Isifo esivela ngegazi, ngezinye izikhathi esibizwa ngokuthi i-coagulopathy, umane nje yisimo esenza ukwenzeke kakhulu kunomuntu ovamile. Umzimba awukwazi ukwenza i-clot kahle. Lokhu kuhilela enye yezingxenye ze-coagulation yethu (uhlelo lokugaya nokugaya).
Uhlelo lwe-coagulation kufanele lube nokulinganisela, hhayi ukuphuma kwegazi okwedlulele kodwa futhi hhayi nokuqeda kakhulu.
Enye ingxenye yenqubo ihlanganisa amaplatelet , elinye lamaseli ethu egazi. Ingxenye yesibili itholakala engxenyeni yegazi ebizwa nge-coagulation izici. Ngezinye izikhathi abantu babhekisela kubantu abanezinkinga zokugaya njenge "bleeders mahhala."
Izimpawu
Izimpawu zesifo sokuphuma kwegazi zingashintsha kakhulu. Akuzona zonke iziguli ezinezinkinga zokugaya zizoba nazo zonke lezi zimpawu.
- Iziphuzo ze-noseble ezihlala njalo noma ezinde
- Ukusuka okuvamile noma okuhlala isikhathi eside kwezinsini
- Izikhathi zokuya esikhathini ezidlulayo ezibizwa ngokuthi i-menorrhagia kanye nokweqa ngokweqile ngemuva kokubeletha (emva kokubeletha)
- Ukuphuma kwegazi isikhathi eside emva kwensimbi yomuthi (igazi ukudweba noma umjovo njengomgomo wokugoma)
- Ukuphuma ngokweqile ngesikhathi noma ngemuva kokuhlinzwa okudinga imizamo eyengeziwe yokuyeka ukuphuma kwegazi
- Imivalo emikhulu enezintambo
Kungenxa yokuthi ungase uhlangabezane nalezi zimpawu akusho ukuthi unesifo sokuphuma kwegazi. Kufanele uxoxisane nokukhathazeka kwakho nomhlinzeki wakho wezempilo.
Izimbangela
- Ifa : Ezinye izifo eziphaphaza njenge-hemophilia ne-Von Willebrand zizuzwa njengefa, okusho ukuthi umuntu uzalelwa ngesifo.
- Isifo sesibindi : Izici ze-coagulation zenziwa kakhulu esibindi. Abantu abanezifo ezinzima zesibindi abakwazi ukukhiqiza izici ezanele zokugcoba ngakho-ke kungenzeka ukuthi baphelelwe igazi.
- Ukuntuleka kwe-Vitamin K : Izici eziningi ze-coagulation zidinga i-Vitamin K ukuthi isebenze kahle ngakho abantu abane-Vitamin K abanakho amathuba okuphuluka.
- Ukwelashwa kwe-Anticoagulation : Abantu abakwelapha i-anticoagulation (imithi evimbela ukuvala ama-clotting) engozini yokwanda kwegazi.
- Iziphazamiso zeplatelet : Uma amaplatelet engakwazi ukusebenza kahle, awakwazi ukwakha i-clot efanele engabangela ukuphuma kwegazi.
Izinhlobo
- I-Hemophilia : Mhlawumbe isifo esingaziwa kakhulu sokugaya igazi yi-hemophilia. Abantu abane-hemophilia abalahlekelwa esinye sezici zabo ze-coagulation. Igama lohlobo lwawo lwe-hemophilia lusekelwe kulokho okushiwo. Uhlobo oluvame kakhulu yi-hemophilia A; lezi ziguli zilahlekile isici 8 kusukela ohlelweni lwazo lwe-coagulation. Kukhona futhi i-hemophilia B (ukungabi nalutho kwe-factor 9) ne-hemophilia C (ukulahlekelwa kwe-factor 11). I-Hemophilia izuzwe njengefa (idluliselwe emindenini). Kuhilela i-chromosome ye-Y ukuze amadoda athathwe kakhulu. Abantu abane-hemophilia bangaba negazi elikhulu ekulimazeni noma ngokuzenzekelayo (ngaphandle kokulimala) ukuphuma kwegazi.
