I-Eosinophilia-myalgia syndrome (EMS) yisifo esingavamile esibangela ukuvuvukala ezingxenyeni ezahlukene zomzimba kuhlanganise imisipha, isikhumba namaphaphu. I-EMS ibangele amazinga aphezulu amangqamuzana egazi amhlophe aziwa njenge-eosinophils. Lezi zinhlayiya zakha ngaphakathi komzimba futhi zingabangela izinkinga ezinkulu.
I-EMS yaqale yaqaphela ngo-1989 lapho abesifazane abathathu eNew Mexico befuna ukwelashwa ngezigcawu zempawu ezifanayo.
Laba besifazane bonke babenomkhiqizo ofanayo wezekeli zezempilo, i-L-tryptophan, okwenzekile ukuthi ingcolile. I-tryptophan yiyinto eyenzeka ngokwemvelo ekudleni (njenge-turkey). Isibalo se-L-tryptophan esithola ekudleni singaphansi kakhulu kunani elitholakala ekudleni kwethu. Inani elikhulu lezinto zakhiwa njengezithako. Nakuba kungekho ubufakazi besayensi, abanye abantu bathi i-L-tryptophan ingaphatha ngempumelelo ukucindezeleka, ukukhathazeka, i-premenstrual syndrome, nokulala. I-tryptophan ye-Over-counter yavinjelwa ngo-1990 ngemva kokuba izinkulungwane zithintekile yi-EMS.
Amacala e-EMS abikiwe ukuthi awaxhunyiwe ukuthatha i-L-tryptophan. Kodwa-ke, inani lamacala e-EMS liye layeka kakhulu kusukela ukuqubuka kuka-1989 no-L-tryptophan bekhishwa emakethe. Inani eliqondile lama-EMS amacala alingaziwa. Noma kunjalo, kulinganiselwa ukuthi noma yikuphi abantu abavela ku-5,000 kuya ku-10 000 banenkinga.
Iningi lamacala labikwa kwabesifazane baseMelika; Nokho, i-syndrome ibike eJalimane, eCanada nase-United Kingdom.
Izimpawu ze-EMS
Isibonakaliso esinzima kunazo zonke se-EMS sijwayelekile, ubuhlungu obunzima bomzimba obuvame ukwedlulela ngaphezu kwamasonto futhi kungabangela ukuphazamiseka kwemisipha . Izimpawu zivame ukuqala ngokuzumayo futhi ziyahluka kusukela komnene kuze kube nzima.
Lesi simo singabangela izinkinga ezisongela impilo futhi zingase zibulale.
Lesi sifo sibheka ngezigaba - esiyingozi futhi esingapheliyo. Izigaba ziningi izimpawu ezivamile ezihlanganisa ubuhlungu besisu nokukhathala. Isigaba esiyingozi siza kuqala futhi singadlulela noma kuphi phakathi kwezinyanga ezintathu nezinyanga eziyisithupha. Izimpawu ezivame kakhulu zesigaba esiyingozi kukhona izinguquko zesikhumba kanye nobuhlungu be-muscle ezandleni nasemilenzeni. Isikhumba salabo abathintekile singase sigweme, siphume noma siyaziwa ngokuthi (i-eosinophilic fasciitis).
Phakathi nesigaba esingapheli, izimpawu zibonakala zivutha. Bangase baphathe isikhathi esithile bese beya ekuxoxweni. Izimpawu jikelele zihlanganisa:
- Ukuvuvukala kwezingalo nemilenze, futhi ngezinye izikhathi ubuso
- Ubuhlungu obuhlangene
- Isikhumba esikhumba kakhulu
- Ukukhwehlela nokuphefumula
- Ukukhathala
- Fever
- Ukulahleka kwezinwele ezimhlophe ( alopecia )
- Izinkinga zesibindi
- Izinguquko zokuziphatha (ukucasula, ukushintsha kwemizwa)
- Izinkinga zokucabanga (izinkinga zememori, inkinga yokugxila)
- Izinkinga zokugaya (isicashu, ukuhlanza, ukuchoboza)
- Ukungavamile kwenhliziyo (ukuvuvukala, ukushaya kwenhliziyo okungavamile)
Izinkinga zokugaya nezinhliziyo zingase zenzeke phakathi nesigaba esingapheli sesimo. I-EMS ngezinye izikhathi ingacutshungulwa njenge- fibromyalgia , isifo esingapheliyo sokukhathala , i-lupus erythematosus, noma i- arthritis .
Ukwelapha i-Eosinophilia-Myalgia Syndrome
Ayikho ikhambi ye-EMS, ngakho-ke ukwelashwa kugxile ekunciphiseni izimpawu. Labo abane-EMS bangabekwa imizimba yokuphumula emzimbeni kanye nokunciphisa ubuhlungu. I-Prednisone isiza abantu abathile, kodwa hhayi bonke. EMS yisifo esingapheli (isikhathi eside) ukugula. Esicwaningweni sama-333 abantu abane-EMS, amaphesenti ayishumi kuphela abike ukutholakala ngokugcwele ngemva kweminyaka emine ngesifo.
Imithombo:
Nasef, S., & Lohr, K. Fasciitis Eosinophilic. iMedicine Journal, Umq. 3 No. 5.
Sairam, S., & Lisse, J. Eosinophilia-Myalgia Syndrome. iMedicine Journal, Umq. 3 No. 1.
Shiel, WC Eosinophilic Fasciitis (Shulman's Syndrome). I-MedicineNet.