Izindleko zokudansa ze-Eyes zokudansa
I-Opsoclonus-myoclonus syndrome (i-OMS) yinkinga yokuvuvukala kwengqondo. Kubangela izingqinamba ezibalulekile ngamakhono emoto, ukunyakaza kwamehlo, ukuziphatha, ukuphazanyiswa kolimi kanye nezinkinga zokulala. Kuvame ukuza ngokuzumayo futhi ngokuvamile kungapheli; uma uthola ukuthi une-opsoclonus-myoclonus syndrome, cishe kuyohlala kuyo yonke impilo yakho.
Igama layo lichaza izimpawu zalo: i- opsoclonus igxilisa ukunyakaza kwamehlo futhi i- myoclonus kusho ukungaxhunyeki kwemisipha. Kuyaziwa nangokuthi "i-Kinsbourne syndrome" noma "amehlo okudansa-amadansa."
Ubani engozini
Esikhathini sokugula okuzenzakalelayo , umzimba uhlasela amaseli akhe aphilile. I-Opsoclonus-myoclonus syndrome ibangelwa ukugula okuzenzakalelayo lapho izifo zomzimba zomzimba ziphendula khona ngokutheleleka ngegciwane noma isisu esibizwa nge-neuroblastoma. Kunoma yikuphi, ama-antibodies aphelela ekuhlaseleni amangqamuzana obuchopho futhi, lokhu kubangela umonakalo oveza izimpawu.
I-Opsoclonus-myoclonus syndrome ibonakala kaningi ezinganeni. Izinsana yiqembu elidala lapho i-neuroblastoma ivame ukukhula; cishe amaphesenti amane alawa bantwana azothuthukisa i-OMS. Noma yimuphi ingane ene-OMS izohlolwa ukuthi ibone ukuthi ingabe unesifo, ngisho noma igula ngesifo sengculazi kusukela kulababili evame ukuhamba ndawonye.
Ukwelapha
Ukukhathazeka okuyinhloko nge-opsoclonus-myoclonus syndrome kuqala ukuxilongwa kanye nokwelapha ukuze kutholakale ukuxolelwa kwegazi nokubuyiswa. Uma ingane ine-opsoclonus-myoclonus syndrome futhi ine-tumor, ngokuvamile isisu siyasuswa. Ngokuvamile, izicubu zikhona ezinkathini zokuqala kanye ne- chemotherapy noma ukwelashwa kwemisebe akudingeki.
Ngezinye izikhathi lokhu kuthuthukisa noma kuqeda izimpawu. Kubantu abadala, ukususwa kwe-tumor ngokuvamile akusizi futhi izimpawu zingase zibe zimbi nakakhulu.
Ezinye zokwelashwa zihlanganisa:
- Amagciwane we-Adrenocorticotrophic hormone (ACTH)
- I-immunoglobulins engenayo i-intravenous - amalungiselelo ezentengiselwano ze-antibodies ezivela kubanikeli begazi abanempilo
- I-Azathioprine (Imuran) - igudluza isimiso somzimba sokuzivikela, esinciphisa ukwenziwa kwama-antibodies
- I-steroid e-oral and intravenous, njenge-prednisone, dexamethasone, ne-hydrocortisone
- I-chemotherapy efana ne-cyclophosphamide ne-methotrexate, yezingane ezine-neuroblastoma
- Apheresis yokwelapha - ukushintshanisa i-plasma yegazi
- Ukuhamba emzimbeni - ukuhlanza ama-antibodies egazini kuye kwavivinywa kubantu abadala abane-OMS.
Ukwelapha okuqhubekayo okudingekayo njalo kuvame ukuphatha izimpawu nokunciphisa ingozi yokubuyiselwa kwesisu.
Isibikezelo
Abantu abanethuba elikhulu lokubuyela esimweni esivamile emva kokwelashwa yibo abanempawu ezimnene kakhulu. Labo abanezibonakaliso ezinzima bangase babe nokukhululeka kwemizwa yabo (myoclonus) kodwa babe nobunzima ngokusebenzisana. Ezinye izinkinga ezibangelwa ukulimala kwengqondo, ezifana nokufunda nokuziphatha kwezinkinga, ukukhathazeka ngokweqile ukugula kwengqondo (ADHD) kanye nokukhathazeka okucindezelayo, kungase kwenzeke, futhi lokhu kungadinga ukwelashwa kwabo.
Izingane ezinezimpawu ezinzima kunazo zonke ze-OMS zingase zibe nokulimala okungapheli kobuchopho okungabangela ukukhubazeka ngokomzimba nangokwengqondo.
Ukuvama
I-Opsoclonus-Myoclonus Syndrome iyinqaba kakhulu; Abantu abayizigidi ezilodwa kuphela bakholelwa ukuthi banenkinga emhlabeni. Ngokuvamile kubonakala kubantwana nakubantu abadala, kodwa kungathinta abantu abadala. Kwenzeka kaningi emantombazaneni kunabantwana futhi kuvame ukutholakala kuphela ngemva kwezinyanga eziyisithupha ubudala.
Imithombo:
U-Pranzatelli, M. "Izimpawu ZaseVital: Umlilo Ohlelekile." Discove r, 2000.
Pranzatelli, M. "Opsoclonus-Myoclonus Syndrome". Inhlangano Kazwelonke Yezinkinga Ezinzima, 2016.