I-Nephrotic syndrome ingahamba nesifo sezinso ngenxa yesifo sikashukela, izidakamizwa, njll
I-Nephrotic syndrome iyinhlanganisela yezibalo ezithile ezitholakala emitholampilo ezingabonakala ezigulini ezinesifo sezinso. Ngakho-ke, ukuxilongwa komtholampilo hhayi isifo ngokwayo. Kungabonakala ngezimo ezihlukahlukene eziholela kuyo. Ukuhlanganiswa kokungajwayelekile okuhlanganiswe ndawonye ngaphansi kwe-ambulandomu i- nephrotic syndrome kufaka:
- Iproteinuria enamandla, noma ukulahlekelwa izinga elingaphelele lamaprotheni emcimbini
- Izinga lamaprotheni aphansi egazini
- I-Edema / ukuvuvukala emzimbeni
- Izinga eliphezulu le-cholesterol egazini
- Ukuthambekela okungenzeka ukwakha ama-blood clots
Indlela Eyakha Ngayo
Ukuguqulwa ezintsheni '(okubizwa ngokuthi i- glomerulus ) kungaholela e-nephrotic syndrome. Lezi zinguquko zingenziwa zodwa ngaphandle kwencazelo ecacile kepha zivame ukubonakala ngenxa yomonakalo ezintsheni 'ezihlungwini kwezinye izifo okukhulunywe ngezansi. Kungakhathaliseki imbangela, ukuguqulwa kwesakhiwo sesihlungi sezinso kuholele ekungajwayelekile emsebenzini wayo.
Ngokuvamile isihlungi sezinso sisungulwa ngendlela evumela kuphela izinto ezithile / ubuthi obuphuma egazini ukuya emcimbini. Ibuyele emangqamuzaneni amakhulu njengezinhlayiyana zeprotheyini ezitholakala egazini (enye yazo i-albinin). E-nephrotic syndrome, isihlungi silahlekelwa ikhono layo lokubandlulula phakathi kwezidakamizwa ezidlula kulo, futhi ngisho nama-molecule amakhulu njengamaprotheni aqala ukuvuza emcinini.
Lokhu kuvimbela ukuhlaselwa kwezenzakalo eziholela e-nephrotic syndrome ephelele. Ngandlela-thile, izinto ezinhle zidlula emcibini kanye nombi, futhi umzimba uqala "ukuphonsa umntwana ngaphandle kwamanzi okugeza".
Yiziphi Izifo Ezithinta I-Inso Yenza I-Nephrotic Syndrome
I-Nephrotic syndrome ingenzeka ngezimo ezihlukahlukene.
Nokho, ngezinye izikhathi asikho isizathu esibonakalayo. Ezinye zezifo ezijwayelekile ezaziwa ezibangelwa ukuguqulwa okuholela ku-nephrotic syndrome zihlanganisa:
- Isifo sikashukela
- Imithi ethile efana ne-bisphosphonates (esetshenziselwa ukwelapha i-osteoporosis), ama-painkillers e-NSAID, nokuningi
- Zenza izifo ezizenzakalelayo njenge-lupus
- Kungenzeka ngokufana namanye amagciwane
- Izifo ezithathelwanayo ngokusebenzisa izindlela ezingaqondile zokuzivikela ngegazi zingase ziholele ku-nephrotic syndrome. I-HIV yisibonelo esivamile.
- Ezinye izinhlayiya zemvelo
Ukuxilongwa
Njengoba kushiwo ngenhla, ukuxilongwa kwe-nephrotic syndrome kuhilela ukuqonda ukuqoqwa kwemiphumela eyenza i-nephrotic syndrome. Ngokujwayelekile, ukusola kusulwe ngesiguli ngenye indlela asikho esinye isizathu sokuvuvukala eduze kwamehlo noma emaqenjini. Ukuphenya ngalokhu kuzovame ukufaka ukuhlolwa komchamo. Lokhu kuzobe sekudalula ukulahleka okukhulu kwamaprotheni kumchamo. Ngezinye izikhathi iziguli ezinamaprotheni aphakeme kakhulu ezilahlekile emcimbini zizokhononda ngokubona u-foam noma ama-urine. Okunye okungavamile okufana nezinga eliphansi lamaprotheni egazini noma amazinga aphezulu e-cholesterol angabuye aqaphelwe ekuhlolweni kwebhu.
Zonke izivivinyo ezingenhla ngeke zibonise imbangela ye-nephrotic syndrome. Uma imbangela ingabonakali emlandweni womtholampilo, ngokuvamile i-biopsy yezinso kuzodingeka yenziwe ukuze ibone isifo esithile esibangela i-nephrotic syndrome.
Izinkinga
I-Nephrotic syndrome ngenxa yezifo ezithile ingase ixazululwe yodwa. Noma kunjalo, i-nephrotic syndrome engakhiwe ingaba nemiphumela emibi.
- Okusobala kunazo zonke ukuqhuma phambili kwezinso zezinso , futhi ikhono layo lokuhlunga imikhiqizo yokudoba nokuphuma ngokweqile emzimbeni.
- Amazinga aphezulu e-cholesterol abonakala ku-nephrotic syndrome ayokwandisa ingozi yesifo senhliziyo.
- Iziguli nazo zinengozini ephakeme yokwenza ama-clots egazi futhi zingabona izinhlangano ezinjenge-thongsis ejulile ye-vein ne-embolism yamapulmoni ithuthuka.
- Ingozi enkulu yokwelashwa ibonakala ngenxa yokulahlekelwa kwamagciwane okuzivikela (okuyiwo amaprotheni) emcimbini.
Ukwelapha
Ukuze uphathe i-nephrotic syndrome, kuqala udinga ukuthola ukuthi kungani une-nephrotic syndrome. Uma isizathu singabonakali emlandweni wemitholampilo kuphela, i-biopsy yezinso kuyodingeka ukuthi uphendule lo mbuzo. Uma ngabe imbangela ethile ikhonjisiwe, ukwelashwa kungase kuhlanganise inhlanganisela yemithi ehlukene evela ku-renin-angiotensin evimbela imithi yomshoshaphansi wegazi (ebizwa ngokuthi i-ACE inhibitors noma i-angiotensin receptor blockers), i-steroids, kwezinye izifo zokuzivikela (njenge-cyclosporine), njll. isimo esiphathwe kangcono ngokufuna iseluleko se-nephrologist ekhethekile .
Khumbula, umphumela wokwelashwa okuphumelelayo futhi uzokuxhomeka ekubambeni. Izinhlangano ezithile zingase zamukele ukwelashwa, kanti abanye ngeke baphendule ngisho nasibhamu esikhulu laphaya.
Ukwelashwa okuqondile nakho kudinga ukuhlanganiswa nokugxila ekwelapheni izinkinga ezizobe zenzeke. Ngakho amaphilisi amanzi afana ne-furosemide angadingeka ukuphatha ukuvuvukala okuvame ukubonakala. Kungase kudingeke ukuthi iziguli ezithile zithole igazi ukuze zivimbele ama-blood clots. Ukudla okuphansi kwe-sodium kuyadingeka njalo.