Iyini Inqubo?

Izimo ezimbili ezibangela ukuguga okusheshayo

Kuyinto evamile ukubuka iminyaka embalwa encane noma ngaphezulu kunalokho oyikho ngempela. Kodwa, ake ucabange ukubuka ubheke iminyaka engamashumi eminyaka kuneminyaka yakho. Kubantu abanokuqhubekayo, isimo sezakhi zofuzo esibangela ukuguga okusheshayo, kuyinto evamile ukubuka iminyaka engama-30 noma ngaphezulu emdala kunayo empeleni.

Ngenkathi i-progeria ivame ukuhambisana ne-Hutchinson-Gilford enyuka phambili, leli gama lingase libheke ku-Werner syndrome, eyaziwa nangokuthi ukhula omdala.

I-Hutchinson-Gilford Progeria

I-Hutchinson-Gilford isandulela ngandlela-thile ingavamile, ithinta izingane ezingaba yizigidi ezingu-4 kuya kweziyi-8. Izingane ezinezinyathelo eziqhubekayo zinokubonakala okujwayelekile uma zizalwa. Izimpawu zalesi simo ziqala ukubonisa noma nini ngaphambi kokubili kweminyaka emibili lapho umntwana ehluleka ukuthola isisindo futhi izinguquko zesikhumba zenzeka. Ngokuhamba kwesikhathi. ingane iqala ukufana nomuntu osekhulile. Lokhu kungafaka:

Cishe amaphesenti angu-97 ezingane eziqhubekayo yiCaucasus. Kodwa-ke, abantwana abathintekayo babheka ngendlela efana naphezu kwezizinda zabo ezihlukahlukene. Iningi lezingane ezinezinyathelo eziqhubekayo ziphila zibe cishe eminyakeni eyi-14 ubudala futhi zifa ngesifo senhliziyo.

Werner Syndrome

I-Werner syndrome kwenzeka cishe ku-1 kubantu abayizigidi ezingu-20.

Izimpawu zikaWerner syndrome - njengezici ezincane noma izici zobulili ezingathuthuki - zingabonisa ngesikhathi sokukhula noma ebusheni. Kodwa-ke, izimpawu zibonakala zibonakala kakhulu uma umuntu ehlasela phakathi no-30s. Izimpawu zingafaka:

Werner syndrome kwenzeka kaningi kubantu baseJapan naseSardinian. Abantu abane-Werner syndrome basinda eneminyaka engama-46 ubudala, kanti baningi banqotshwa yisifo senhliziyo noma umdlavuza.

Ucwaningo lwesikhathi esizayo

I-Werner syndrome ibangelwa ukushintshashintsha kwegciwane le-WRN kwi-chromosome 8. Iprojekthi ebangelwa ukuguqulwa kwesakhi se-LMNA ku-chromosome 1. I-LMNA gene iveza i-Lamin A protein, ephethe i-nucleus yamaseli ethu ndawonye. Abacwaningi bakholelwa ukuthi lawa maseli angaqiniseki anesibopho sokuguga okusheshayo okuhambisana nentuthuko. Abacwaningi bethemba ngokutadisha lezi zakhi zofuzo ezingabangela ukwelashwa kuzo zombili izimo kanye nesifo esiqeda ukubulala abantu abanezinhlobo zombili zokuqhubeka - njenge- atherosclerosis nezinye izifo ezihambisana nokuguga.

> Imithombo:

Kaiser, HW, (2002). I-Hutchinson-Gilford enyuka phambili. iMedicine, ifinyelelwe ku-http: //www.emedicine.com/derm/topic731.htm

I-Progeria Research Foundation.

Scientific American.com. (1999). Yini esikwaziyo mayelana nesisusa sikaWerner syndrome nokuqhubeka, isifo esiholela ekugugeni kusenesikhathi ezinganeni?

I-Wozniacka, A. (2002). Iprogeria (Werner syndrome). eMedicine