Ingabe Imithi Ehlukile Ingasiza Ukuphatha I-Dystrophy YamaMisipha?

Lezi zinketho ezihlukile ezingozi ezingase zibe yingozi zingenza umehluko omuhle

I-dystrophy yama-musculazi yiklasi lezinkinga zokuzibulala eziphilayo ezikhonjiswe ubuthakathaka obuqhubekayo, ukuchithwa, nokuguqulwa kwemisipha yamathambo elawula ukunyakaza. Ayikho ikhambi elaziwa le-muscular dystrophy, futhi iziguli zivame ukuphendukela emithi ehlukile ukusiza ukuphatha lesi sifo.

Izixazululo zemvelo zeDystrophy yamaMuscular

Kuze kube manje, izibalo ezimbalwa ziye zahlola ukusetshenziswa kwemithi ehlukile ekwelapheni i- muscular dystrophy .

Kodwa-ke, kunobunye ubufakazi bokuthi izinhlobo ezithile zokwelashwa okunye zingase zinikeze ezinye iziguli iziguli ze-muscular dystrophy, nakuba iningi lezifundo likhulile. Nakhu ukubuka okutholwe okutadisha okuyinhloko:

1) Izithako zokudla

Ucwaningo oluthile oluncane lubonisa ukuthi izithako zokudla zingase zizuze iziguli ze-muscular dystrophy. Isibonelo, isifundo se-2006 esivela ku- American Journal of Clinical Nutrition sathola ukuthi ukuxhaswa ngama-amino acids kwasiza ekuvimbeleni ukungcoliswa kwamaprotheni omzimba wonke (isibonakaliso se-Duchenne muscular dystrophy). Ucwaningo lwabandakanya abafana abangama-26 abane-Duchenne muscular dystrophy, ngamunye wabo owaphethwe ama-amino acid supplement izinsuku ezingu-10.

Ucwaningo lokuqala lubonisa ukuthi i-creatine (i-amino acid esiza ukuhlinzeka ngamaseli omzimba ngamandla) ingasiza ekuphatheni i-dystrophy ye-muscular. Kodwa-ke, ocwaningweni luka-2005 lwabafana abangama-50 abane-Duchenne muscular dystrophy (eshicilelwe ku- Annals of Neurology ), ososayensi bathola ukuthi ukwelashwa kwezinyanga eziyisithupha nama-creatine supplements kwahluleka ukuthuthukisa amandla omzimba kwabahlanganyeli.

2) Qigong

I-Qigong ingathuthukisa inhlalakahle kubantu abane-dystrophy yemisipha, ngokusho kocwaningo lwango-2004 olushicilelwe ukukhubazeka nokuvuselelwa. Ucwaningo lwabandakanya iziguli ezingama-28 ezine-muscular dystrophy, ezinye zazo ezabika ukuthuthukiswa kwengqondo engokwengqondo, ngokomzimba nangokwengqondo (ngaphezu kokunciphisa amazinga okucindezeleka) ngemva kokusebenzisa i-qigong.

3) Ithi elihlaza

Itiye elihlaza lingase lizuze abanye abantu abane-Duchenne muscular dystrophy, ngokusho kocwaningo olusencwadini eyamemezelwa e- American Journal of Physiology: Cell Physiology ngo-2006. Ekuhlolweni kwamagundane, abacwaningi bathola ukuthi i-epigallocatechin gallate (i-antioxidant etholakala itiye elihlaza) siza ukuvikela ukuhlukunyezwa kwemisipha ebangelwa ukuxoshwa kwemisipha. Kodwa-ke, kusheshe ukutshela ukuthi itiye elihlaza lingaba nomphumela ofanayo kubantu.

Amafomu e-Muscular Dystrophy

Kunezifo ezingaphezu kuka-30 ezihlukaniswa njenge-dystrophy yemisipha. Ngenkathi ezinye izinhlobo zivela ebuntwaneni noma ebuntwaneni, ezinye azibonwanga kuze kube seminyaka ephakathi noma kamuva ekuphileni. Izinto ezifana nobudala bokuqala, ubukhulu obuthakathaka be-muscle, kanye nokukhula kwentuthuko kuyahluka kuye ngokuthi uhlobo lwe-muscular dystrophy.

Ifomu elivamile kakhulu le-muscular dystrophy liyaziwa ngokuthi iDuchenne muscular dystrophy. Ethinta kakhulu abafana, i-Duchenne i-dystrophy yemisipha ibangelwa ukungabi khona kwe-dystrophin (iphrotheni edlala indima ebalulekile ekugcineni ubuqotho be-muscle). I-dystrophy ye-duchenphy i-duchenne ivela phakathi kweminyaka emithathu kuya kwemihlanu, ngokuvamile ishiya iziguli ezingakwazi ukuhamba ngezineminyaka engu-12.

Ezinye izinhlobo ze-muscular dystrophy zihlanganisa i-facioscapulohumeral muscular dystrophy (ekhonjiswe ubuthakathaka obuqhubekayo emisipha ebusweni, izingalo, imilenze, nasemaphandleni nasesifuba) kanye ne-myotonic muscular dystrophy (ephawulwe ama-spasms ahlala isikhathi eside, ama-cataracts, ukungavamile komzimba, nokuphazamiseka kwe-endocrine ).

