Ukungondleki kuyimbangela evamile yokukhula okubi kubantu abane-cystic fibrosis
Ukungondleki kungumuthi ojwayelekile we- cystic fibrosis engalashwa noma engalawulwa kahle (CF). Ukungondleki kuholela ekukhuleni okuncane nokunciphisa umzimba, okuvame ukuba yizimpawu zokuqala ezenza odokotela bacabange ukuthi ingane ingase ibe neCF. Uma ingane yakho ingakhula ngoba ingondlekile, ungase uzwe udokotela wakho asebenzise igama elithi "ukwehluleka ukuphumelela." Lokhu kusho ukuthi ingane yakho ayikathuthuki ngezinga elijwayelekile leminyaka yabo.
Lapho ukwelashwa sekuqalisiwe, iziguli zivame ukusabela kahle ekushintsheni kokudla futhi ziqale ukulandela amaphethini okukhula okujwayelekile.
Yini Ebangelwa Ukungondleki Kwabantu Nge-Cystic Fibrosis?
Impendulo elula kulo mbuzo ukuthi ngaphandle kokwelashwa, abantu abane-cystic fibrosis basebenzisa amandla amaningi kunalokho abasebenzisa. Ngokuyinhloko, ama-akhawunti azo asebhange asekhishiwe. Kunezizathu ezintathu ezinkulu zokungalingani kwamandla.
Izidingo zamandla aphezulu. Abantu abane-cystic fibrosis kufanele basebenze kanzima ukuphefumula nokuthi umsebenzi udinga amandla. Kulinganiselwa ukuthi umsebenzi wokuphefumula wedwa ukwandisa izidingo zamandla ezingaphezulu kwamaphesenti angu-9 kunomuntu onempilo onesisindo esisodwa somzimba.
Ukumamatheka okuncane. Ngenxa yethonya le-CF elinama-pancreas , umzimba awukwazi ukuthatha amandla amaningi ekudleni okudliwayo. Ngisho noma umuntu onesifo se-cystic fibrosis esidla ukudla okuningi, amandla amaningi angase aqedwe, angasetshenzisiwe.
Abantu abane-CF bavame ukuba ne-steatorrhea, izitshalo ezihambayo futhi ngokuvamile ziphosa. Lokhu kubangelwa inani elikhulu lamanoni aqedwa kusukela esitokisini.
Ukudla okubi. Abantu abanesifo se-cystic fibrosis bavame ukuba nesifiso esikhulu ngoba imizimba yabo ibatshela ukuthi badinga amandla amaningi, kepha ukudla yedwa akusilo okwanele ukuqinisekisa ukuthi ukudla okufanele.
Ngezinye izikhathi abantu abane-CF banezinye izinkinga eziqhubekayo okwenza kube nzima ukudla, ezifana ne-acid reflux, izinkinga zokuphefumula, noma ukulwa nokucindezeleka.
Ukuntula ukudla okunomsoco kuthathwa kanjani?
Umgomo wokwelapha okunomsoco kubantu abane-CF ukubuyisela ibhalansi emihle kuma-akhawunti abo asebhange. Izimfuneko zamandla azikwazi ukuguqulwa ngakho ukugxila kokwelashwa kuwukuthuthukisa ukumuncwa nokudla, abanye abanikeli ababili ebhalansi engalungile.
Ama-enzyme. Ngaphambi kwesidlo ngasinye futhi ngezinye izikhathi ukudlala, abantu abane-CF kumele bathathe amaphilisi aqukethe ama-enzyme e-pancreatic imizimba yabo engakwazi ukuyibeka. La ma-enzyme asiza uhlelo lokugaya ukudlala izakhi nemandla ekudleni okungeke kukhishwe.
Ukudla. Izindlovuzi zakha izinhlelo zokudla ezizimele ukuze zihlangabezane nezidingo zesiguli ngasinye, kodwa umthetho oyisisekelo wesithupha ungadla ukudla okunamafutha aphezulu okuhlanganisa amaphesenti angama-35 kuya kwangu-40 amakhilogremu ayizinkulungwane. Ukudla okuphelele kwe-caloric kuvame ukuhluka kusuka kumaphesenti angu-110 ukuya kwangu-150 okunikezwayo kwansukuzonke kunomuntu onempilo oneminyaka efanayo nobulili. Ama-fibre kufanele adliwe ngokulinganisela ukuvimbela ukuqotshwa, kepha ukudla okuphezulu kwe-fiber kufanele kugwenywe ngoba kungenakuhlinzeka ngekhalori elanele futhi ngezinye izikhathi kungaholela ekuvimbeleni emathunjini kubantu abane-cystic fibrosis.
Umthombo:
I-Pencharz, i-PB ne-Durie, i-PR "I-Pathogenesis Yokungondleki Kwama-Cystic Fibrosis ne-Treatment Yayo". Ukudla okunomtholampilo 2000 19 (6): 387-394. 20 Juni 2008.