Funda kabanzi mayelana nezinkinga ezihlukile, izimo ze-Prune Belly Syndrome
I-Prune Belly syndrome, eyaziwa nangokuthi i-Eagle-Barrett noma i-triad syndrome, iyisici esithile sokuzalwa esinezinhlu ezihlukile zezinkinga ezingokomzimba ezizalwa yingane. Lezi zinkinga:
- Imisipha yomzimba engaphambili komzimba ibuthakathaka noma ilahlekile
- Izingxenye ze-urinary tract zakha ngokungavamile. Lokhu kuhlanganisa ukuvuthwa okungavamile (ukuhlenga) kwamatayipi omchamo, ukuqoqa umchamo emadayeni adlula umchamo kusuka ezinseni kuya kwesinye, kanye / noma ukubuyela emuva komchamo kusuka kwesigqila ukuya emathanjeni nasemidayeni (ebizwa ngokuthi i-reflux vesicoureteral).
- Emadodeni (amacala angu-95%), ama-testes ahlala phezulu ngaphakathi kwesisu futhi angenanga esiqongweni se-scrotum.
Kungase kube nezinye izinkinga ezingokwenyama ebusaneni, njengesivunguvungu somgogodla, ukuchithwa kwe-hip, clubfoot, izinkinga zokuphefumula noma zenhliziyo, nezinkinga zemathunjini.
Izimbangela ze-Prune Belly Syndrome
Isizathu se-syndrome asiziwa, kodwa abacwaningi bakholelwa ukuthi ukuphazanyiswa kokukhula kwe-fetus kubangela ukuthi izinkinga zikhule. Kucatshangwa ukuthi into ethile ivimbela ingxenye yengane ye-fetus, futhi lokhu kubangela ezinye izingxenye zepheshana ukuba zikhule ngendlela engavamile. I-Prune Belly syndrome kwenzeka ku-1 ku-40,000 ukuzalwa okuphilayo e-US
Ukuhlonza Isimo
I-ultrasound ngesikhathi sokukhulelwa ngezinye izikhathi ingase ibone ukuthuthukiswa okungavamile kwesigcawu sesinye nesisu. Ngenkathi i-fetus ikhula, i-fluid iqala esiswini sayo, elula nakakhulu. Umswakama uphinde uvuselelwe ngaphambi kokuzalwa, ngakho ngesikhathi sokuzalwa, usana luba nesisu esiswini noma senziwe ngobuningi (ngaleyo ndlela igama elithi "lesi-prune belly").
Ngemuva kokubeletha, i-ultrasound kanye ne-x-ray inganquma ukuthi yiziphi izinhlobo ze-urinary tract ezingajwayelekile. I-Prune Belly syndrome ivame ukubonakala yi:
- Eminye imisipha noma emathunjini amaningi isuke ingekho. Lokhu kunikeza ukubukeka okunobunjiwe noma okunjenge-prune.
- Nakuba izinhlanganisela zomzimba emathanjeni zingase zibe khona, izihlungulu zincane futhi zincipha phezu kwesihenya.
- Udonga lwamathumbu lunomzimba omncane, isisu esisodwa sikhombisa ukuthi sikhulu futhi sikhululekile, kanti amathumbu angabonakala ngodonga oluncane lwesisu.
- Izikhumba zesikhumba zibonakala ziphuma ebhokisini lesisu noma ziwela ngapha kwesisu.
- I-crease evela enkabayeni eya endaweni yezokusakaza kungenzeka ngezinye izikhathi ibe khona futhi ngezinye izikhathi inkinobho yesisu ingase ixhunywe esithombeni ngokusebenzisa i-canal (urachus) noma i-cyst.
- Ukushaywa kwezimbambo noma ukugcoba kwesifuba kungabangela ukuba isifuba siphumelele ezinganeni ezine-syndrome.
- Isibilini esikhulisiwe sikhona cishe kuzo zonke izimo.
Ngeshwa, i-Prune Belly syndrome ingaba nemiphumela emibi kakhulu kosana. Izibalo zibonisa ukuthi izingane ezingama-20% ziyafa ngaphambi kokuzalwa, kanti ama-30% abulawa ngezinkinga zezinso neminyaka emibili yokuqala yokuphila. Kule 50% esele yezinsana, kunezinhlobo ezihlukahlukene zezinkinga zomchamo.
I-Prune Belly Syndrome ivame ukutholakala ngaphansi kwamagama ahlukahlukene ahlukahlukene, njengokungasebenzi kwesisu esiswini, ukungahambi kahle kwesisu semisipha yomzimba, ukuntuleka kwesisu esiswini, i-Eagle-Barrett syndrome, i-Obrinsky syndrome noma i-triad syndrome.
Ukwelashwa kwe-Eagle-Barrett
Akukho ukwelashwa kwe-Eagle-Barrett (prune belly syndrome), kodwa ukulungiswa komgudu wokuvuthwa kungenziwa.
Abanye odokotela abahlinzayo bazama ukulungisa izinkinga ezinganeni ngaphambi kokuba zizalwe, kodwa lokhu kuye kwaba nemiphumela ehlangene. Izingane ezivame ukutheleleka kwezidakamizwa zamagciwane zinikezwa ama-antibiotic kanye nokuhlinzwa okuvimbelayo kungaletha ama-testes omfana angene esiqwini sakhe.
Ngezinye izikhathi naphezu kokwelashwa okungcono, izinso zomntwana zizoyeka ukusebenza (ukwehluleka kwenqunu). Ukwelashwa kwalokhu kungaba i- dialysis noma ukufakelwa kwezinso zezinso.
Izindlela zokuhlinzeka kangcono, ikakhulukazi ukusebenzisa i-laparoscopy, zizokwenza imisebenzi yokulungisa edingekayo yengane encane ne-Prune Belly syndrome nzima. Njengoba okunye okufundwayo nge-syndrome, ukwelashwa kungathuthukiswa futhi izingane zisiza ekuphile isikhathi eside.
Imithombo:
I-Prune Belly Syndrome Network. Mayelana ne-Prune Belly.
UFranco, I. (2001). I-Prune Belly syndrome. I-eMedicine ifinyelele ku-http: //www.emedicine.com/med/topic3055.htm
Leeners, B., Sauer, I., Schefels, J., Cotarelo, CL, Funk, A. (2000). I-Prune-belly syndrome: Izinketho zokwelapha ezifaka ukufakwa kwe-utero ye-vesica amniotic shunt. J Clin Ultrasound, Umq. 28, No. 9, iphe. 500-507.