Izimpawu Nezibonakaliso Ze-Dystrophy Yama-Muscular

Izimpawu ze-dystrophy ye-muscular ziyahlukahluka kuye ngokuthi uhlobo lwe-dystrophy ye-muscular. Ngokwesibonelo, izibonakaliso nezimpawu ze-Duchenne muscular dystrophy zingabandakanya ukubambezeleka kwezimoto, ukuwa njalo, ubuthakathaka emiphakathini engezansi, imisipha yamathole amakhulu nokukhubazeka kwengqondo. I-myotonic muscular dystrophy, okwamanje, ingabangela izimpawu ezinjengobuthakathaka emasipha ebusweni (kanye nasezingalweni nasemilenzeni nasezintanjeni eziphazamisa inkulumo nokugwinya), ukujula, izinkinga zokuphefumula, nokukhubazeka kwenhliziyo ekukhuleni kwabantu abadala.

Ukwelashwa kwe-Muscular Dystrophy

Ukwelashwa kwe-dystrophy ye-muscular ngokuvamile kuhlanganisa ukwelashwa ngokomzimba, ukwelapha okuphefumula , ukwelashwa kwenkulumo , imishini yamathambo asetshenziselwa ukwesekwa, nokuhlinzwa okulungiswa komzimba wama-orthopedic .

Imithi ethile isetshenziselwa ukwelapha i-dystrophy ye-muscular, kuhlanganise ne-corticosteroids (ukuphuza ukuguquka kwemisipha), i-anticonvulsants (ukulawula ukuqubuka nokunye kwemisipha), ama-immunosuppressants (ukulibalaza umonakalo othile emangqamuzaneni abulala ama-muscle), nemithi elwa namagciwane (ukulwa nezifo zokuphefumula) .

Kwezinye izimo, iziguli ze-muscular dystrophy zingadinga umoya wokuphuza umoya (ukuphatha ubuhlungu obuthakathaka bokuphefumula) kanye / noma i-pacemaker (ukuphatha ukukhubazeka kwenhliziyo).

Ukusebenzisa Imithi Ehlukile KwamaMody Dystrophy

Uma ucabangela ukusetshenziswa kwanoma yiluphi uhlobo lwemithi ehlukile ekwelapheni i-muscular dystrophy, kubalulekile ukubonana nodokotela wakho (noma isazi sesazi somntwana wakho) ngaphambi kokuqala ukwelashwa. Ukuzibulala ngokwemithi ngamanye amayeza nokugwema noma ukubambezela ukunakekelwa okujwayelekile kungaba nemiphumela emibi.

> Imithombo:

> Dorchies OM, Wagner S, Vuadens O, Waldhauser K, > Buetler > TM, Kucera P, Ruegg UT. "I-Green Tea Extract and Its Poly Polyphhenol (-) - I-Epigallocatechin Gallate Ithuthukisa Umsebenzi We-Muscle Ngomfanekiso Wemouse Ye-Duchenne Muscular Dystrophy." Am J Physiol Cell Physiol. 2006 Feb; 290 ( > 2): C616-25 >.

> Escolar DM, Buyse G, Henricson E, Leshner R, Florence J, Mayhew J, Tesi-Rocha C, Gorni K, Pasquali L, Patel KM, McCarter R, Huang J, Mayhew T, Bertorini T, Carlo J, Connolly AM , UClemens PR, Goemans N, Iannaccone ST, Igarashi M, Nevo Y, Pestronk A, Subramony SH, Vedanarayanan VV, Wessel H; Iqembu le-CINRG. "I-CINRG Isivivinyo Esilawulwe Ngokungahleliwe Sokudala Ne-Glutamine ku-Duchenne Muscular Dystrophy." Ann Neurol. 2005 Jul; 58 (1): 151-5.

> Felber S, Skladal D, Wyss M, Kremser C, Koller A, Sperl W. "Izidakamizwa ze-Oral Creating in Duchenne Muscular Dystrophy: Isifundo se-Spectroscopy Clinic ne-31p Magnetic Resonance." I-Neurol Res. 2000 Mar; 22 (2): 145-50.

> I-E E, i-Eléouet-Da Violante C, > i-Daubrosse > C, i-Gottrand F, i-Rigal O, i-Fontan JE, i-Cuisset JM, i-Guilhot J, i-Hankard R. "I-Oral Glutamine ne-Amino Acid Supplementation Ivimbela Ukubola Kweprotheyini Yonke Yezingane Ezine-Duchenne I-Dycular Dystrophy. " I-Am J Clin Nutr. 2006 Apr; 83 (4): 823-8.

> Nabukera SK, PA Romitti, Campbell KA, Meaney FJ, Caspers KM, Mathews KD, Hockett Sherlock SM, Puzhankara S, Cunniff C, Druschel CM, Pandya S, Matthews DJ, Ciafaloni E, Starnet M. "Ukusetshenziswa kokuhambisana nokunye Imithi Ngamadoda Nge-Duchenne noma i-Becker Muscular Dystrophy. " J Child Neurol. 2011 Dec 7.

> I-National Institute of Neurological Disorder and Stroke. "Ikhasi Lolwazi Lwe-Muscular Dystrophy." Ngo-Novemba 14, 2011.

> Pearlman JP, i-Fielding RA. "Yakha i-Monohydrate njenge-Aid Therapeutic in Dystrophy Muscular." Isitifiketi seNutriti 2006 Feb; 64 (2 Pt 1): 80-8.

> Wenneberg > S, Gunnarsson LG, Ahlström G. "Ukusebenzisa Uhlelo Lokuzivocavoca Novel for Iziguli With Muscular Dystrophy. Ingxenye I: Isifundo Esifanele." Ukubuyisela kabusha ukukhubazeka. 2004 Meyi 20; 26 (10): 586-94.