I-Epithelial basement membrane dystrophy (EBMD), eyaziwa nangokuthi isifo se-embroideni esingaphansi kwesifo sangasese noma i-map-dot-fingerprint dystrophy, isimo esivamile esithinta ingxenye yangaphakathi yeso. Isimo ngokuvamile sithinta abantu abangaphezu kweminyaka engu-30 ubudala. Ngezinye izikhathi i-EBMD iyathula, ishiya labo abathintekayo ukuthi abazi isimo sabo. Abanye abantu abanesifo banokucasuka okungaqondakali okwesikhashana lapho abanye bengase babe nezibonakaliso ezingapheli ezibonakala zisebenza nsuku zonke.
Ukuqonda i-EBMD
I-EBMD yinkinga yamaseli e-basal epithelial asezindaweni zangaphambili ze-cornea. Lawa maseli ase-basal anamathele kwesigcawu sesibili se-membrane, esabizwa nangokuthi ungqimba lukaBowman. Ku-EBMD, amangqamuzana ase-basal enza izilinganiso ezingavamile ezinomunwe eziphuma ngaphandle kwekhanda elifakwe ngaphansi. Lezi zilinganiso zibangela ukuthi amangqamuzana e-epithelial alahleke futhi anganamatheli ngisho nasendlini. Kanye nezinye izinguquko ezenzeka phakathi kwamaseli e-epithelial, lezi zinguquko ziveza amabalazwe, amachashazi, nezinyathelo zeminwe ngaphakathi kwe-cornea. Lezi zinguquko zemizimba zingabonakala ngokusetshenziswa kwe- biomicroscope lamathambo okubamba .
Izimpawu ze-EBMD
Abantu abane-EBMD bangase bakhononde ngalezi zimpawu ezilandelayo:
- Umbono wokushintshashintsha
- Umbono ophundlekile
- Ubuhlungu obungapheli
Abantu abaningi abathintekayo yi-EBMD banemibono eguqukayo ngaphandle kokungakhululeki. Noma kunjalo, amaphesenti angaba ngu-10 aneziqephu ezibuhlungu zokuguguleka komzimba okuqhubekayo.
Izimo ezivame ukuqhutshwa komzimba ziyiziphene ezincane ebusweni be-cornea ezenzeka ngezikhathi ezithile. Lezi ziphutha ziyizingxenye zama cell epithelial alahlekile awela kalula ngenxa yesifo. Lawa maseli alahlekile ngenxa yezilinganiso ezifana nomunwe ezenzayo, ezibangela ukuba zilahlekelwe ukunamathela kumbundu wesisekelo.
Izimpawu zivame ukuba zimbi nakakhulu lapho zivusa noma ngesikhathi sokusa ngoba ilanga limila ebusuku futhi amangqamuzana angabambeki kahle abonakala evele kalula.
Ukuxilongwa kwe-EBMD
I-EBMD ivame ukuphuthelwa odokotela njengebalazwe elimhlophe, ichashaza, nokubukeka komunwe okuvame ukukhula nesimo kungaba yisimo esibucayi ezimweni eziningi. Noma kunjalo, ekuhlolisweni okusheshayo, lezi zinguquko zokuziphatha zingatholakala. Odokotela bezilanga bazolalela ngokucophelela izimpawu zakho kanye nomlando jikelele wezokwelapha ongabanika izinkomba. Idayi ekhethekile ephuzi ingase ibekwe esweni lakho ukwenza izinguquko ezicashile ezibonakalayo ezibonakalayo ngaphezulu. Odokotela bangase benze ne-keratometry noma i- corneal topography esilinganisa isimo somumo we-cornea. Ifilimu yakho yezinyembezi izophinde iphindwe ngaphansi kwe-microscope ukulawula ezinye izimo ezifana ne-keratoconjunctivitis sicca nezinye izimo zamehlo ezomile ezomile.
Ukwelashwa kwe-EBMD
Ukwelashwa kwe-EBMD kubantu abangenayo izimpawu ezibonakalayo kufaka phakathi ukusebenzisa izinyembezi zokufakelwa izikhathi eziningana ngosuku ukugqugquzela impilo enhle ye-cell epithelial. Abantu abanezimpawu ezibonakalayo bazokwaziswa ukuthi basebenzise njalo izinyembezi zokufakelwa, kanye namafutha okugcoba amehlo ngaphambi kokulala.
Uma kukhona umlando weso elomile, ukukhishwa kwesikhashana kunconywa futhi. Ukwehla kwesigcawu kuhilela ukufaka ipulaki encane ye-collagen noma ye-silicone emgodini wezinkomba zokudabuka zeso ukugcina izinyembezi zesiguli. Izimpumputhe noma izigqoko zingase ziyingxenye yocwaningo lokulashwa ukuvimbela ukoma okungenzeki ebusuku.
Ezimweni ezinzima ngokulinganisela, odokotela bazongcoma ukuthi i-hypertonic iso noma i-ointment ngosuku noma ebusuku okuyisisombululo sikasawoti esithinta uketshezi olusuka ku-cornea, okwenza kube lula kakhulu. Lokhu kusiza amangqamuzana e-epithelial ahlale ngokuqinile ngokunamathela ku-cornea. Ngezinye izikhathi, odokotela bazosebenzisa ama-lens okuxhumene nabo ukuze athambile i-cornea.
Ezimweni lapho isiguli siqala ukuqhutshwa kwezikhathi eziqhubekayo, odokotela bayomisa amaconsi okulwa namagciwane. Amaconsi aseCycloplegic angasetshenziselwa ukunciphisa ubuhlungu nokuthuthukisa induduzo. I-Cycloplegic yehla iyancipha ukuvuvukala esweni ngokuphazamisa okwesikhashana imisipha ngaphakathi kweso elingakwazi ukuvumelanisa ngokuqinile futhi lenze ubuhlungu. Izinyembezi ezibandayo, izinyembezi ezifakiwe ezinamafutha kanye namaconsi angama-non-steroidal anti-inflammatory amaconsi angase anqunywe.
Izwi elivela
Uma ungaphenduli kahle imithi, inqubo ebizwa ngokuthi i-anterior stromal puncture inganconywa. Ukuguqulwa kwe-stromal yangaphambili kuhilela udokotela usebenzisa inaliti oyinyumba ukuze akhe amaphuzu amancane, ajulile awela embundwini ophansi. Lokhu kubangela izibazi ezincane ukwakha futhi ukusheshisa ukuphulukisa, okwenza amangqamuzana aphezulu azinamathele embundeni kangcono. Enye indlela yokwelashwa yi-PTK. I-PTK, i-keratectomy yokwelapha i-photorefractive, isebenzisa i-laser ukuze ibambelele phezulu kwe-cornea ukunciphisa izimpawu.
Umthombo:
Ukunakekelwa Okuyisisekelo Kwengxenye Ephakathi, Uhlelo Olubili. I-Copyright 1995, i-Appleton & Lange.