I-Sweet's syndrome yisimo esingavamile esibandakanya ukuqhuma okubuhlungu, ngokuvamile kanye nomkhuhlane. Ukuqhuma kuqhuma kakhulu esikhunjeni sezingalo, intamo, ikhanda nesiqu. Isizathu se-Sweet's syndrome asikwazi ngokugcwele, kodwa kunezimo eziningana ezijwayelekile lapho kuthiwa zikhona khona.
Kwabanye abantu, kubonakala sengathi kubangelwa ukutheleleka, noma kungenzeka kuhlotshaniswa nesifo sofuba nesibindi nokukhulelwa; kwezinye, kungase kuhlotshaniswe nomdlavuza, ngokuvamile uvame uketshezi lwe-myelogenous leukemia; kanti abanye banesimo esibangelwa izidakamizwa se-Sweet's syndrome.
I-Sweet's syndrome ingase ihambe yodwa, kodwa ivame ukuphathwa ngamaphilisi e-corticosteroid, njenge-prednisone. I-Sweet's syndrome yaziwa nangokuthi i-acute febrile neutrophilic dermatosis noma isifo se-Gomm-Button.
Izimpawu
I-Sweet's syndrome ibhalwe izimpawu ezilandelayo:
- Fever
- Amabhande amancane obomvu ezandleni zakho, entanyeni, enhloko noma esihlahleni esheshayo, esakazeka emaqenjini amabi kuze kube ngamasentimitha noma ububanzi
- I-Rash ingavela ngokushesha ngemuva komkhuhlane noma ukutheleleka okuphezulu kokuphefumula .
Izinhlobo ze-Sweet's Syndrome
Lesi simo sibonakala ngezinhlobo ezintathu ezahlukene:
Zasendulo
- Ngokujwayelekile kwabesifazane abaneminyaka engama-30 kuya kweyama-50
- Ngokuvamile kulandelwa ukutheleleka okuphezulu kokuphefumula
- Kungase kuhlotshaniswe nesifo sofuba sesibindi nokukhulelwa
- Cishe i-1/3 yeziguli zinokuphindaphindiwe kwe-Sweet's syndrome
I-Malignancy-Associated
- Kungenzeka kube komunye umuntu owaziwa ukuthi unomdlavuza
- Kungenzeka kube kumuntu onomdlavuza wegazi noma isisu esiqinile ngaphambili angatholakali
- Ngokuvamile kuvumelana ne- acute myelogenous leukemia , kodwa ezinye izifo zomdlavuza kungenzeka, njengebele noma ikholoni
Ukudakwa kwezidakamizwa
- Okuvame ukuvela ezigulini eziye zaphathwa nge-granulocyte-colony eshukumisayo isici esinikezwe ukuthuthukisa amangqamuzana amhlophe egazi
- Nokho, eminye imithi ingase ihlotshaniswe; izidakamizwa ezixhunywe ku-Sweet's syndrome zifaka i-azathioprine, ama-antibiotic athile kanye nezinye izidakamizwa eziphikisana nezidakamizwa
Ukubandakanya Ngaphandle Kesikhumba
Ngenxa yokungabi nalutho kwe-Sweet's syndrome, idatha elinganiselwe, nemibandela eminingi engase ibe ngaphansi, akuzona zonke iziphumo ezixhumene nalesi sifo ezibangelwa yi-syndrome ngokwayo.
Lokho kusho ukuthi i-Sweet's syndrome kucatshangwa ukuthi ingabandakanya ezinye izicubu nezitho, ngaphezu kwesikhumba. Ukuhlanganiswa kwamathambo namalunga kuye kwabhalwa, njengoba kuhileleke ohlelweni lwezinzwa-i-"neuro-Sweet". Amehlo, izindlebe, nomlomo nakho kungathinteka. Ama-bumps obomvu amancane angadlulisa endlebeni yangaphandle, angene emgodini nase-eardrum. Amehlo angabandakanywa, ngokuvuvukala, ubomvu, nokuvuvukala. Izilonda ngolimi, ngaphakathi emathunjini nasezinsini zingase zikhule. Ukuvuvukala kanye / noma ukukhuliswa kwezitho zangaphakathi zesisu nesifuba nakho kubikiwe.
Izingozi Zezingozi
I-Sweet's syndrome iyinto engavamile kakhulu, ngakho-ke izici zayo eziyingozi azikhulumi kahle njengoba zingase zibe ezinye izifo. Ngokuvamile, abesifazane banamathuba amaningi okuba ne-Sweet's syndrome kunamadoda, futhi, nakuba abadala asebekhulile ngisho nezinsana zingakha i-Sweet's syndrome, abantu abaphakathi kweminyaka engama-30 no-60 yiqembu elidala elikhuthele.
Ukwengeza, izimo ezichaza izinhlobo ezibalwe ngenhla zingabhekwa njengengozi, ngakho-ke i-Sweet's syndrome ngezinye izikhathi ihlotshaniswa nomdlavuza, ingahle ihlotshaniswe nokuzwela emithini ethile, ingase ilandele ukutheleleka okuphezulu kokuphefumula (futhi abantu abaningi babika ukuthi bane-flu- njengezimpawu ngaphambi kokuba kuvele ukuqhuma) futhi kungase kuhlotshaniswe nesifo sofuba sesibindi, esihlanganisa isifo se-Crohn nesifo sofuba esiswini.
Abanye besifazane baye bahlakulela i-Sweet's syndrome ngesikhathi sokukhulelwa.