- Isifo se-Von Willebrand : Isifo se- Von Willebrand (VWD) yisifo esivame kakhulu sokuphuma kwegazi emhlabeni. Kulinganiselwa ukuthi u-1% wabantu banesimo esithile se-Von Willebrand. I-VWD nayo izuzwe njengefa kodwa kokubili amadoda nabesifazane bangathinteka ngokufanayo. Inani lokuphuma kwegazi lingahluka kakhulu kuye ngokuthi hlobo luni lwe-VWD umuntu aluthola.
- Isifo sesibindi : Uma isibindi singasebenzi kahle, asikwazi ukukhiqiza izici ze-coagulation. Ngaphandle kwalezi zici, iziguli zingaba nokuphuma okuphawulekayo.
- Ukubalwa kweplatelet ephansi (thrombocytopenia) : Kunezizathu eziningi ze-platelet count ephansi kuhlanganise ne- leukemia , umphumela ohlangothini lwe-chemotherapy, i- thrombocytopenia ye- immune (lapho amasosha omzimba ebhubhisa amaplatelet).
- Iziphazamiso zomsebenzi weplatelet: Ngaphezu kwamanani aseplatelet aphansi abangela ukuphuma kwegazi, uma amaplatelet engasebenzi kahle, kungenzeka ukuthi kuphuma igazi.
Ukwelapha
Kunezinhlobo eziningi zokwelashwa okungenzeka ukwelapha kumuntu one-disorder disorder.
Ukwelashwa okhethiwe kuncike ekubambeni kwe-disorder disordination noma indawo yokuphuma kwegazi.
- Ukushintshwa kwe-Factor : Iziguli ezine-hemophilia zingakwazi ukuzifaka ngemikhiqizo yokuguqula izinto ezingaphazamisa iziqephu zegazi. Namuhla, iziguli eziningi ezine-hemophilia zenza ukushintshwa kwezinto ezivamile ukuze kuvinjelwe iziqephu zegazi.
- I-Desmopressin (ekhonjiswe igama elithi Stimate): I-Desmopressin ingumkhiqizo oshintshayo we-hormone vasopressin. Ukuthatha i-desmopressin kubangele ukwanda okwesikhashana ku-von Willebrand antigen ne-factor 8 okungase kumise ukuphuma kwegazi kwiziguli ezine-hemophilia enomzimba A noma isifo se-von Willebrand.
- Ukumpontshelwa kweplatelet : Uma inani leplatelet liphansi noma amaplatelet awenzi kahle, ukunikezelwa kweplatelet kunganikezwa ukuvimbela / ukuphatha ukuphuma kwegazi.
- I-plasma efriziwe efriziwe : Izimboni ze-coagulation zitholakala e-plasma (ingxenye yetshezi yegazi). Uma umuntu elahlekelwa izici eziningana ezihlukene, njengokwehluleka kwesibindi, ukunikezwa kwamaplasma amnandi aqhwaziwe kunganikwa.
- I-Vitamin K : Uma isiguli uma i-Vitamin K ihlulekile, inganikezwa isithasiselo.
- I-Antifibrinolytics : Le mithi igwema ukuphuma ngokweqile ngokwezintambo ezizinzile. Lokhu kusetshenziselwa ukulawula ukuphuma emlonyeni noma izikhathi ezinzima zokuya esikhathini.
Nini Ukubona Udokotela Wakho
Uma ucabanga ukuthi uphepha ngokweqile, ikakhulukazi uma abanye abantu emndenini wakho benza kanjalo, kufanele ukhulume nalokhu nodokotela wakho. Uma udokotela wakho futhi ekhathazekile, angase asebenze umsebenzi wokuqala wegazi noma akudlulisele ku-hematologist, udokotela ogxile ekuhluphekeni kwegazi.