Sibutsetelo
Nakuba amagama angase abonakale esabekayo, i-Erythroblastopenia ehamba phambili yezingane (i-TEC) i- anemia yokulinganisa ngokwanele yobuntwana. Yimbangela ejwayelekile kunazo zonke yokunciphisa ukukhiqizwa kwe-cell cell ebomvu ebuntwaneni. I-Erythroblast yilezi amangqamuzana ezikhula zibe amangqamuzana egazi abomvu futhi -penia livela egameni lesiGreki lokuntula. Ngokuyinhloko, i-anemia ibangelwa ukuhluleka komnyosa wethambo ukukhiqiza amangqamuzana egazi abomvu isikhathi esithile.
Izimpawu
I-anemia ku-TEC inqubo encane ngakho ezinye izingane zingenayo izimpawu. Lezi zingane zingatholakala ngengozi yomsebenzi wegazi njalo noma zingabuyiselwa ngaphandle kokuthola usizo lwezempilo. Kwezinye iziguli, izimpawu zihlobene ne-anemia. Zihlanganisa:
- Ukukhathala noma ukukhathala
- Isikhumba esikhuphukile noma esikhuphukile
- Isizungu
- Ukushaya kwenhliziyo okusheshayo, okubizwa ngokuthi i-tachycardia
- Ukuphelelwa umoya
Ama-Rick Factors
Njengoba igama liphakamisa, i-TEC ivela ebuntwaneni. Iningi lezingane litholakala ukuthi liphakathi kweminyaka eyodwa neyodwa ubudala. Abafana babonakala benengozi encane uma kuqhathaniswa namantombazane.
Ukuxilongwa
Akukho ukuhlola okukodwa kokuhlola kwe-TEC. Ezinye iziguli zingase zihlonzwe ngomsebenzi wegazi ojwayelekile wokuhlola izingane kahle. Kwezinye iziguli, uma kutholakala ukuthi i-anemia iyasolwa, i-TEC ibonakala ngokuphelele kwegazi (CBC). Ngokuvamile, i-CBC izokwethula i-anemia ehlukanisiwe. Ngezinye izikhathi kungase kube neutropenia (inani elinciphile lama-neutrophils, uhlobo lweseli elimhlophe legazi).
Amangqamuzana egazi abomvu ajwayelekile kodwa angakhula lapho isiguli siqala ukubuyiswa.
Ingxenye elandelayo ye-worp kuyinto count reticulocyte. Ama-reticulocytes amamasosha egazi abomvu asanda kukhishwa emnothweni wethambo. Ekuqaleni kwenkambo, inani le-reticulocyte liphansi, elibizwa nge-reticulocytopenia.
Uma ukuxoshwa komnyosi wethambo kuxazululwa, inani le-reticulocyte likhuphuka (eliphakeme kunejwayelekile) ukugcwalisa ukunikezwa kwegazi elibomvu futhi libuyele evamile uma i-anemia ixazulula.
Ngesikhathi sokusebenza, kubaluleke kakhulu ukuhlukanisa i-TEC esuka ku-Diamond Blackfan Anemia (i-DBA), uhlobo olululwane lwe-anemia. Iziguli ezine-DBA zine-anemia enkulu yokuphila. Iziguli ezine-DBA ngokuvamile zincane (ezingaphansi kweminyaka engu-1) lapho zixilongwa futhi amangqamuzana egazi abomvu amakhulu kunejwayelekile (macrocytosis). Ngokuvamile, uma ukuxilongwa akucaci ukuthi i-aspirate yomnkantsha wamathambo kanye ne-biopsy kungadingeka kwenziwe. Ngezinye izikhathi ukuhlolwa okungcono kokuqinisekisa kwe-TEC ukuthi isiguli siyithola ngaphandle kokungenelela.
Izimbangela
Impendulo emifushane asiyazi. Cishe isigamu seziguli sizobika ukugula kwegciwane lesiguli 2 - 3 ngaphambi kokuxilongwa. Kucatshangwa ukuthi igciwane lidala ukususwa okwesikhashana kwe-red cell cell production in the bone. Amagciwane amaningana ahlotshaniswa ne-TEC kodwa ayikho ngesisekelo esifanayo.
Isikhathi
Ezimweni eziningi, i-TEC ixazulula ezinyangeni ezingu-1 kuya kwezingu-2 kodwa kukhona imibiko yezingane ezithatha isikhathi eside ukuze zilulame.
Ukwelapha
- Ukuqaphela: Uma i-anemia ilula futhi ingane yakho ingabonakali, akukho ukwelashwa okungadingeka. Udokotela wakho angathuthukisa ukubala kwegazi kwengane yakho ngokuhamba kwesikhathi kuze kuxazululwe.
- I-Corticosteroids: Ngezinye izikhathi ama-steroids afana ne-prednisone asetshenzisiwe kodwa abukho ubufakazi obuqinile bokuthi le ukwelashwa kuphuthuma isikhathi sokubuyiselwa.
- Ukuguqulwa komzimba: Uma i-anemia inzima noma ingane yakho isifo esibangelwa yi-anemia (isizungu, ukukhathala, ukuphefumula, izinga lokushaya kwenhliziyo, njll) ukunikezelwa kwegazi kunganikezwa.