Ukunyakaza okujwayelekile kuxhomeke ekuqhekekeni okuhlanganisiwe kwesisipha esisodwa nokuphumula kwesinye. Isibonelo, i-biceps yakho ifinyelela ingalo yakho futhi i-triceps yakho iyakwandisa. Uma kokubili i-triceps yakho ne-biceps inkontileka ngesikhatsi esifanayo, isikhathi sezingalo kodwa asihambisani. Eqinisweni, uma inkontileka yemisipha ngesikhathi esisodwa futhi engahlosile, ingxenye yomzimba ingase ishintshwe ekufweni okungajwayelekile.
Yilokho okwenzeka ku-dystonia.
I-Dystonia ingathinta noma iyiphi ingxenye yomzimba, kuhlanganise izingalo, imilenze, i-trunk, intamo, amajwabu amehlo noma ubuso. Elinye lamafomu ajwayelekile kakhulu e-dystonia yi-cramp's, okuyinto ethinta isandla uma ubhala. Lesi yisibonelo se-dystonia eqondene nomsebenzi, kepha i-dystonia nayo ingenzeka noma kunini. Kungaba okuphakathi, okuqinisiwe, okuyisigqi, noma okunamandla. Njengezinkinga eziningi zezinzwa, i-dystonia igcwele ukucindezeleka noma ukukhathala.
Ukusiza ukuphatha i-dystonia, kusiza ukuhlukanisa inkinga. Kunezindlela eziningana zokuhlukanisa i-dystonia, kuhlanganise nesikhathi sokuqala, ukusatshalaliswa komzimba, imbangela ye-dystonia, ne-genetics.
Ubudala bokuqala
Uma umuntu oneminyaka engaphansi kwengu-26 ehlushwa i-dystonia, lokhu kubhekwa njengokuqala kokuqala. Nakuba singazi ukuthi kungani, i-dystonia yokuqala iqala ukuqala ngaphezulu emilenzeni kunezingalo. Ngokuvamile, imbangela iyigciwane.
Ngaphezulu kweminyaka engama-26, i-dystonia ivame kakhulu entanyeni nasezingalweni kunemilenze.
Esikhundleni sokuthi i-genetic iyimbangela enkulu, i-dystonia kubantu asebekhulile ivame ukuhlotshaniswa noma kubangelwa ezinye izici, nakuba i-dystonia yezimbangela ezingaziwa zisasebenza.
Isibonelo, esinye sezimbangela ezivame kakhulu ze-dystonia yindlela yokubhekana nemithi efana ne- Reglan , esetshenziselwa ukwelapha izinkinga zamathumbu.
Ezinye izifo eziningana zesistimu yezinzwa zomphakathi ziba zivame kakhulu njengoba sikhula, futhi zingaholela e-dystonia. Izibonelo zifaka isifo sikaParkinson , ukulimala kokwehla kwengqondo, noma ukushaywa yisifo .
Ukusakaza Bodily
I-Dystonia ingabuye ihlukaniswe ukusatshalaliswa komzimba. Mhlawumbe okuvame kakhulu ukuthi i-dystonia ephawulekayo, okusho ukuthi ingxenye eyodwa yenyama kuphela ethinteka, njengokwesikhala somlobi.
Izazi ze-neurologists zinamagama akhethekile ezinhlobonhlobo ezivamile ze-dystonia. Isibonelo, i-dystonia ephikisayo entanyeni ibizwa ngokuthi i-torticollis, kanti i-dystonia yamajwabu amehlo abizwa nge-blepharospasm.
E-dystonia ehlangene, izifunda zomzimba ezimbili ezixhunyiwe komunye nomunye zithinteke, futhi ku-multifocal dystonia, izifunda ezimbili zomzimba ezingathandeki ziyi-dystonic.
E-hemidystonia, isigamu somzimba siyathinteka. Okokugcina, ku-dystonia jikelele, zombili imilenze futhi okungenani ingxenye eyodwa yomzimba eyengeziwe yidystonic. Lokhu kungabonakalisa isifo esibucayi esinomzimba, noma uma kwenzeka ngaso sonke isikhathi, kungase kube umphumela wokuphendula kwezidakamizwa.
Izimbangela zeDystonia
E-dystonia eyinhloko, akukho ukulimala okuyisisekelo noma isifo. I-dystonia ingase ibe ngenxa yokuguquka kwezakhi zofuzo, njengokungathi ku-DYT1 idiopathic torsion dystonia, noma kungenzeka ngenxa yezizathu ezingaziwa.
Kunezinhlobo eziningi zefa le-dystonia.
Okuvamile kunazo zonke i-DYT1, eqala engalo nasemlenzeni oneminyaka engama-13. Amaphesenti angamashumi ayisithupha nesikhombisa sesikhathi, iqhubekela phambili ku-dystonia ehlukahlukene noma ejwayelekile. Ezinye izinhlobo ze-genetic dystonia azivamile, kuhlanganise ne-Lubag's syndrome, i-Segawa syndrome nokuningi. Uhlobo ngalunye lwe-dystonia lunezici ezihlukile. Isibonelo, i-Lubag syndrome ithinta amadoda kakhulu. I-dystonia ye-Segawa syndrome inezimpawu ezimbi kakhulu ebusuku futhi ziphendule kahle imithi ye-levodopa ejwayele ukusetshenziselwa ukwelapha isifo sika-Parkinson.
E-dystonia yesibili, i-dystonia ibangelwa uhlobo oluthile lomonakalo ohlelweni lwezinzwa, njengokulimala kwesisu, noma umphumela wezokwelapha .
Izifo ze-neurodeergenerative, njengezifo zikaPasinson, isifo sikaWilson, isifo sikaHuntington , kanye nezinye izifo ezibangelwa mitochondrial nazo zingaholela e-dystonia.
Ngezinye izikhathi, akukho sizathu se-dystonia esitholakala. Lokhu akusho ukuthi i-dystonia ayikwazi ukuphathwa, noma kunjalo. Ukwelashwa ngokomzimba , imithi yomlomo kanye nejojo, kanye nezinketho zokuhlinzwa ezifana nokujula kobuchopho obujulile kungasiza. Ezimweni eziningi ze-dystonia ezibangelwa umphumela womuthi wezidakamizwa, iBenadryl elula ingakwazi ukuxazulula le nkinga. Njengoba kunezinketho eziningi zokwelashwa ezitholakalayo, kubalulekile ukuthi abantu abane-dystonia babone ochwepheshe bezokwelapha ukuze bathole usizo abaludinga.
Imithombo:
I-Breakefield XO, i-Blood AJ, i-Li Y, i-Hallett M, i-Hanson PI, i-Standaert DG. Isisekelo se-pathophysiological ye-dystonias.Nat Rev Neurosci. 2008 Mar; 9 (3): 222-34.
I-Carbon M, i-Eidelberg D. Isakhiwo esingavamile-ukusebenza ubudlelwane kwi-dystonia yefa. I-neuroscience. 2009 Nov 24; 164 (1): 220-9. Epub 2009 Jan 1.
I-Fuchs T, i-Ozelius LJ. I-Genetics ye-dystonia. Semin Neurol. 2011 Nov; 31 (5): 441-8. Epub 2012 Jan 21.
I-Ozelius LJ, i-Bressman SB. Izakhi zofuzo nezomtholampilo we-torsion primary dystonia. I-Neurobiol Dis. 2011 Meyi; 42 (2): 127-35. Epub 2010 Dec 17.