I-Hematohidrosis-isimo esingavamile, esingasongeli, nesicindezelayo
Nakuba ukukhukhumeza igazi-noma i-hematohidrosis-kungase kubonakale kushaqisayo, kusukela embonweni we-somatic, kuyisimo esibucayi kakhulu. Imiphumela emibi yalesi simo esingavamile ingokwengqondo, futhi abantu abane-hematohidrosis banenkinga yokuxhumana nabanye ngoba besaba ukuthi bangase baqale ukuphuma, ikakhulukazi ngaphansi kwezimo ezicindezelayo.
Kulezi zincwadi, kunemibiko embalwa yecala, noma ama-akhawunti, noma ukuthuthumela okugazini.
Kunezizathu ezithile zokucabanga ukuthi yiziphi izimbangela noma ezibangelwa i-hematohidrosis, kodwa ukwesekwa okunamandla kuyasweleka. Ngaphezu kwalokho, akukho ukwelashwa okusekelwe ebufakazini be-hematohidrosis ekhona. Ake sibheke okuncane esikwaziyo ngokukhukhumeza igazi.
Izimpawu
I-Hematohidrosis yenzeka ngaphezu kwesikhumba esingapheli, isikhumba esingenalutho ngaphandle kwezilonda. Ngokuvamile kwenzeka ngesikhathi sokucindezeleka ngokomzwelo. Kungenzeka futhi ngesikhathi sokuzivocavoca noma ukulala. Ukujuluka kwegazi kuphefumula ebusweni nasezandleni. Ngokuthakazelisayo, i-hematohidrosis nayo ibhaliswe entombazaneni eneminyaka engu-10 ene-hemolacria, esinye isimo esingavamile esiholela ezinyembezini ezinamanzi. (Le ntombazane yabhekana nokukhukhuma nokulala izinyembezi.)
Iziqephu zokukhukhumeza igazi ziye zaphawula ukuba zigcine phakathi kwemizuzu emihlanu kuya kwemihlanu. Ngokusobala, ukujuluka kukhishwa ngegazi ngokuvumelana nokujuluka okuvamile.
Ukuxilongwa
Ngaphandle komlando wezokwelapha, i-hematohidrosis itholakala lapho amaseli abomvu egazi (okungukuthi, ama-erythrocytes) abonakala ekhukhumeza igazi ngaphansi kwe-microscope.
Ezinye izinyathelo ze-laboratory zegazi zingaphakathi kwemingcele evamile kufaka inani eliphelele le-cell cell, iphaneli yamagciwane, nezifundo ze-coagulation. Ngaphezu kwalokho, imiphumela yokuhlolwa ngokomzimba nangokomzimba ayinakwenzeka.
I-skin biopsies yenzelwe abantu abambalwa abatholwa ukuthi bane-hematohidrosis.
Imiphumela yalezi zinhlobo ze-biopsies ayihambisani futhi ayihambisani, ezinye zibonisa i-histology evamile ngenkathi abanye bebonisa ukuxubana kwemithwalo yegazi ye-periglandular, ukuvuza kwegazi eduze kwama-capillaries, noma amangqamuzana abomvu egazi emaceleni ezinwele zezinwele.
Okunye ukuhlukana-noma okunye-ukuxilongwa kweziguli ezethula ukukhukhumeza kwegazi kuyisifo esiyiqiniso. Ukukhathazeka okuyiqiniso kuyinkinga enkulu yengqondo ehilela isiguli esithatha indima egulayo, futhi eveza ngamanga ngokugula, ukulimala noma izimpawu zomzimba. Ngokufanayo, ukuxilonga kubhekwa njengesihlonzi sokuhlukanisa i-hematohidrosis. Okubaluleke kakhulu, ukuhlukunyezwa kuhluka ekungeneni okuyiqiniso ngenhloso: Ukukhwabanisa kushukunyiswa yinzuzo yomuntu siqu. Ukulawula kokubili ukuphazamiseka okwenyukayo nokuhlukumeza, iziguli ezethula ukujuluka kwegazi zingabhekwa ngokucophelela emasontweni egazi.
