Ingabe kukhona into enjalo njengamaseli amaningi abomvu amaningi? Lapho abantu abaningi becabanga ngezinkinga ngamaseli abomvu egazi, bacabanga nge- anemia , inombolo encishisiwe yamaseli abomvu obomvu, kodwa amangqamuzana amaningi obomvu agazi angase abe inkinga futhi. Lokhu kubizwa ngokuthi i-polycythemia, noma i-erythrocytosis. Kukhona umehluko wezobuchwepheshe phakathi kwalababili kodwa ngokuvamile usetshenziselwa ngokungafani.
Inkinga Yezinqwaba Eziningi Ezibomvu zegazi
Kungani ucabanga ukuthi kungcono kunalokho okwanele, i-polycythemia ingabangela izinkinga ezibalulekile. Lokhu kwandisa igazi ngoba manje kunamaseli amaningi ngesilinganiso esifanayo samanzi (okuthiwa i-plasma). Leli gciwane linzima ukuhamba emithanjeni yegazi futhi kungabangela ukushaywa, ukuhlaselwa yinhliziyo, ama-blood clots noma i-pulmonary embolus (i-clot yegazi emaphashini).
Izimpawu zePolycythemia
Izimpawu ze-polycythemia azicacile futhi abanye abantu abanalo izimpawu futhi batholakala ngemuva kokusebenza komsebenzi we-laboratory.
- Ubuthakathaka noma isiyezi
- Ukukhathala noma ukukhathala
- Izinsizwa
- Ukucheka, ngezinye izikhathi emva kokugeza noma ukugeza
- I-Joint Pain, ngokuvamile inzwane enkulu
- Ubuhlungu besisu
- Ukubomvu kobuso
Ukuxilongwa
I-polycythemia ibonakala ngokubala kwegazi eliphelele . Ukubala kwesibalo segazi obomvu (kubhalwe i-RBC), i-hemoglobin, kanye / noma i-hematocrit iphakanyisiwe. Umsebenzi wegazi uzophindaphindiwe ukuze uphathe iphutha le-laboratory.
Kubalulekile ukuqaphela amanani ajwayelekile ahluka ngobudala nobulili (emva kokukhulelwa) futhi kuthinte incazelo ye-polycythemia.
Okunye ukusebenza-up kwenziwa ukuze ubone ukuthi imbangela ingabonakala. Lokhu kufaka phakathi izinga lokulinganisa oksijeni (okuvame ukubizwa ngokuthi inkabi ye-pulse) nokwenza ukuhlola kwenhliziyo nesiphuphu (i-chest x-ray, EKG, ne-echocardiogram) ukulawula amazinga aphansi e-oxygen njengesizathu.
Izinga lika-Erythropoietin, i-hormone efihliwe yizinso ezikhuthaza ukukhiqizwa kwamaseli obomvu, ingalinganiswa. I-Bone marrow aspirate ne-biopsy nayo ingenziwa.
Yonke yale migomo ingase ikhale entsha kuwe. Uma udokotela wakho esebenzisa, noma uma uthola umbiko webhu futhi unenkinga yokuyiqonda, cela usizo. Ukwenza ucwaningo lwakho kungasiza, kodwa ukuba nomuntu ochwepheshe bechaze kuwe kunenzuzo eyengeziwe: bazobe bachaza ukuthi imiphumela yisho ukuthini ngokuqondene nawe ngqo.
Izimbangela
- I-Polycythemia vera : Lesi simo esingavamile somnyofu wethambo. Ngokujwayelekile, nawe unesisindo se-white white cell (leukocytosis) kanye nenani eliphakeme leplatelet (thrombocytosis). Lokhu kungabangelwa ukuguquguquka kwezakhi zofuzo okuthiwa i-JAK2.
- Ejwayelekile: Lezi zimo ezizuze njengefa lapho umzimba uveza amangqamuzana amaningi egazi obomvu kunalindelekile.
- Izimo ezibangela amazinga aphansi oksijeni egazini (hypoxia), njenge:
- Isifo se-Chronic obstructive pulmonary (COPD)
- Isifo senhliziyo
- I-apnea yokulala
- Ukucindezeleka komfutho wegazi
- Izicubu ezibeka i-erythropoietin, njenge:
- I-hepatocellular carcinoma (umdlavuza wesibindi)
- Renal cell carcinoma (umdlavuza wezinso)
- Izicubu zezingqungquthela ze-adrenal
- Ngezinye izikhathi ama-cysts ezinso
Izinsana nazo zingaba ne-polycythemia evame ukuhlobene nayo
- Izimo ezihambisana namazinga aphansi e-oxygen ngenkathi utero
- I-twwin kuya kwe-twin ukumpontshelwa: Kulesi simo, iwele elilodwa lithola igazi elingaphezulu kusuka kwe-placenta kunezinye.
Ukwelapha
- Ukuqaphela: Uma kungenakulinganiswa, udokotela wakho angase akugcine nje
- Ukwelashwa kwesimo esibhekene nesimo esibangela i-polycythemia
- I-Phlebotomy: Igazi liyasuswa emvuthweni ngezikhathi ezijwayelekile ukuvimbela izinkinga. Igazi livame ukufakwa esikhundleni saline evamile (i-fluid enikezwe emthanjeni).
- I-Hydroxyurea: I-Hydroxyurea, imithi yomlomo, ingasetshenziswa uma i-phlebotomy ingavumi. I-Hydroxyurea izokwehlisa zonke izibalo zegazi: amaseli egazi amhlophe, amangqamuzana egazi abomvu namaplatelet.
- I-Interferon-alpha: I-Interferon-alpha ingasetshenziselwa ukuvuselela amasosha omzimba wakho ukuba alwe nokukhipha ngokweqile amaseli egazi abomvu.
- I-Aspirin: I-Aspirin ingasetshenziselwa ukunciphisa ingozi yezindwangu. I-aspirin ivimbela ama-platesthi kusukela ekugqibeleni.
- I-Ruxolitinib: I-Ruxolitinib ingasetshenziselwa iziguli ezine-JAK2 ukuguquguquka futhi noma ayibekezelelanga noma ayiphenduli ukwelashwa kwe-hydroxyurea.