Ukuxilongwa
I-Sweet's syndrome ingase isolwe noma ibonakale ngokuhlola ukuqhuma, kodwa-ke, ukuhlolwa okuhlukahlukene kuyadingeka ukuthi kutholakale ukuhlolwa kanye / noma ukulawula ezinye izimbangela.
Isampula segazi lakho lingathunyelwa ebhokisithri ukuthola inombolo enkulu engavamile yamaseli amhlophe wegazi noma ukutholakala kwezifo zegazi.
I-skin biopsy, noma ukususwa kweqephu elincane lesikhumba esithintekile ukuhlolwa ngaphansi kwe-microscope, kungenziwa. I-Sweet's syndrome inezinhlobo ezingavamile: amaseli avuthayo, amangqamuzana amhlophe ahlanzekile egazi we-neutrophil, angena ngaphakathi futhi ahlala egciniwe elingenhla kwengxenye ephilayo yesikhumba.
Okuphawulayo, ama-agent angenelele angaveza okufanayo okwenziwe esikhumbeni, ngakho-ke kuye kwaphakanyiswa ukuthi kungaba nokuhlakanipha ukuba nesampuli ehlolwe amabhaktheriya, isikhunta kanye namagciwane.
Ukuthola okutholakala kunazo zonke ezitholakala ematokisini ane-Sweet's syndrome kuphakanyiswe amangqamuzana egazi amhlophe nama-neutrophils egazini kanye nesilinganiso se-erythrocyte sedimentation ephakeme, noma i-ESR. Lokho kusho ukuthi inani eliphakeme legazi elimhlophe alitholakali njalo kuzo zonke iziguli ezine-syoprome eziqinisekisiwe ze-biopsy.
Ukwelapha
I-Sweet's syndrome ingase ihambe yodwa, ngaphandle kokwelapha, noma ngabe ukwelapha kuyasebenza futhi ngokuvamile kusebenza ngokushesha. Ukungabonakali, ukuqhuma kungadlulela amasonto kuya ezinyangeni. Imithi ejwayelekile kakhulu esetshenziselwa i-Sweet's syndrome yi- corticosteroids . I-corticosteroids yomlomo, njenge- prednisone , ingahle isetshenziswe, ikakhulukazi uma unezindawo ezimbalwa zesikhumba ezithintekile. Lezi mithi ziyi-systemic, okusho ukuthi ziyahamba kuwo wonke umzimba futhi hhayi nje isikhumba.
Ezinye izinhlobo ze-steroids ezifana nama-creams noma amafutha okugcoba ngezinye izikhathi zisetshenziselwa ukuhlukumeza okuncane, okuncane kakhulu. Uma umuntu one-Sweet's syndrome engavumi ukubekezelela i-corticosteroids yesimiso noma enezimo ezimbi nge-corticosteroids yesikhathi eside, kuneminye imithi engasetshenziswa, njenge-dapsone, iodide ye-potassium, noma i-colchicine.
Iziguli ezine-Sweet's syndrome zingase zenze izinkinga ngenxa yokubandakanyeka kwesikhumba, izimo ezihambisana ne-Sweet's syndrome, noma kokubili. Ukwelashwa kwama-antimicrobial kungasetshenziswa uma izilonda zesikhumba ezivela ku-rash zisengozini yokutheleleka okwesibili.
Ukunakwa kunoma yiziphi izimo ezihambisana ne-Sweet's syndrome kungase kube yingxenye ebalulekile yokwelashwa kwe-Sweet's syndrome, ngokwayo. Isibonelo, izimpawu ezihambisana nesifo ngezinye izikhathi zikhumbuza ukwelashwa noma ukwelashwa kwesifo esibulalayo.
Izwi elivela
Imithi efana ne-corticosteroids ingase ihlinzeke ukukhululeka kwi-syndrome, kodwa ukunakekelwa kwezimo ezihambisanayo kungase kubalulekile. Uma une-sweet's syndrome ekhishwa izidakamizwa, uma isidakamizwa se-causative sesishiywe, lesi sifo ngokuvamile, kodwa hhayi ngaso sonke isikhathi, sithuthukisa futhi sizithumela ngokuzenzakalelayo.
Ngokusobala, akuwona wonke umuntu onesifo sika-Sweet's umdlavuza; futhi, ekutadisheni nabantu abangu-448 abane-Sweet's syndrome, amaphesenti angu-21 kuphela (noma abantu abangu-96 ku-448) atholakale enesifo sofuba noma isifo esiqinile. Kodwa-ke, inothi ukuthi i-Sweet's syndrome ngezinye izikhathi ingabangela ukutholakala komdlavuza ongaziwa-futhi nokuthi ukuphindaphinda kwesifo sika-Sweet's syndrome esihlotshaniswa nokulimala kungabonisa ukubuyela emuva komdlavuza.
> Imithombo:
> Cohen PR. I-Sweet's syndrome - ukubuyekezwa okuphelele kwe-acute febrile neutrophilic dermatosis. I-Orphanet J Rare Dis. 2007; 2: 34. i-doi: 10.1186 / 1750-1172-2-34.
> Hussein K, Nanda A, Al-Sabah H, i-Alsaleh QA. I-Sweet's syndrome (i-acute febrile neutrophilic dermatosis) ehlotshaniswa ne-adenocarcinoma ye-prostate ne-transitional cell carcinoma ye-vestiva. J Eur Acad Dermatol Venereol. 2005; 19: 597-599.
> I-Sweet RD. An acute febrile neutrophilic dermatosis. Br J Dermatol. 1964; 76: 349-356. i-doi: 10.1111 / j.1365-2133.1964.tb14541.x.