Isifo Sobuningi Siba Ngesikhathi Esibulalayo
Isifo se-Creutzfeldt-Jakob senza isihloko seminyaka ngonyaka ka-2000 lapho kuqhuma amacala e-United Kingdom. Lezo zimo zazixhunyaniswe nokudla okonakele nge-bovine spongiform encephalopathy (BSE), isifo se-prion esibangele i-CJD ehlukile, okuthiwa ngokuthi "isifo sofuba".
Umphakathi unesizathu esihle sokukhathazeka ngokudluliselwa kwe-BSE kubantu.
Isifo esivela ku-Creutzfeldt-Jakob, njengezinye izinhlobo ze- Creutzfeldt-Jakob , isifo esiqhubekayo, esiyingozi njalo yesifo sezinzwa. Kodwa lesi sifo siyinto engavamile kakhulu: Kusukela ngo-Okthoba 1996 kuya ku-Mashi 2011, kwafika amacala angu-175 kuphela e-United Kingdom, e-France, e-5 eSpain, e-4 e-Ireland, e-3, e-Netherlands nase-United States of America kuphela. USA), 2 eCanada, e-Italy nasePortugal, futhi eyodwa ngayinye eJapane, e-Saudi Arabia naseTaiwan.
I-Centers for Disease Control and Prevention (CDC) ihlola izimo e-United States yazo zonke izinhlobo zeCreutzfeldt-Jakob isifo.
Izinhlobo Ezihlukahlukene Zesifo, Ezibulalayo
Akukho ukwelashwa kwesifo seCreutzfeldt-Jakob, esingaba khona kumuntu ngezindlela ezintathu:
- Amacala angu-10 kuya kwangu-15 amacala azuzwe njengefa, okubangelwa ukuguqulwa kwezakhi.
- Amacala amaningi abonakala sengathi avela kancane, kumuntu ongenalo umlando womndeni wesifo.
- Amaphesenti amancane amacala atholakala ngokutheleleka, ngokuxhumana nomzimba wesifo sobuchopho. Kukhona amacala aqoshiwe okwenzeka njengomphumela ongalindelekile wenqubo yezokwelapha.
Isifo se-Creutzfeldt-Jakob asithelelisi ngezindlela ezivamile, njengokusikhipha noma ukukhwehlela - azikho amacala owaziwayo omshado noma amalungu omndeni womuntu onegciwane obhekene nalesi sifo.
Imikhiqizo yezinyosi ezingcolile
Izimo ze-Creutzfeldt-Jakob isifo sibonakala sengathi zihlobene nokudla imikhiqizo yenkomo engcolile eYurophu. Isifo esifanayo, uma kwenzeka ezimvu, sabizwa ngokuthi "scrapie." Kukholelwa ukuthi imikhiqizo yezimvu ezithathelwana ngesibhamu yayisetshenziselwa ukondla izinkomo, futhi yileyo ndlela izinkomo ezithole ngayo.
Ososayensi bathole ukuthi yini ebangela ukuthi i-BSE, i-scrapie, ne-Creutzfeldt-Jakob izifo azilona igciwane noma amabhaktheriya njengezinye izifo, kodwa i-protein ebizwa ngokuthi i-prion. I-prion iguqula amaprotheni ajwayelekile kubantu ababulalayo, ababulalayo.
Imiphumela kwi-Brain
Njengoba isifo seCreutzfeldt-Jakob sithinta ubuchopho, izimpawu ezikhiqizayo ziyizinzwa. Kungase kuqalwe ngokuzenzakalelayo ngokulahla, ukucindezeleka, ukudideka, izinguquko zobuntu nezokuziphatha, nezinkinga zememori, ukuxhumana nokubona. Njengoba iqhubekela phambili, lo muntu ukhula ngokushesha futhi azinakekele, ukunyakaza okungavamile okubizwa ngokuthi i-myoclonus.
Esigabeni sokugcina sesi sifo, isiguli sigula yonke imisebenzi yengqondo nengokwenyama, ihluleka ukuba i-coma, futhi ekugcineni ife. Inkambo yesifo ngokuvamile ithatha unyaka owodwa. Lesi sifo ngokuvamile sithinta abantu phakathi kweminyaka engama-50 kuya ku-75, noma kunjalo, isifo esihlukile seCreutzfeldt-Jakob sithinte abantu ngesikhathi esincane - ngisho nentsha (iminyaka isukela eminyakeni engu-18 kuya kwengu-53 ubudala).
Kunzima Ukuzihlola
Akukhona, okwamanje, ukuhlolwa okuqondile kwezokwelapha ukuthola ukugula kwe-Creutzfeldt-Jakob, futhi ukuqinisekiswa kwesifo kungenziwa kuphela ngemva kokufa nge-autopsy. Njengoba lesi sifo singavamile, abanye odokotela bangase bangacabangi njengento yokuxilongwa futhi bangase baphephe izimpawu zenye izifo ezibuchopho ezifana ne- Alzheimer's noma i- Huntington . Ososayensi basikisela ukuthi ukuhlolwa okusha kwe-laboratory entsha, eyinkimbinkimbi kuzokwenzeka esikhathini esizayo ukwazi ukubona izimpendulo kumuntu wegazi noma izicubu zomuntu onegciwane.
Imithombo:
Collins, S., A. Boyd, A. Fletcher, MF Gonzales, CA McLean, CL Masters. "Intuthuko yakamuva ekuxilongweni kwangaphambi kokufa kwesifo seCreutzfeldt-Jakob." J Clin Neurosci 7 (2000): 195-202.
"i-vCJD (i-Variant Creutzfeldt-Jakob Disease)." NCIDOD. 29 Nov 2006. Izikhungo zokuLawula nokuvimbela izifo. 28 Dec 2006 http://www.cdc.gov/ncidod/dvrd/vcjd.
Will, R., M. Zeidler, GE Steward, MA Macleod, JW Ironside, SN Cousens, J. Mackenzie, K. Estibeiro, AJ Green, R. Knight. "Ukuxilongwa kwesifo esisha seCreutzfeldt-Jakob." U-Ann Neurol 47 (2000): 575-582.
Wilson, K., ikhodi C., M. Ricketts. "Ingozi yokuthola isifo seCreutzfeldt-Jakob ekumpompheni igazi: Ukubuyekezwa okuhlelekile kwezifundo zokulawula icala." I-BMJ 321 (2000): 17-19.