Izimpawu, Ukuxilongwa Nokuphathwa Kwe-Pheochromocytoma
I-pheochromocytoma uhlobo lwe-tumor elitholakalayo ezigulini ezinama-adrenal noma ezinye amaseli ezinzwa. Lezi zicubu zingavamile kakhulu kodwa zingabangela izimpawu ezinkulu ngoba zivame ukusungula ama-hormone athile okuthiwa ama- catecholamines . Nakuba amanye ama-pheochromocytomas angavela emangqamuzaneni omzimba, cishe zonke zazo zivame ukutholakala kwelinye lamaconsi amabili adrenal.
Lezi zicubu cishe zihlale zingenomdlavuza, kodwa zisadinga ukwelashwa ngenxa yamakhono abo okukhululwa kwe-hormone.
Imininingwane mayelana ne-Pheochromocytoma ne-Blood Pressure
- Ama-Pheochromocytomas akhiqiza amazinga aphezulu amakhemikhali abizwa ngokuthi ama-catecholamines, ama-hormone aqinile ahambisana nokucindezeleka, futhi enza ngesimiso senhliziyo ukukhulisa izinga lenhliziyo, ukucindezeleka kwegazi nokugeleza kwegazi.
- Lezi zicubu ngokuvamile zikhiqiza i-epinephrine (i-adrenaline), i-norepinephrine ne-dopamine - izinhlanganisela ezintathu eziphakathi kweziqine eziqine kakhulu ngokunyuka kwengcindezi yegazi . Ngokuvamile umzimba usebenzisa amanani amancane alawa makhemikhali ukubhekana nezimo eziyingozi noma ezicindezelayo.
- Ngisho nangamanani amancane, bonke abathathu banemiphumela emikhulu ekucindezelekeni kwegazi.
- Ngenxa yokuthi i-pheochromocytomas ikhiqiza inani elikhulu lalezi zinhlobo ze-hormone, imiphumela yomsindo wegazi ngokuvamile iyamangalisa kakhulu.
- Cishe zonke iziguli ezine-pheochromocytomas ziye zaphakamisa ukucindezelwa kwegazi, futhi uphawu oluphezulu lwegazi olubangelwa yilo mkhuba ukucindezela kwegazi okwedlulele phakathi nosuku.
Izimpawu Nezimpawu Ze-Pheochromocytoma
Iqembu elivamile lezimpawu ezimweni ze-pheochromocytoma libhekwa ngokuthi "i-triad" futhi liqukethe:
- Izinwele
- Ukujuluka ngokweqile
- ITachycardia
Ukuphakama kwengcindezi yegazi, evame ukuphakama kakhulu, yilona uphawu oluvame kakhulu kwiziguli ezine-pheochromocytoma. Okunye, izimpawu ezingavamile kakhulu zihlanganisa:
- Izinkinga ezibonakalayo (okungaqondile)
- Ukulahlekelwa kwesisindo
- Ukoma ngokweqile / ukuchama
- Ushukela ophezulu wegazi
Zonke lezi zimpawu zingabangelwa izifo ezahlukene, ngakho kubalulekile ukuba zihlolwe udokotela.
I-Pheochromocytoma Diagnosis
Iningi lama-pheochromocytomas empeleni litholakala ngokuzenzakalelayo ("ngengozi") ngesikhathi sokufunda olunye ucwaningo (i-MRI, CT Scan) eyenziwe ngenkinga engavumelani. Izitholampilo ezitholakale ngale ndlela ngokuvamile zibukeka njengengcosana encane noma ubuningi obuhlala endaweni ezungeze izinso. Umlando womndeni noma izinhlobo ezithile zamaphrofayli wezibonakaliso zingase zibonise udokotela ukuthi i-pheochromocytoma ingaba khona.
Lezi zinambuzane nazo zihlobene nezimo ezithile, ezingavamile zezakhi zofuzo. Ukuxilonga ngokuvamile kuhilela ukulinganisa amazinga amaningi e-hormone egazi esikhathini esifushane (amahora angu-24 ajwayelekile), kanye nokuthatha izithombe zesifuba nesisu esisodwa. Ngezinye izikhathi "ukuhlolwa kobunzima" kuqhutshwa, lapho udokotela ejoza khona into eyodwa, ulinde isikhathi esifushane, bese udweba igazi bese uhlola ukuze ubone ukuthi into ejojowe yandisa inani lama-hormone egazini.
Ukwelashwa kwe-Pheochromocytoma
Wonke ama-pheochromocytomas adingeka ukuthi asuswe ngokuhlinzwa. Ngenkathi ukucindezeleka kwegazi ngokuvamile akuyona into ebalulekile ekunqumeni ukuthi kungenziwa noma cha ukuhlinzwa, lokhu kungenye yezenzakalo ezingavamile lapho kwenziwa khona umzamo wokunciphisa ukucindezelwa kwegazi ngaphambi kokuhlinzwa.
Izizathu zalokhu ziyinkimbinkimbi kodwa zihlobene nokuthi lokhu kuyingozi yokuhlinzwa futhi engase ibe yingozi.
Ukuze unciphise ingozi, isethi esimisiwe sezinyathelo ngokuvamile senziwa, nakuba ezinye zalezi zinyathelo zivame ukuphakamisa ukucindezelwa kwegazi. Njengoba ingcindezi yegazi ngokuvamile isivele iphakanyisiwe, ukwanda okwengeziwe kungaba yingozi. Ukuhlinzwa kwangempela kuzokwenziwa ngososayensi kanye nokuhlolwa okukhethekile kuzokwenziwa kokubili ngesikhathi nangemva kokuhlinzwa ukuze kuqinisekiswe ukuthi lonke isisu sasuswa.
Imithombo:
I-Baguet, i-JP, i-Hammer, i-L, i-Mazzuco, i-TL, ne-al. Izimo zokuthola i-phaeochromocytoma: ukutadisha okuphindaphindiwe kweziguli ezingu-41 ezilandelanayo. I-European Journal of Endocrinology 2004; 150: 681.
I-Bravo, EL. Ukuguqula imiqondo ekuthatheni i-pathophysiology, ukuxilongwa, nokuphathwa kwepheochromocytoma. Ukubuyekezwa kwe-Endocrinology 1994; 15: 356.
Oishi, S, Sasaki, M, Ohno, M, et al. Ukuguquguquka kwesikhashana kwengcindezi yegazi kanye nabaphathi bayo kuziguli ezine-pheochromocytoma. Umbiko wekhasi nokubuyekezwa kwezincwadi. I-Japan Heart Journal 1988; 29: 389.
Stein, PP, Black, HR. Indlela elula yokuhlonza i-pheochromocytoma. Ukubuyekezwa kwezincwadi kanye nokubika kwesipiliyoni seziko elilodwa. Imithi (Baltimore) 1991; 70:46.
Ulchaker, JC, Goldfarb, DA, Bravo, EL, Novick, AC. Imiphumela ephumelelayo ekuhlinzekeni kwe-pheochromocytoma ezikhathini zanamuhla. I-Journal of Urology 1999; 161: 764.