Izimpawu Zingadlulela Ngokwemibangela Eyisisekelo
I-hemosiderosis ye-pulmonary isifo se-lungs esibangela ukuphuma kwegazi, noma ukushaya igazi, ngaphakathi kwamaphaphu, okuholela ekwakheni okungavamile kwensimbi. Lesi sakhi singabangela ukutholakala kwe-anemia nephaphu ebizwa ngokuthi i-pulmonary fibrosis. I-Hemosiderosis ingaba isifo esiyinhloko samaphaphu, noma isifo sesibili kuya kwesifo senhliziyo noma isistimu njenge-systemic lupus erythematosus.
Izifo eziyinhloko ngokuvamile zixilongwa ngenkathi zisencane.
Izimbangela ze-Hemosiderosis eyinhloko
I-hemosiderosis eyinhloko ingabangelwa yi:
- Isisu sokuphumula: I-pulmonary hemorrhage kanye ne-autoimmune disorder ezichaphazela izinso namaphaphu.
- I-Heiner syndrome: A hypersensitivity ubisi lwezinkomo.
- Idiopathic hemosiderosis: I-pulmonary hemorrhage engenawo amagciwane omzimba. Isiyaluyalu singase sihlotshaniswe nezinye iziphazamiso noma singazi imbangela eyaziwayo.
I-syndrome ye-goodpasture ivame ukubonwa kubantu abesilisa abadala ngesikhathi i-Heiner syndrome ivame ukutholakala ukuthi isencane. Idiopathic pulmonary hemosiderosis ingenzeka kubantu banobuphi ubudala kodwa ngokuvamile ixilongwa ezinganeni eziphakathi kweminyaka engu-1 no-7.
Izimpawu ze-Hemosiderosis
Izimpawu eziyinhloko ze-hemosiderosis ye-pulmonary zihlanganisa ukukhwehlela igazi (i-hemoptysis), ukuntuleka kwensimbi (i-anemia), kanye nezinguquko zamathambo emaphaphu. Izimpawu zingase ziqale kancane noma zivele ngokuzumayo. Uma isimo sikhula kancane, izimpawu ezifana nokukhathala okungapheli, ukukhwehlela okuqhubekayo, impumulo egijimayo, ukuvuthwa, nokukhuphuka ukukhula kungenzeka.
Uma ingane yakho ine-Heiner syndrome, ungase uphawule ukutheleleka kwezindlebe eziphakathi kwesikhashana, ukukhwehlela okuqhubekayo, impumulo engapheliyo, kanye nokuzuza kahle kwesisindo.
Ukuthola Ukuxilongwa
Uma udokotela wakho esola i-hemosiderosis, angase alandise ukuhlolwa kwegazi, amasiko asezingeni eliphansi , ukuguqulwa kwamanzi, nokuhlaziywa kwe-sputum egazi. Lezi zivivinyo zingasiza ukuhlukanisa phakathi kwe-hemosiderosis eyinhloko - I-syndrome ye-Goodpasture, i-Heiner syndrome, nesifo se-idiopathic - nesimo se-hemosiderosis yesibili.
Ukuhlolwa kwegazi kuzohlola i-anemia kanye nezinkomba zezinye izimo. Amazinga aphezulu e-immunoglobulin angabonisa i-Heiner syndrome ngenkathi ehamba ngamagciwane okulwa ne-GBM akhomba ukugula kwe-Wellpasture. Izivivinyo ze-Stool zizobuka igazi esitokisini, okungenzeka nge-hemosiderosis. I-urinalysis izophinde ifune igazi. Uma i-blood noma amaprotheni ekhona, ingabonisa ukuthi isifo esiyinhloko noma sesibili. I-x-ray yesifuba ingabuye ibe ithuluzi lokuxilonga eliwusizo.
Izinketho zokwelapha
Imithi yokwelapha i-Hemosiderosis igxile ekutheni imithi yokuphefumula, i-oksijeni, ukuguqulwa kwamagciwane kanye nokumpompela igazi ukuxazulula i-anemia enkulu. Uma ingane yakho ine-Heiner syndrome, lonke ubisi nemikhiqizo yobisi kufanele kususwe ekudleni kwabo. Lokhu kuphela kungokwanele ukususa noma yikuphi ukuphuma kwamaphaphu. Uma i-hemosiderosis ingenxa yesinye isifo, ukwelashwa kwesimo esibucayi kunganciphisa ukuphuma kwegazi. I-Corticosteroids ingasiza abantu abanezibonakaliso zabo kuphela eziphuma emaphashini abo, kungekho zinye izimbangela noma izifo eziyisibili. Imithi ye-immunosuppressive ingaba yindlela yokwelapha. Noma kunjalo, ucwaningo lusacubungula ukuthi lusebenza kangakanani isikhathi eside.
Ingabe kufanele, noma ingane yakho, ihlolwe ukuthi i-hemosiderosis, cishe uzodinga ukulandelelwa ukunakekelwa okuqhubekayo.
Kungenzeka ukuthi udokotela wakho uzofuna ukugcina iso lakho lokugcwalisa oksijini. kanye nomsebenzi wakho wephaphu neyezinso. Udokotela wakho angase futhi acele ukuhlolwa kwegazi njalo kanye nesifuba x-rays.
Umthombo:
I-Napchan, i-GD (2015). I-Hemosiderosis. I-Medscape. http://emedicine.medscape.com/article/1002002- ukubukwa kokubukwa