Abaningi bethu bajwayele izinkinga zamehlo ezivame kakhulu - i- glaucoma , i-cataracts, i-eye eye syndrome kanye nokwehla kwe-macular. Ulwazi oluphathelene nalezi zimo lubonakala lulula ukuthola. Kodwa-ke, i-Dych's Dystrophy iyinkinga ejwayelekile yamehlo futhi labo abathintekayo bavame ukushiya ehhovisi likadokotela ngemibuzo eminingi engaphenduliwe. Ukuzifundisa ngalesi simo kungaba yinselele.
Uma wena noma omunye umuntu owaziwa ukuthi unesifo se-Fuch's Dystrophy, okulandelayo kuzokusiza ukuthi ufunde kabanzi.
Iyini i-Dych's Dystrophy?
I-Dych's Dystrophy yisimo sengqondo esizuzwe njengefa esibangela isifo ku-cornea, isakhiwo esicacile se-dome-like on the front of our eye. I-cornea ikhiqizwa izingqimba eziyisithupha zamangqamuzana anama cell endothelial abe yisigcina sokugcina ngakwesokunxele kwe-cornea. Omunye wemisebenzi yamaseli endothelial ukuqhubeka ushaya uphethiloli ngaphandle kwe-cornea, ugcine uhlanganiswa futhi ucacile. Lapho la maseli eqala ukuhluleka, uketshezi lukwakha ku-cornea okubangela ukucindezeleka kumaseli. I-cornea ivuvukala nombono iba sezulu. Ngezimo ezinzima ze-Dych's Dystrophy, i-cornea ingakwazi ukukhokha.
Ingabe ukuxilongwa kwe-Dych's Dystrophy kuyathinta kakhulu ukuphila kwami?
Ubukhulu be-Dych's Dystrophy bungahlukana. Iziguli eziningi azizi ukuthi zinesimo kanti abanye bangase bakhungatheke ngombono wehle.
Kodwa-ke, iziguli eziningi zigcina izinga elihle lombono lokusebenza kahle ngemisebenzi yansuku zonke.
Ingabe i-Dychrophy ye-Fuch iyongenza ngibe yimpumputhe?
Ngokwebuchwepheshe bwanamuhla, ukuphuphuthekisa cishe akukho okwamanje iziguli ezibhekene neDystrophy ejulile ye-Fuch. Kubalulekile ukuqonda ukuthi i-Dych's Dystrophy ayithinti i- retina , i-layer ye-receiver sensitive receptor ye-cornea noma i-nertic optic, i-cable yezinzwa ezixhuma iso ebuchosheni.
I-cornea inikeza iso ngokugcwele kwamandla ayo okubhuka. Ngezifo ezinzima zalesi sifo, ukufakelwa kwe-corneal noma inqubo entsha ebizwa ngokuthi i-DSEK ingabuyiselwa eduze komsebenzi ojwayelekile ku-cornea.
Ngihlobo luni lwezimpawu engingazibona nge-Fuch's Dystrophy?
Ezinye izikhalazo zombono ophuthumayo ekuseni obonakala ubhekana kangcono njengoba usuku luqhubeka. Lokhu kungenxa yokuthi uketshezi lukwakha ku-cornea ubusuku bonke. Njengoba uvuka uphinde uhambe cishe ngosuku lwakho, iso livulekile imvelo futhi umthamo omswakama empeleni uphuphuka ngaphandle kwe-cornea nombono uvame ukuba ngcono. Ungabona futhi ukubona ama-rainbows noma ama-halos azungeze izibani, ukukhanya, nombono wakho kungahle kubonakale kunzima. Ezinye izikhalazo zesobuhlungu noma ukuzwa komzimba wangaphandle emehlweni abo.
Ingabe ukwelashwa kuyothinta indlela yami yokuphila kwansuku zonke?
Ukwelashwa kwe-Dych's Dystrophy ezinyathelweni zakuqala kulula kakhulu. Ngokuvamile, kuhilela ukufaka isisombululo se-sodium chloride noma amafutha e-sodium angama-5% emehlweni ukuze adonse umthamo. I-5% ye-chloride ye-sodium iyinhlanganisela esekelwe usawoti evame ukufakwa izikhathi ezimbili kuya kwezine ngosuku. Ezinye iziguli zithola imiphumela engcono ngokusebenzisa ukuguqulwa kwamafutha ukuthi zifaka iso labo ebusuku kuphela.
Kwenzekani uma i-Dystrophy yami ye-Fuch iba yimbi kakhulu?
Ezinye iziguli azikaze zakha uhlobo olunzima lwe-Dych's Dystrophy.
Kodwa-ke, uma iqhubekela esiteji esinzima kakhulu, ungase uhlakulele isifo sofuba. Yilapho lapho amanzi egcwele ama-bullae noma ama-blisters egcwalisa amanzi futhi enza umbono ubonakale futhi ungaqhuma futhi ubangele ubuhlungu obusweni obukhulu nokuzwa komzimba wangaphandle. Kulolu daba, odokotela abathile bazofaka i- bandage contact lens esweni lakho futhi banikeze amaconsi ama-eye ahlotshisiwe. Uma lesi simo siba sibi, udokotela wakho angase ancoma ukufakelwa kwe-corneal noma inqubo ye-DSAEK. I-DSAEK (i-Descemet's Stripping Automated Endothelial Keratoplasty) iyinkqubo lapho kuphela ingxenye yangemva ye-cornea ithathelwa ngamaseli endothelial enempilo.
Inqubo ye-DSAEK inezinkinga ezincane kunokufakelwa kwe-corneal yangempela kanye nombono ophumela ekungcono kakhulu.
Ingabe izingane zami zizozuza i-Dych's Dystrophy?
Ezinye izimo ze-Dych's Dystrophy kubonakala sengathi azikho uhlobo lwezakhi zofuzo. Kodwa-ke, amacala amaningi analokho owaziwa ngokuthi i-autosomal iphethini yefa. Lokhu kusho ukuthi uma unesimo, kanti omunye wabazali bakho ube nesimo, ingane ngayinye inethuba elingama-50% lokuba ne-Fuch's Dystrophy.
> Umthombo:
> Afshari, Natalie A. MD; U-Aaron B. Pittard, MD; U-Adnan Siddiqui, BS; UGordon K. Klintworth, MD, PhD. Ukufundwa kwe-Fuchs Corneal Endothelial Dystrophy Eholela ekungeneni Keratoplasty, Arch Ophthalmol. 2006.