Izimpawu Zokuqala Nezinyathelo Eziphakeme ze-CF, i-Progressive and Genetic Disease
Ngokuvamile, izimpawu ze-cystic fibrosis ziyanda njengoba lesi sifo siqhubeka. Isimo, esibangelwa isakhi sofuba, senza uhlaka olunzulu lwamakhemikhali ukwakha emaphashini (ukuvala imimoya yomoya kanye nokuholela ekutheleleni, umonakalo wamaphaphu, nokuhluleka kokuphefumula), i-pancreas (ukuvimbela umzimba ukuba ungaphuli kahle ukudla ukuthatha izakhi), nezinye izitho.
Ifulethi elingalungile alivumeli umzimba ukuthi udlulisele amanzi nosawoti ukuya nasuka kumaseli, okwenza imfihlo (ngokuvamile ibe yincinci kanye namanzi kubantu abanobuchopho obukhulu kakhulu nabanamathele kubantu abane-CF). Iminyango eminyene yilokho izitho ze-clog futhi ivimbela ukusebenza kahle komzimba.
Izimpawu Zokuqala Zama-Cystic Fibrosis
Esikhathini esiningi, izinsana ezinama-cystic fibrosis (CF) zibukeka njengezinsana ezinempilo ngoba lesi sifo asibangeli noma yikuphi ukungafani okubonakalayo ezigabeni zokuqala. Cishe ngo-20% wesikhathi, izinsana ezinama-CF zizovimbela kakhulu emathunjini ekubelethweni okuthiwa i-leec meconium. Lolu hlobo lwesithiyo aluvamile ukuba lube khona ngaphandle uma umntwana enesifo se-CF, ngakho-ke uma kwenzeka kwenzeka ukuthi kubhekwe njengesifo sokuqala sesifo.
Izimpawu Ezivamile Zama-Cystic Fibrosis
Uma i-cystic fibrosis ingatholakali ngesikhathi sokuzalwa, ezinye izimpawu zizoqala ukuvela ngonyaka wokuqala noma ezimbili zokuphila, njenge:
- Ukutholwa kwesisindo esibi. Ama-blockages kuma-pancreas nama-glands omathumbu avimbela uhlelo lokugaya ukusebenza kahle. Ukudla okudliwa kudlula emzimbeni ngaphandle kwezakhi eziningi ezitholakalayo, okuholela ekukhuleni okubi. Uma ingane ingabuyisanga isisindo sakhe sokuzalwa ngamasonto angama-4-6 noma ikhombisa iphethini eqhubekayo yokukhula okuncane, udokotela angase aqale ukusola uCF.
- Ukudla okunamandla. Ngenxa yokuthi izakhi azitholakali ekudleni, ubuchopho buzama ukuhlangabezana nezidingo zomzimba ngokuthumela izimpawu zendlala. Abantu abane-cystic fibrosis bavame ukuba nesifiso esikhulu futhi bangadla ukudla okungenakudla ngaphandle kokuthola inzuzo yesisindo.
- Ama-Bulky, Oily, ama-Smelling Bowel Movements. Isistimu yokugaya kahle engasebenzi kahle inenkinga ethile yokugaya amafutha namaprotheni. Iningi lalokho okwakungase lithathwe yindlela yokugaya ukudla okunempilo kukhishwa ngamathumbu, okwenza kube nokunyakaza okungavamile kokugaya okwenzeka ngokuvamile kwiziguli ezine-CF.
- Izifo Ezingavamile Nezifo Zokuphefumula. Ukukhukhuma, ukuphefumula ubunzima, kanye nokutheleleka okuphefumula njalo kuvame ukubonakaliswa kwabazali bezingane abane-CF.
- Isikhumba Soshevu. Isici esiyimvelo esenza i- cystic fibrosis iphazamise ikhono lomzimba lokuhambisa usawoti ngaphakathi nangaphandle kwamaseli. Usawoti ongeke ukwazi ukungena uyadonswa esikhumbeni ngama-sweat sweat, okuholela ekubonisweni kwe-salta salit. Ngezinye izikhathi, kungase kube khona usawoti obonakalayo ebeka esikhumbeni. I-salt excretion yizigulane ezikhukhulayo isisekelo sohlolo oluvame kakhulu olusetshenziselwa ukuxilonga i-cystic fibrosis.
Izimpawu ezithuthukisiwe nezinkinga ze-CF
Izimpawu ezithuthukisiwe ze-cystic fibrosis azivamile izimpawu zesifo ngokwazo, kodwa izimpawu zokulimala okubangelwa yisikhathi se-CF. Ngesikhathi lezi zimo zivela, abantu abaningi sebeyazi kakade ukuthi bane-cystic fibrosis futhi baye bahlala nesifo isikhathi esithile. Izinkinga ezilandelayo yizimpawu eziphambili zeCF:
- Ukuqeda Ukukhulelwa. Ngesinye isikhathi kubonakala sengathi ukubeletha okudabukile kumantombazane ane-cystic fibrosis ngenxa yokudla okungenamsoco.
- Ukungenzi lutho. Abaningi besilisa abane-cystic fibrosis abangenasifo ngenxa yemfihlo yokuvimbela isidoda. Abesifazane bangase babone ukungabi nabantwana ngenxa yesikhwama esincane somlomo wesibeletho esivimba ukungena kwesidoda zibe izitho zokuzala.
- Isifo sikashukela. Ngokuhamba kwesikhathi, umonakalo owenzelwe ama-pancreas yi-cystic fibrosis uyabangela ukuba ayeke ukukhiqiza i-insulin eyanele. Abantu abangaba ngu-15% abanesifo se-cystic fibrosis esingaba abantu abadala bazoba nesifo sikashukela esinesifo sikashukela .
- Izifo zesibindi. Ukuvinjelwa kwama-bile embindi kubangela ukulimala kwesibindi kanye nesibindi kuma-5% weziguli ze-cystic fibrosis. Uma ukulimala kwesibindi kwenzeka, ngokuvamile kubonakala kubantu abadala.
- Izifo ze-Gallbladder. I-gallbladder igcina izinto ezibizwa ngokuthi i-bile ezidalwe yisibindi nezinsizakalo ekugayeni kwamafutha. Kubantu abaningi abane-cystic fibrosis, i-bile ilukhuni futhi ayikwazi ukudlula phakathi kwe-bile duct ukushiya i- gallbladder . Esikhathini esiningi lokhu lokhu kungabonakali izimpawu, kepha cishe u-10% we-cystic fibrosis izokwakha ama-gallstones adinga ukuhlinzwa.
- Pancreatitis. Uma i-bile ishiya i-gallbladder, ifinyelela emathunjini amancane nge-buct evamile ekwabelwana ne-pancreas. Uma i-gallstone ishiya i-gallbladder futhi ibambeke emgodini we-bile ovamile, ukuvinjwa kwe-pancreatic akunakwenzeka. Lokhu kubangela ukuvuvukala nokucasuka okubuhlungu kwe-pancreas eyaziwa njenge-pancreatitis, edinga ukungenelela okuhlinzayo.
Umthombo:
I-Cystic Fibrosis Foundation. Mayelana neCystic Fibrosis. 10 Apreli 2016