaphezulu (okudingekayo ukuxilongwa nge-Kawasaki Disease)
- I-conjunctiva evulekile (amehlo) ngaphandle kwe-pus
- izindebe ezinobomvu obomvu
- izibomvu zamangqamuzana abomvu emlonyeni
- ulimi olubomvu olune-strawberry
- ihamba ngesiqu somzimba
- izandla ezibomvu zezandla nezinyawo ezibomvu ezinyaweni
- i-edema yezandla nezinyawo
- ukudweba isikhumba ezandleni, ezinyaweni nasezifweni zobulili
- isifo se-lymph node ngokuvamile esiseduze nentamo
- ubuhlungu obuhlangene nokuvuvukala kaningi emaceleni omabili omzimba
Okunye okutholakele okungavamile okungenzeka ngezifo ze-Kawasaki kuhlanganisa i-aseptic meningitis, i- pyuria oyinyumba kanye ne-urethritis, isifo sohudo, ubuhlungu besisu, ubuhlungu besisu, i- pericardial effusion , i-jaundice obstructive, nama-hydrops we-gallbladder.
Isizathu
Abanye abasolwa banezifo ezithathelwanayo zesifo seKawasaki, kodwa akukho okuye kwafakazelwa. Kunezinhlobo eziningana zokungalingani kwe-immunologic ezihlobene nesifo se-Kawasaki, kanti abanye bakholelwa ukuthi yisimo sokuzimela .
Ukuvama
E-United States, isifo se-Kawasaki sithinta izingane ezingu-4 000 unyaka ngamunye. Liyanda kakhulu eJapane lapho litholakala khona ngamacala angu-5 000 kuya ku-6 000 unyaka ngamunye.
Ukwelapha
Uma lesi sifo sitholakale, ukwelashwa okusheshayo kunconywa ukuze umonakalo emithanjeni ye-coronary nenhliziyo ingavinjelwa. I-immune globulin (IVIG) engenakulinganiswa ehlinzekwa ngamanani aphezulu kubhekwa ukwelashwa okuvamile kwe-Kawasaki isifo. I- aspirin ye -High-dose iyingxenye yehlelo lokulashwa kanye. I-glucocorticoids ayisetshenziselwa ukuphatha isifo se-Kawasaki.
Ngenkathi yokwelashwa kwasekuseni ye-Kawasaki isifo, kungenzeka ukuthi iningi likwazi ukululama ngokuphelele, kepha iziguli ze-Kawasaki ezi-2% zifa ngenxa yezimo ze-coronary artery inflammation. Kunconywa ukuthi iziguli ezinezifo ze-Kawasaki zine-EKG (echocardiogram) njalo eminyakeni emibili noma emibili ukuhlola izinkinga zenhliziyo ezisele.
Imithombo:
Vasculitides. Izifo Kawasaki (Isahluko 21). I-Primer kuma-Rheumatic Diseases . Edition 13. Ishicilelwe yi-Arthritis Foundation. Klippel J. et al.
Akukona nje Ukukhula Okubuhlungu . Isifo Se-Kawasaki Isahluko 17. Thomas JA Lehman, MD. I-Oxford University Press. 2004.
Isifo Se-Kawasaki. I-MedlinePlus. I-NLM ne-NIH. 11/29/2006.