Lapho izimpawu ze-Migraine zibuyiselwa isifo
I-hemiplegic migraine iyinhlobo engavamile ye-migraine eqala ebuntwaneni.
Isici esibalulekile se-hemiplegic migraine yi-aura motor, ebangela ubuthakathaka noma ukukhubazeka kolunye uhlangothi lomzimba
Ngenkathi eshaqisayo ukuzwa i-hemiplegic migraine, izindaba ezinhle ukuthi kunezindlela zokwelashwa ezitholakalayo.
Ukuqonda i-Hemiplegic Migraines
I-migraines yama-Hemiplegic ayifani ne-classic migraines ene-auras ngenxa ye-motor aura.
Noma kunjalo, umuntu one-hemiplegic migraine ngokuvamile uhlangabezana namanye ama auras ngaphandle kwe-motor aura.
Isibonelo, umuntu ohlaselwa i-hemiplegic migraine angase athole kuqala i-aura ebonakalayo (isibonelo, ukubona izibani ezikhanyayo) kulandelwa i-aura yezinzwa (isibonelo, ukuphazamiseka nokugubha), futhi ekugcineni, i-aura motor, ebuthakathaka ngokuvamile iqala esandleni, isakaze engalweni nasobusweni. Ngenkathi ubuthakathaka buvame ukwenzeka ngakolunye uhlangothi, abanye abantu bakuthola ezinhlangothini zombili zomzimba.
Ngaphandle kwezimpawu ze-aura, ubude be-hemiplegic migraine aura buhlukile kohlobo lwe- migraine ejwayelekile ne-aura . Empeleni, i-aura ye-hemiplegic migraine attack ngokuvamile ihlala amahora angaphezu kweyodwa, futhi cishe abantu abangamaphesenti amahlanu, ihlala amahora angaba ngu-24.
Izinhlobo
Kunezinhlobo ezimbili ze-hemiplegic migraine:
I-Hemiplegic Migraine ejwayelekile (FHM)
Njengoba igama liphakamisa, ifomu lomndeni lizuzwe njengefa.
Abacwaningi kuqala baqaphela ukuguquka kwezinto ezintathu ezihlobene nomndeni we-hemiplegic migraine:
- I-FHM1 ibangelwa ukuguqulwa kwesakhi se-CACNA1A esise-chromosome 19
- I-FHM2 ibangelwa ukuguqulwa kwesakhi se-ATP1A2 esise-chromosome 1
- I-FHM3 ibangelwa ukuguqulwa kwesakhi se-SCN1A esise-chromosome 2
Njengoba lezi zakhi zofuzo (lapho i-DNA ilandelana ngokuguquguquka) zizuzwa njengefa eliphakeme kakhulu, uma umzali enehlobo lomndeni we-hemiplegic migraine, ingane yakhe inamathuba angu-50 okuthola lelo hlobo.
Njengoba ucwaningo luvela ku-hemiplegic migraine, kutholakala ezinye izakhi zokuguqula izakhi zofuzo. Isibonelo, izinguquko ezakhiweni ze-PRRT2 nazo ziye zaxhunyaniswa nomndeni we-hemiplegic migraine.
I-Hemiplegic Migraine (SHM)
Lolu hlobo aluvamile kakhulu kune-familial hemiplegic migraine futhi alululwanga, okusho ukuthi umuntu ngeke abe nomlando womndeni we-hemiplegic migraine. Esikhundleni salokho, ukuguquguquka kwezakhi zofuzo zomuntu one-migraine ene-spmatically migraine kwenzeka ngokuzenzekelayo.
Izimpawu
Izimpawu zezinsizwa ezincane zesikhumba se-hemiplegic zifana nalabo abanekhanda lomndeni. Ngaphandle kobubuthakathaka obulodwa obuhlangene phakathi nesigaba se-aura (okuthiwa i-hemiplegia), ukuhlaselwa kwe-hemiplegic migraine kungase kuhlanganise noma eyodwa noma ngaphezulu yalezi zimpawu ezilandelayo:
- Izinwele ezinzima
- I-nausea kanye / noma ukuhlanza
- Ukuzwela ukukhanya noku / noma umsindo
- Izimpawu ze-aura ezinjengezithombe zenguquko, ukuphazamiseka nokukhwaza, kanye / noma ukukhathazeka ukukhuluma
Ehlakalweni esinzima kakhulu lokuhlasela kwe-hemiplegic migraine, umuntu angase abe nesifo somkhuhlane, ukuhlukunyezwa, kanye ne-coma.
Ukwelapha
Ukuvimbela ukuhlaselwa kwe-hemiplegic migraine, udokotela oyinhloko angase athi uCalan SR (i-verapamil ekhululwayo) noma i-Diamox SR (i-acetazolamide ekhululwayo). Le mithi ithathwa nsuku zonke.
Ukwelapha ukuhlasela okukhulu kwe-hemiplegic migraine kungaba yinkinga enkulu, ngokusho kwe-American Migraine Foundation. Lokhu kungenxa yokuthi kunezidakamizwa odokotela abafuna ukuthi abantu abanalesi sifo bagweme ngoba bangandisa amathuba okuba nesifo sohlangothi.
Le mithi ihlanganisa:
- I-Triptans
- Izidakamizwa ze-Ergotamine
- Beta-blockers
Ngokujwayelekile, izidakamizwa ezingezona izifo ezingekho emthethweni (i-NSAID), izidakamizwa eziphikisana nokuhlukunyezwa, noma i-opioids zisetshenziselwa ukunciphisa i-migraine engavamile.
Izwi elivela
Uma ukholelwa ukuthi unenkinga yekhanda le-hemiplegic, kuyadingeka ukuthi ufune usizo lwezokwelapha ukuhlolwa okuphelele. I-migraine yama-Hemiplegic ayivamile futhi ingalingisa nezinye izimo ezibucayi, njenge- stroke noma isifo se-vascular. Uma uthola ukuthi une-hemiplegic migraine, kubalulekile ukubona isazi sekhanda ukwelashwa.
> Imithombo:
> Ikomidi Lokuhlukanisa Amakhanda Ye-International Headache Society. "I-International Classification of Headache Disorders: I-3rd Edition (i-beta version)". I-Cephalalgia 2013; 33 (9): 629-808.
> Pelzer N, Stam AH, Haan J, Ferrari MD, Terwindt GM. I-hemiplegic migraine ejwayelekile kanye neyakhekile: ukuxilongwa nokuphathwa. I-Curr Phatha Izinketho Neurol . 2013 Feb; 15 (1): 13-27.
> Pelzer N et al. I-coma ejwayelekile kanye nomkhuhlane ohlotsheni lomndeni we-hemiplegic migraine 2. Umuntu oneminyaka engu-15 ozolandelwa umndeni omkhulu onokushintshwa kwe-ATP1A2 inoveli. I-Cephalalgia. 2017 Jul; 37 (8): 737-55.
> Robertson CE. (2017). Hemiplegic migraine. Ku: UpToDate, Swanson JW (Ed), UpToDate, Waltham, MA.
> MBR Russell, Ducros A. Spradic and familila hemiplegic migraine: izindlela zokwelapha, izici zomtholampilo, ukuxilongwa, nokuphathwa. I-Lancet Neuro l. 2011 Meyi; 10 (5): 457-70.