I-cardiomyopathy ye-hypertrophic (HCM) ingenye yezimo zenhliziyo ezihlobene nokufa okungazelelwe kubadlali abasha. Eqinisweni, i-HCM ingenye yezinkinga ezivamile zengqondo zofuzo, ezithinta umuntu kubo bonke abantu abangu-500. E-United States, i-HCM ibhalwa ngamaphesenti angama-36% okufa okuphazamiseka okubuhlungu okuvela kubadlali abasha. Ngaphezu kwalokho, ngaphezu kwengxenye yokufa okungazelelwe okubangelwa yi-HCM kwenzeka ema-Afrika aseMelika.
Abantu abane-HCM ngokuvamile abavinjelwe kuyo yonke imisebenzi yezemidlalo, nakuba bevinjelwe.
Noma ubani onayo i-HCM udinga ukwazi ngengozi yokufa okungazelelwe, futhi kufanele aqaphele ukuthi izincomo zokuqeqeshwa kochwepheshe zivumelane kufanele zilandelwe abantu abanalo lesi simo.
Yikuphi Ngokuqondile Ukuthi I-Cardiomyopathy I-Hypertrophic?
I-HCM yisimo senhliziyo esimelwe ukuqina okungavamile kwenhliziyo yesisu, isimo esibizwa ngokuthi i-hypertrophy. I-hypertrophy ingabangela izinkinga eziningana. Iveza "ukuqina" ngokweqile kwi-ventricle yesokunxele yenhliziyo. Kungabangela ukuvinjelwa okuyingxenye ekugezeni kwegazi engxenyeni engakwesokunxele, okwenza isimo esifana ne- aortic stenosis . I-HCM ihlobene nokusebenza okungavamile kwe- valve mitral.
Lezi zici ze-HCM zingaholela ekusebenziseni kwe-diastolic nokuhluleka kwenhliziyo ye-diastolic , noma ukuhlukunyezwa kwe-cardiomyopathy nokunye okuhlukahlukene "okuvamile" kokuhluleka kwenhliziyo .
Kungabangela ukuphindaphindiwe kwe-mitral , okungabangela noma ukuhluleka kwenhliziyo.
Kodwa imiphumela evelele kakhulu ye-HCM yukuthi ingenza imisipha yenhliziyo ijwayele ukuthuthukisa i- tricycardia ye- ventricular kanye ne- fibrication ye-ventricular, i- arrhythmias engabangela ukufa okungazelelwe. Nakuba lezi zi-arrhythmias zingenzeka nganoma isiphi isikhathi, zivame kakhulu ukuba zenzeke ngesikhathi sokuzivocavoca okukhulu.
Ngeshwa, ukufa okungazelelwe kungase kube ukubonakaliswa kokuqala kwe-HCM, ikakhulukazi kubadlali abasha. Ukuhlolwa kwansuku zonke nge- ECG , noma kangcono, okwamanje, i-echocardiogram, izokwethula inkinga kubagijimi abaningi ngaphambi komcimbi osongela impilo - kodwa ukuhlolwa okunjalo kwenzelwe ukuthi kubizwe izindleko.
Noma kunjalo, noma yimuphi umdlali osemusha oye waba nelungu lomndeni afe ngokuzumayo, noma ngubani onomlando womndeni we-HCM, udinga ukuhlolwa ngalesi simo. Futhi uma i-HCM itholakale, kufanele ilandele izincomo zohlelo olwamukelekile olwamukelekile lwabadlali abasha abane-HCM.
Yiziphi Izincomo Ezijwayelekile Zokuzivocavoca Zabadlali Abasha Ne-HCM?
Ngokomhlangano we-Bethesda we-36 we-36 we-Eligibility Izincomo Zabadlali Abanokuncintisana Nezinkinga Zezinhliziyo Zegazi, abagijimi abane-HCM akufanele babambe iqhaza emidlalweni enokuncintisana kakhulu, ngaphandle kwemidlalo ephansi (njenge bowling noma igalofu).
Labo abane-HCM abangekho eqenjini elihleliwe kodwa bahlanganyele emidlalweni ngezikhathi ezithile kufanele futhi bagweme imidlalo yemidlalo ephakeme kakhulu njengehokkey, basketball, kanye ne-tennis yokudlala.
Ezinye zezemidlalo ezibandakanya ukulinganisela okulinganiselayo, nemidlalo eminingi enamandla kakhulu, ingahle ijabule ngokulinganisela.
Lezi zihlanganisa igalofu, i-tennis kabili, ukubhukuda nokubhukuda.
Imithombo:
Maron, BJ, Ackerman, MJ, Nishimura, RA, et al. Umsebenzi we-4: I-HCM nezinye izinto ze-Cardiomyopathies, i-Mitral Valve Prolapse, i-Myocarditis, ne-Marfan Syndrome. J Am Coll Cardiol 2005; 45: 1340.