Umphumela Wegene Eliyingozi Emzimbeni
I-Cystic fibrosis (CF) isifo esingapheli, sokunciphisa impilo esenzeka ngenxa yesici sokuzalwa. Isakhi sofuzo sithinta ikhono lomzimba lokudlulisa amanzi nosawoti ukuya nakwamaseli avumela ukujuluka, ama-mucus, nama-enzyme yokugaya. Lokhu kubangela ukufihla, okuvame ukuthi kube mncane futhi kunamanzi kubantu abanobuhle, ukuba kube mnandi kakhulu futhi kunamathele.
Iminyango encane ivala izitho futhi iwavimbele ekusebenzeni kahle. Imiphumela ye-cystic fibrosis ingathinta izitho eziningana nezinhlelo.
I-Cystic Fibrosis Impact
Ku-CF, izitho eziningi zomzimba nezinhlelo zithintekayo, kubandakanya:
- Uhlelo lokuphefumula (izitho ezithile ezifana namaphaphu nezinye izakhi emzimbeni okuvumela ukuba uphefumule futhi usakaze igazi eliphefumulayo kuwo wonke umzimba)
- Uhlelo lwesisu (oluphathelene nesisu kanye namathumbu)
- Uhlelo lwe-musculoskeletal (imisipha namasipha)
- Isistimu ye-Genitourinary (ephathelene nezitho zangasese nezomchamo)
- Uhlelo lokuzala (uhlelo lwezitho zobulili oluhlanganisa amanzi, amahomoni, nama-pheromone)
Amalungu Ayingxenye Ethintekayo CF
Ezinye zezinhlaka ezinkulu ezithintekayo yi-CF zihlanganisa amaphaphu, ama-pancreas, isibindi kanye ne-gallbladder, amathumbu kanye nezitho zokuzala.
Amapulazi
Kukhona umkhiqizo ongajwayelekile ongenawo wonke umzila wokuphefumula ngenxa yokuthutha okungafanelekile kwe-electrolytes emazingeni amancane.
Lesi sikhukhu siphume kalula futhi kunzima ukusula emgwaqweni, okungabangela ukuvinjelwa, ukulimaza i-alveoli (ama-sacs amancane) emaphashini futhi kuvumela izinhlayiya zangaphandle ukwakha (ezibangela izifo ezingapheli zamapayipi).
I-cystic fibrosis ibangela izinkinga emaphashini lapho i-mucus ebanzi ikhula futhi ibambeke emoyeni.
Uma lokhu kwenzeka:
Izindlela zokuphefumula zivinjelwe futhi umoya awukwazi ukufika.
Ama-bacteria akhula emqoqweni we-mucus futhi abangela ukutheleleka emaphashini, emakhaleni nasesimweni.
Ama-polyp nasal angathuthuka kwezinye iziguli ze-CF.
I-Pancreas
I- pancreas iyingxenye yesimiso sokugaya. Umsebenzi wawo ukuvikela ama-enzyme adingekayo ukugaya ukudla, ne-hormone ebizwa ngokuthi i-insulin elawula ushukela wegazi. I-fibrosis yama-cystic nayo ibangela ukuthi lezi zimfihlo zingene.
Uma lokhu kwenzeka:
Amathanga we-pancreatic agqwaliwe.
Ama-enzyme awakwazi ukudlula ukuvinjelwa.
Ukudla akugcini kahle futhi umzimba awunakuthola izakhi.
Ekugcineni, ukuvinjelwa kwama-pancreas kungabangela ukulimala okulimaza amangqamuzana okukhiqiza i-insulin futhi kuvimbele ukuba bakhiqize i-insulin. I-insulini ayitholakali amangqamuzana, okubangela ukuba amazinga kashukela egazi avuke. Lesi sifo sabizwa ngokuthi isifo sikashukela esise-insulin, okwenzeka cishe ku-15% kuzo zonke iziguli ze-CF.
Isibindi ne-Gallbladder
Nakuba kungavamile, ukuvinjelwa okweqile nakho kungagcwalisa ama-bucts we-bindi wesibindi ne-gallbladder futhi kuvimbele ukuthi bangasebenzi kahle.
Uma ukuvinjwa kwamathaya esiqindi kuqhubeka isikhathi eside, isibindi singasengozini unomphela.
Uma amadoksi e-gallbladder evuliwe, i-gallbladder ivame ukususwa.
Amathumbu
Ngezinye izikhathi, amathumbu ayilungu lokuqala lokuthinteka yi-cystic fibrosis. Ezinganeni ezingaba ngu-20 kuzo zonke izinsana ezine-CF, ifomu elikhuni lokuvimba emathunjini okwenza kube nokuvinjelwa okusempilo kwamathumbu okuthiwa yi-ileus ye-meconium.
Amalungu Okuzala
I-cystic fibrosis ithinta izitho zokuzala zamadoda nabesifazane ngendlela ehlukene nangendlela elandelayo:
- Amadoda cishe njalo engaphelele ngoba ukucinana okukhulu emgodini wesilisa kubangela ukuvinjelwa okuvimbela isidoda ukuba singadluli.
- Abesifazane bavame ukukhulelwa kodwa kungenzeka ukuthi banciphise ukuzala ngoba umqubu womlomo wesibeletho uvimbela ukungena kwesidoda.
Umthombo:
I-Cystic Fibrosis. Zonke izibhedlela zezingane. Ulwazi lwezeMpilo.