Nakuba i-lymphomas yiwo wonke amagciwane angathinta i-lymphocytes - uhlobo lwegciwane legazi elimhlophe - ngezinye izikhathi lapho ukuphela kufinyelela khona. Kunezinhlobonhlobo eziningi nezinhlobo eziningi ze-lymphoma. Izigaba ezimbili eziyinhloko yi- Hodgkin's lymphoma , noma i-HL, ne-non-Hodgkin's lymphoma, noma i- NHL . Iningi lazo zombili i-NHL ne-HL ziyi-nodal lymphomas, okusho ukuthi iphuma emagqumeni lymph.
Kodwa kungenzeka ukuthi i-lymphomas iphakame cishe noma yikuphi.
Incazelo: Lymphoma Primary Extranodal
Uma kuthiwa i-lymphoma ivela ngaphandle kwe-lymph nodes , ibizwa ngokuthi i-extranodal lymphoma, noma ngokuqondile, i-primary extranodal lymphoma. Ngezinye izikhathi, kungaba nzima ukukhomba ukuthi emzimbeni kuqale i-lymphoma. Kulezi zimo, odokotela bangase balandele incazelo ecacile: Uma i-lymphoma ngesikhathi esisodwa sinesisindo esikhulu se-tumor - isisindo sayo esicacile kakhulu - endaweni engaphandle, khona-ke ingase ibhekwe njenge-extranodal lymphoma.
Umehluko obalulekile
Kulezi zitholampilo eziqala kuma- lymph nodes , noma i-nodal lymphomas, cishe bonke bangabandakanyeka kakhulu-okungukuthi, bangakwazi ukusabalalisa kumasayithi e-extranodal. I-lymphoma esakazekela kwezinye izitho ezivela emantanjeni ayizibhekwa njenge-primary extranodal lymphoma. Ukuze ube yi-extranodal eyinhloko, i-lymphoma kumele ivele ngaphandle kwama-lymph nodes.
Sibutsetelo
I-lymphomas e-extranodal eyinhloko ivame kakhulu e-NHL kune-Hodgkin's lymphoma. Kuze kube amaphesenti angu-33 azo zonke i-NHL kubhekwa njengenhloko ye-extranodal lymphoma, kuyilapho i-HL, isifo sokuqala se-extranodal kucatshangwa ukuthi i-rarer.
Isayithi elivame kakhulu le-extranodal lymphoma elisezingeni eliyinhloko lisendaweni yomzimba, futhi cishe zonke lezi ziyi-NHL.
Isiza esilandelayo kunazo zonke ngemuva kwepheshana le-GI yisikhumba . Kodwa-ke, uma i-NHL iqala kuphela esikhumbeni, ibizwa ngokuthi i-lymphoma yesikhumba, noma i-lymphoma encane.
I-Extranodal lymphoma nayo ingavela emathangeni e-lymphoid we-spleen, umnkantsha we-bone, i-thymus, i-tonsils, ne-adenoids - izilinganiso ezincane zezicubu ezinjenge-tonsil ezifihliwe lapho izingxenye zamanzi zihlangana nomphimbo.
Amangqamuzana omzimba noma amangqamuzana esiswini, amaphaphu, ezakhiweni ezungeze amehlo, egulini le-thyroid, izigulane ezitholakala emathunjini, kanye namathumbu amancane nawo angabangela ukuba i-lymphomas eyinhloko. Ama-lymphomas kulezi zindawo afaka phakathi 'indawo engaphansi kwe-B-cell lymphomas ye-mucosa-ephathelene nezicubu ze-lymphoid,' noma i- MZBCL ye-MALT, okwesikhashana.
Ama-lymphomas ayisisekelo emphuneni nasemphinjeni afaka i-MZBCL ye-MALT, isakaza i-B-cell lymphoma enkulu noma i-DLBCL , kanye nombulali wemvelo / i-T-cell lymphomas.
I-lymphomas eyinhloko ingathinta ama -testes emadodeni futhi kuthiwa yi-primary testicular lymphomas. I-lymphoma ebuchosheni, noma i-CNS lymphoma, ingaba yinto eyinhloko. Nakuba i- lymphoma eyinhloko ye-extranodal yobuchopho nama-testes iye yahlotshaniswa nezifo ezinzima zokwelapha, ucwaningo lwamuva luye lwabonisa ukuthi ukwelashwa ngokukhethekile okuhambisana nalezi zindawo kungaholela ekuthuthukiseni okukhulu.
I-extranodal prilicodal follicular lymphomas engeyona isikhumba se-lymphomas eyenzeka njalo.
I-bone primary lymphoma yisimo esingavamile lapho i-lymphoma iqala khona emathanjeni.
I-primary cardiac lymphoma ingenye yezicubu ezihlukumezayo zenhliziyo. Kucatshangwa ukuthi i-cardiac primary lymphoma ibhala amaphesenti angu-1.3 kuphela wezinambuzane zenhliziyo futhi kuphela amaphesenti angu-0.5 awo wonke ama-lymphomas extranodal. Uma kwenzeka, uhlobo oluvame kakhulu kwalolu dumbula luhlukanisa i-B cell lymphoma enkulu, futhi ngokuvamile, i-atrium efanele ne-ventricle efanele ihilelekile.
Ukubona okunye kwe-lymphomas e-extranodal eyinhloko, ngokuvamile, ukuthi banda ngokuphawulekayo ngokuvela kwe- HIV ne-AIDS.
I-Extranodal Primary Lymphoma - I-Prognosis
Ukuthi i-lymphoma iyinhloko ye- extranodal lymphoma ingase ibangele ohlelweni lwezokwelapha nokubikezela, kodwa ezinye izici zingase zibaluleke kakhulu noma zibaluleke kakhulu.
I-subtype ye-lymphoma, uhlobo lwe-B noma i-T cell, kanye nesitho esiyinhloko noma izicubu zomsuka kungabonakala kuyizinto ezibalulekile zokubikezela.
Ukubandakanyeka kwe-Extranodal - Isibikezelo
Cishe wonke ama-lymphomas e-nodal angasakazeka ezindaweni ezise-extranodal, kodwa kulezi zimo, azibhekwa njengeziqalo ze-extranodal lymphomas.
Ku-NHL, izinhlelo zokwelashwa eziphumelela kakhulu zixhomeke ezintweni eziningana, nokubandakanyeka kwe-extranodal kungaba omunye wabo. Ngezinye izikhathi i-lymphoma ehlanganiswe namagciwane lymph iyaphulukiswa kakhulu futhi inamaphilisi amaningi kunokuba i-lymphoma esakaze ngaphandle kwe-lymph nodes. Kodwa-ke, izinhlobo ezihlukahlukene ze-NHL eyinhloko ye-extranodal - kanye nezinye izici eziningi ezithonya ukwelashwa nemiphumela - kusho ukuthi uhlelo lokwelapha kanye nokuguqulwa kungaba umuntu ngamunye.
Kwezinye izimo, ukuzibandakanya kwe-extranodal kubonisa kakhulu izifo eziphambili. Ngokwesibonelo, esibhedlela saseHodgkin, ukubandakanyeka kwe-extranodal - ngaphandle kwe-spleen ne-thymus - kubonisa isigaba se-IV Hodgkin isifo. Ngisho nesifo se-Hodgkin isifo sekwephuzile singaphathwa kahle, noma kunjalo.
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