Uma i-Blood Flow Out of the Ibindi ivinjelwe
I-Budd-Chiari syndrome yisimo esibangelwa ukuvinjelwa kwegazi okuphuma esibindi, kaningi ngegazi legazi. I-Budd-Chiari syndrome ivame ukuvela kubantu abanezinkinga ezingezansi ezibangelwa ukunqamuka kwegazi, kuhlanganise ne- antiphospholipid syndrome kanye nokuphazamiseka kwe-myeloproliferative efana ne-polycythemia vera ne-paroxysmal nocturnal hemoglobinuria.
Izifo eziphuthumayo zokuphuza izifo ezifana nesifo se-Behcet, isifo sofuba esibulalayo, i-sarcoidosis, i-Sjogren syndrome, noma i-lupus ingabangela nesifo se-Budd-Chiari.
Isifo se-Budd-Chiari sithinta abantu bazo zonke izinhlanga futhi sithinta amadoda nabesifazane ngokulinganayo. Kuyaziwa ukuthi i-Budd-Chiari syndrome iyisifo esingavamile, kodwa ukuthi kwenzeka kaningi kangako.
Izimpawu
Iningi labantu abahlakulela i-Budd-Chiari syndrome banezimpawu ezintathu eziyinhloko:
- Ama-Ascite, lapho i-fluid iqoqa khona emgodini wesisu, ngokuvamile yenza isisu sithinteke
- Ubuhlungu besisu
- Isibindi esandisiwe, esibizwa nge-hepatomegaly, ngoba igazi lingadlulela esibindi kodwa hhayi kulo.
Ukwakhiwa kwegazi esibindi kungabangela ukulimala kwamaseli wesibindi. Uma isibindi singasebenzi kahle, lo muntu angathuthukisa i-jaundice (ukuphuka kwamehlo nesikhumba) nezinkinga zezinso.
Ukuxilongwa
Izimpawu ezijwayelekile ze-Budd-Chiari syndrome azikho ukuthi ziyabonakala yini ngoba lezo zimpawu zingabangela ukuhlupheka okuningi.
Uma umuntu enesifo esingabangela i-Budd-Chiari syndrome, lokho kungasiza ekuxilongweni. Uketshezi oluqoqa esiswini lungabuyekezwa ukuze kusize ukuqinisekisa ukuxilongwa. I-ultrasound kanye ne-imagery resonance imaging (MRI) ingasiza ekuhloleni ukusebenza kwesibindi nokugeleza kwegazi. Isampula (i-biopsy) yesibindi ingathathwa ukuze ihlolwe amaseli ngaphansi kwe-microscope.
Ukwelapha
Uma ishiywa ingalashwa, i-Budd-Chiari syndrome ingaphazamisa isibindi. Imithi inganikezwa ukuba ichithe noma yikuphi ama-clots ekhona e-isibindi futhi inciphise ukwakheka kwezindwangu ezintsha. Ukudla okusawoti ophansi kungasiza ukulawula ama-ascites. Izinqubo ezikhethekile zokuhlinzeka zinganciphisa ukucinana kwegazi esibindi. Uma isibindi sonakaliswe kabi, ukufakelwa kwesibindi kungadingeka.
> Umthombo:
Roy, P., Nwakakwa, Shojmanesh, H., & Khurana, V. (2003). I-Budd-Chiari syndrome. eMedicine.