Izifo Zengane Ezizuziwe
I-Bartter syndrome iyicala le-kidney elibhekwa njengefa elibangelwa yi-defect ekukhunjweni kwezinso ukubuyisela kabusha i-potassium. Lokhu kwenza izinso zisuse i-potassium kakhulu emzimbeni.
I-Bartter syndrome izuzwe njengefa le- autosomal pattern , kodwa ngezinye izikhathi kungenzeka kumuntu ongenalo umlando womndeni wesifo. Ayaziwa ukuthi kaningi kangakanani i-Bartter syndrome eyenzekayo, kodwa isifundo esisodwa sinquma ukuthi sithinta abantu abangu-1.2 kubantu abayizigidi.
Kubonakala sengathi kwenzeka njalo kaningi ezinganeni ezizalwe abazali abazitholayo, noma ezihlobene eduze. I-Bartter syndrome ithinta bonke abesilisa nabesifazane bazo zonke izizinda.
Izimpawu
Izimpawu ze-Bartter syndrome zingabandakanya:
- ubuthakathaka jikelele kanye nokukhathala
- ukwanda kwamanzi (polyuria)
- ukoma okwandayo (polydipsia)
- Ukuvuvuka ebusuku ukuvuthwa (i-nocturia)
- ukuphelelwa amandla kwamanzi
- ukuthanda usawoti
- imisipha ye-muscle
- ukuqotshwa
Izingane ezine-Bartter syndrome zinzima ukukhula futhi zikhula ngendlela evamile.
Ukuxilongwa
I-Bartter syndrome ivame ukutholakala ebuntwaneni ngokususelwa ekuhlolweni kwangokwenyama, izimpawu ezikhona, kanye nemiphumela yokuhlolwa kwegazi ne-urine. Lokhu kufaka:
- izinga eliphansi le-potassium egazini
- izinga eliphezulu le-potassium emcinini
- izinga eliphansi le-chloride egazini
- izinga eliphezulu le-chloride emcini
- amazinga aphezulu ama-hormones renin ne-aldosterone egazini
I-Gitelman syndrome ifana ne-Bartter syndrome ukuze kudingeke ukuhlolwa okwengeziwe ukuze kunqume ukuthi iyiphi i-disorder ekhona.
Ukwelapha
Ukwelashwa kwe-Bartter syndrome kugxile ekugcineni i-potassium yegazi ezingeni elivamile. Lokhu kwenziwa ngokudla okucebile nge-potassium nokuthatha izithako ze-potassium uma kudingeka. Kukhona nezidakamizwa ezinciphisa ukulahlekelwa kwe-potassium kumchamo, njenge-spironolactone, triamterene, noma i-amiloride.
Eminye imithi esetshenziselwa ukuphatha i-Bartter syndrome ingafaka i-indomethacin, i-captopril, kanye nezingane, i-hormone yokukhula.
> Imithombo:
> "Bartter Syndrome." I-Medical Encyclopedia. 15 Okthoba 2008. I-MedlinePlus.
> "Kuyini i-Bartter's Syndrome?" Izihloko. 5 Okthoba 2008. I-Bartter Site.
> "Bartter Syndrome." Izifo ezibuhlungu zama-Tubular and Cystic Kidney. Dec 2006. I-Merck Manuals Online Medical Library.