Ukwazi Isazi Sakho
Umonakalo wokulimala obangelwa izifo eziphefumula ngokuphindaphindiwe yiyona imbangela eholela ekufeni kwabantu abane- cystic fibrosis . Ukukwazi ezinye zezifo ongase ubhekane nazo kungakusiza ukuba ulungiselele izinselelo ezizayo futhi uhlele amasu okunciphisa izingozi zakho. Izilwane ezilandelayo aziveli kakhulu kubantu abanempilo, kodwa ziyinkinga kakhulu kulabo abaneCF.
I-Aspergillus
I-Aspergillus iyi-fungus eyenzeka ngokuvamile emvelweni, ngakho kunzima uma kungenakwenzeka ukugwema ukuxhumana naye. Kubantu abaningi, i- Aspergillus ayinabungozi kepha ngamaphesenti angu-15 abantu abane-cystic fibrosis, ingaholela esimweni esisongela ukuphila esibizwa ngokuthi i-allergenic bronchopulmonary aspergillosis (ABPA).
Kulesi simo, uzoba ne- Aspergillus emashumini akho emaphashini kepha akusiyo ingozi. Esikhundleni salokho, kubangelwa ukusabela ngokuzivikela komzimba ngama-antibodies kanye namaseli omzimba omzimba, okwenza i-eosinophilic pneumonia. Izimpawu zibandakanya ukukhwehlela ngamanqamu aluhlaza okweluhlaza noma obomvu ku-sputum yakho. Uzothola izimpawu ezifana ne-asthma ezifana nokuvinjelwa kwesondo nokuhamba emoyeni. Ezimweni ezimbi, ungase ube nomkhuhlane, ikhanda, nokulahlekelwa ukudla. Kutholakale ukuhlolwa kwe- Skin prick ye- Aspergillus antigen kanye nokuhlolwa kwegazi kwe- Aspergillus precipitins kanye ne-IgE antibodies kanye ne-X-ray noma CT.
Ukwelashwa kunomlomo we-prednisone womlomo njengoba i-corticosteroids engenayo ifakwe kahle ku-ABPA. Uma i-ABPA iphikelela, ungase uphathwe ngesidakamizwa esiphikisayo. Iziguli zilandelwa ngesifuba se-X-rays, ukuhlolwa komsebenzi we-pulmonary, kanye nokuhlolwa kwelebhu njengomonakalo wamaphaphu kungase kuqhubeke kwenzeke ngaphandle kokushintsha kwezibonakaliso. Kukhona ingozi yokukhuliswa okuqhubekayo kwe-airways ephakathi, eyaziwa ngokuthi i-bronchiectasis, nokuqeda amaphaphu.
Pseudomonas aeruginosa
Ingaphezu kwesigamu sabo bonke abantu abane-cystic fibrosis bayolwa nokutheleleka kwamapayipi okubangelwa amagciwane Pseudomonas aeruginosa ngesikhathi esithile ekuphileni kwabo. Eqinisweni, yiyona engokwemvelo evame ukwenzeka ku-CF-ehlobene ne-lung lung infection. Ngakho-ke, i- P. aeruginosa nayo ibhaktheriya enesibopho sokufa kwabantu abaningi abane-CF.
I-P. aeruginosa yi-bacteria evamile etholakele nxazonke emhlabathini, emanzini, emanzini, nakweminye indawo enomanzi, ngakho-ke ayikwazi ukugwema. Kunzima ukuqeda lapho kuhlasela umzila wokuphefumula.
Ifomu ephikisiwe ye-tobramycin yama-antibiotic, eyaziwa ngokuthi i-TOBI, isetshenziselwa ukwelapha izifo ezingapheli ze- Pseudomonas kubantu abane-cystic fibrosis. I-powder eyomile TOBI Podhaler nayo yasungulwa.
Burkholderia cepacia
I-Burkholderia cepacia , eyayivame ukubizwa nge- Pseudomonas cepacia , iyingozi engavamile kodwa ephawulekayo kubantu abane-cystic fibrosis. Ngenkathi izinkinga ezithandekayo ukuthi awusoze wahlangana noBurkholderia cepacia , kufanele ube nokuqonda okuyisisekelo ukuthi ungubani nokuthi unganciphisa kanjani ingozi yokuyithola.
Ngenkathi isemvelo, izinkinga ezithinta abantu manje ziboniswa ukuthi zisakazwa kusuka komuntu kuya komuntu. Kungenza i-colonize amaphaphu futhi ibangele ukutheleleka okuye kwancipha kancane kancane umsebenzi wamaphaphu. Ingabuye isakaze kuwo wonke umzimba odala i-cepacia syndrome ngokuwohloka okusheshayo kwamaphaphu. Lokhu kungaholela ekufeni. Iphathwa ngethrashini yokuhlanganiswa ngoba ingamelana nama-antibiotic amaningi.
MRSA
I- Staphylococcus aureus engamelana ne-Methicillin (MRSA ), iba yinkimbinkimbi evame kakhulu kubantu abane-cystic fibrosis. I-MRSA itholakale esikhumbeni, ngamanxeba, emcintweni, nakwezinye izingxenye zomzimba kodwa amaphaphu yindawo ejwayelekile kakhulu yokutheleleka kwe-MRSA kulabo abane-CF.
I-MRSA isakazwa ngokuxhumana ngqo nangokungaqondile futhi ingatholakala emphakathini noma esibhedlela. Ukusebenzisa ukulawula ukutheleleka okuhle kungasiza ukunciphisa ingozi.
> Imithombo:
> Gautam, V .; Singhal, L .; noRay, P. "I- Burkholderia cepacia complex: Beyond pseudomonas ne-acinetobacter." I-Ind J Med Microb. 2011; 29 (1): 4-12.
> I-Ortega VE. I-Asergic Bronchopulmonary Aspergillosis (ABPA). I-Merck Manual Professional Version. http://www.merckmanuals.com/professional/pulmonary-disorders/asthma-and-related-disorders/allergic-bronchopulmonary-aspergillosis-abpa#.
> Ramphal R. Izifo Ngenxa ye-Pseudomonas Species and Related Organisms. Ku: Kasper D, Fauci A, Hauser S, Longo D, Jameson J, Loscalzo J. eds. I-Harrison's Principals of Internal Medicine, 19e . ENew York, NY: McGraw-Hill; 2015.