I-Lymphangiomatosis kanye ne-Lymph System

I-Lymphangiomatosis yisifo lapho izicubu eziningi (i-lymphangiomas) noma i-cysts zikhula khona ohlelweni lomzimba lymph . Nakuba lezi zicubu ezingenayo umdlavuza, zihlasela izicubu zomzimba futhi zibangela ubuhlungu, ukuphefumula ubunzima, nezinye izimpawu ezihlukahlukene kuye ngokuthi zivela kuphi. Ama-lymphangiomas angakhula emathanjeni, izicubu ezihlangene, nezitho zomzimba, futhi zingavimbela, zicindezele noma zibhubhise izicubu.

Yini eyenza i-lymphangiomatosis ingakaziwa.

I-Lymphangiomatosis ijwayele ukutholakala ezinsaneni nasezingane ezincane kepha zingase zenzeke kunoma yikuphi ubudala. Lithinta kokubili abesilisa nabesifazane bazo zonke izizinda ezihlukahlukene. Ngenxa yokuthi i-lymphangiomatosis ayidabuli futhi inzima ukuyihlolisisa kahle, aziwa ukuthi bangaki abantu abathintekayo kulo lonke izwe.

Izimpawu

Izimpawu ze-lymphangiomatosis zixhomeke lapho izidumbu zikhula khona emzimbeni.

Ngokuhamba kwesikhathi, isifo esisodwa noma ngaphezulu singashintshwa yizicubu ze-lymphangioma, eyaziwa ngokuthi isifo se-Gorham. I-Lymphangiomas ayikhuli ebuchosheni ngoba uhlelo lymph alufaki kulo.

Ukuxilongwa

Ukuxilongwa kwe-lymphangiomatosis kusekelwe ezimpawu kanye nokutholakala kwe-lymphangiomas eminingi emzimbeni. I-CT (i-computed tomography) ne-imagery magnetic resonance (MRI) isetshenziselwa ukuhlola lesi sifo. Isampula yamathambo (i-biopsy) ithathwa ukusiza ukuqinisekisa ukuthi izicubu ziyi-lymphangiomas.

Ukwelapha

I-Lymphangiomatosis ikhula kancane kancane. Njengoba izikhumba zikhula, zingabangela izimpawu ezinzima, ezinye zazo ezingase zisongele ukuphila, njengokubangela uketshezi ukuqoqa emaphashini avimbela ukuphefumula. Ukususwa kokuhlinzwa kwezicubu kungenzeka, kodwa ezinye izicubu zingase kube nzima ukususa ngokuphelele uma zisakazekile. Imithi ebizwa ngokuthi i-Intron A (interferon alfa), i-chemotherapy, noma imithi yokwelashwa ingase ibe usizo ekuphatheni lesi sifo. Ezinye zokwelapha noma ukuhlinza kungasiza ekunciphiseni ezinye izimpawu noma izinkinga ezibangelwa i-lymphangiomatosis. Isibonelo, ithubhu ingafakwa efubeni (thoracentesis) ukukhipha uketshezi oluthile, noma ukuhlinzwa kungenziwa emgodleni ukuze kukhululeke izinzwa eziphethwe.

Imithombo:

> "Mayelana ne-Lymphangiomatosis." I-Lymphangiomatosis & I-Gorham's Disease Alliance. 06 Sep 2007. Lymphangiomatosis & Gorham's Disease Alliance.

> Marom, Edith, Cesar Moran, & Reginald Munden. "I-Lymphangiomatosis Ejwayelekile." I-American Journal ye-Roentgenology 182 (2004): 1068.

> Rostom, A Y. "Ukwelashwa kwe-thoracic lymphangiomatosis." Archives of Diseases In Childhood 83 (2000): 138-139.