Ngokusekelwe ekufundweni kwezincwadi ezincwadini, kubonakala sengathi i-hematohidrosis ingadala ukugula kwengqondo, njengokucindezeleka, ukukhathazeka okwenziwe jikelele, nokuphazamiseka kwesifo. Ngokudabukisayo, abantu abanalesi simo bazihlukanisa nabanye ngenxa yokwenza amahloni nokukhathazeka.
Izimbangela
Ngokuvamile, kuye kwaphakanyiswa ukuthi izitsha zegazi ezizungeze izigulane ezikhukhulayo zixosha igazi emiphakathini yalezi zinhlayiya ngenxa yezingqinamba ezingavamile kanye nokukhula (okungukuthi, ukukhuphuka).
Ezinye izincazelo ziphakamisa ukucindezela kwegazi eliphezulu nokuvuvukala kwemithambo yegazi (okungukuthi, i-vasculitis) njengezimbangela zokugaya emasongweni e-sweat.
Lezi zicabangela, kodwa, zihlala zingavunyelwe, futhi ukuphuma kwegazi okufanayo kufana nezinhlanzi zezinwele kanye nasezindaweni ezingenalutho. Eqinisweni, ezincwadini, iziguli ezimbalwa ziye zanikeza i-otorrhea enegazi, noma umcengezi wezindlebe.
Ku-athikili ka-2015 okuthiwa "i-Hematohidrosis: ulwazi emathakathini," u-Uber nozakwethu babhala okulandelayo mayelana ne-hematohidrosis:
Ezinye izinkomba ziye zahlongozwa, kufaka phakathi: ukwanda kwengcindezi ye-vascular eholela ekuhambeni kwamaseli egazi ngokusebenzisa imigqa yezingqimba zomzimba; i-vasculitis yemikhumbi ye-dermal; futhi kukhulise ukuvuselela ukuzwela okuholela ekwenzeni i-periglandular ye-vessel kanye nokwandiswa okulandelayo, okuvumela ukuthi okuqukethwe kwegazi kungene emadakeni.
Kulesi sihloko, u-Uber nozakwabo babokuqala ukubhala isixhumanisi phakathi kweziqephu ze-hypertensive ne-hematohidrosis. Ukusebenzisa ukuqapha kwengcindezi yengcindezi yegazi lehora eli-24, abacwaningi baqaphele ukuthi ukucindezelwa kwegazi owesifazane oneminyaka engu-18 ubudala oneminyaka engu-18 ubudala ufike ku-180/90 ngesikhathi segazi.
Ukwelapha
Ayikho indlela eqinisekisiwe yokwelapha i-hematohidrosis. I-Propanolol, okuyi-beta-blocker esetshenziselwa ukwelapha ukucindezelwa kwegazi eliphezulu, isize abanye abantu ngalesi simo. Isizathu sokuthi kungani i-beta-blockers ephumelela ekwelapheni i-hematohidrosis ingase ihlangane neqiniso lokuthi ukusizwa okungenabubeleko, okubhekiswe ngabakwa-beta-blockers, cishe kudlala indima kule nkinga.
> Imithombo:
> Biswas S, Surana T, De A, Nag F. Icala elifuna ukwazi ukushaya igazi. I-Int J Dermatology . 2013; 58 (6): 478-480. https://doi.org/10.4103/0019-5154.119964
> Maglie R, Caproni M. Icala legazi lokujuluka: i-hematohidrosis syndrome. I-CMAJ . 2017; 189: E1314. https://doi.org/10.1503/cmaj.161298
> Praveen, BK, Vincent, J. Hematidrosis noHemolacria: Umbiko Wezehlakalo. I-Indian J Pediatr . 2012; 79: 109. https://doi.org/10.1007/s12098-011-0449-2
> Uber M et al. I-Hematohidrosis: ukuqonda emathambo. I-Int J Dermatology . 2015; 54: e542-e543. http://dx.doi.org/10.1111/ijd.12932