Ubuningi Ngemva kokuthola ukuhlolwa
Uma wena noma othandekayo uthola ukuthi une- amyotrophic lateral sclerosis (ALS), ebizwa nangokuthi isifo sikaLou Gehrig, enye yemibuzo yakho iyisiguli sokuthi lesi sifo. I-ALS inegalelo elibalulekile ekulindeni kokuphila kodwa kunezokwelapha ezinganciphisa ukulahlekelwa komzimba futhi zingase zandise ukuphila.
Kuyini i-ALS?
I-ALS yisifo esiwumphumela we-neurodegenerative esithinta amangqamuzana ezinzwa emqondweni nasezintanjeni zomgogodla.
Kuyinto isifo esiphuthumayo esithinta ama-neurons asemoyeni afinyelela ebuchosheni ukuya emthonjeni womgogodla. Lezi zinzwa ze-neurons zilawula umzimba wonke. Ngokuhamba kwesikhathi, ubuchopho bulahlekelwa ikhono lokulawula imisipha yokunyakaza ngenxa yokushona kwalezi zithuthuthu.
ALS Ukulindela Ukuphila
Ukulinganiselwa kokuphila komuntu onama-ALS iminyaka emibili kuya kwemihlanu kusukela ngesikhathi sokuxilongwa. Nokho, lihluka kakhulu:
- Abantu abangaphezu kwamaphesenti angu-50 abano-ALS baphila iminyaka engaphezu kwengu-3.
- Amaphesenti angu-20 ahlala iminyaka emihlanu noma ngaphezulu.
- Amaphesenti ayishumi ahlala iminyaka eyishumi noma ngaphezulu.
- Amaphesenti amahlanu azohlala iminyaka engaphezu kwengu-20.
Izindlela Zokukhulisa Ukulindela Ukuphila
Nakuba kungekho ukwelashwa kwe-ALS noma izindlela zokumisa ukuqhubeka kwesifo ngokuphelele, kunezinto ezithile ongayenza ukuze uthuthukise isikhathi sokuphila. Lokhu kufaka:
- Imithi: I- Riluzole isetshenziswe kusukela ngo-1995 futhi ikhonjiswe ngezivivinyo zomtholampilo eziphuphuthelwe kabili ukuze zenze isikhathi sokuphila isikhathi esingangezinyanga ezimbili kuya kwezintathu, nakuba ezinye izifundo ezinzima kakhulu zibonise ukuthi umuthi ube nomthelela omncane kakhulu. Ngaphezu kwalokho, ezinye izidakamizwa zisetshenziselwa ukuphathwa kwezibonakaliso ezingasiza ekuthuthukiseni ikhwalithi yokuphila nokusebenza isikhathi eside. I-Radicava (i-edaravone) yamukelwa ngo-2017. Ekuvivinyweni kokwelashwa, yehlisa ukuncipha kokusebenza ngokomzimba.
- Ukuphumula okungeyona engavamile : Ukusetshenziswa kwe- ventilation engeyona ingavamile (NEV) kuboniswe ukuba kuqhubeke isikhathi eside phakathi kwezinyanga eziyisikhombisa nezinyanga ezingu-11, kuye ngokuthi kusetshenziswa isikhathi esingakanani usuku ngalunye nezici ezihlukahlukene zesineke. Imodi eyinhloko ye-NEV i-positive-pressure ventilation, okuyinto ngokuphefumula ehamba nge-mask ehambisana nomlomo nekhala.
- I-Percutaneous Endoscopic Gastronomy (PEG): I-tube yokudla ifakwa esiswini futhi iphuma ngaphandle komzimba ngodonga lwesisu. Nakuba izifundo zehlulekile ukubonisa umthelela oqhubekayo ngesikhathi sokuphila, i-American Academy of Neurology incoma ukuthi i-PEG isetshenziselwa abantu abane-ALS ukugcina isisindo somzimba sizinzile. Odokotela abahlukene banemiqondo ehlukene ngesikhathi sokuhamba kahle kwenqubo ye-PEG futhi baqala ukudla ngale ndlela.
Izwi elivela
Izinqubekela phambili zenziwe eminyakeni yamuva ekusekeleni nasekwelaleni kwe-ALS. Ukuzifundisa ekwenzeni nokwelashwa kwe-ALS kungakusiza uqonde lokhu kutholakala okunzima nokulukhuni. Khuluma nodokotela wakho ngalokho ongakwenza ukuze usize umuntu onama-ALS aphile ngokunethezeka isikhathi eside ngangokunokwenzeka.
Imithombo:
> Amaqiniso Okufanele Ukwazi Nge-ALS. ALS Association. http://www.alsa.org/about-als/facts-you-should-know.html.
> Imibuzo evame ukubuzwa mayelana neRadicava (i-Edaravone). ALS Association. http://www.alsa.org/research/radicava/radicava-enjalo-asked-questions.html.
> Miller RG, et. al. Ukuzivocavoca Ukubuyekezwa kweParameter: Ukunakekelwa kwesiguli nge-amyotrophic lateral sclerosis: Imithi yokwelapha izidakamizwa, okunomsoco kanye nokuphefumula (ukubuyekezwa okusekelwe ebufakazini): Umbiko weKomidi leMigomo yezinga eliphezulu le-American Academy of Neurology. I-Neurology 2009; 73; 1218-1226.
> Pinto S, uCarvalho MD. Ukuphefumula impilo emisha ekwenzeni ukwelashwa okuqhubekayo kokuhluleka ukuphefumula ezigulini ze-amyotrophic lateral sclerosis. Ukuphathwa kwezifo ze-Neurodegenerative . 2014; 4 (1): 83-102. i-doi: 10.2217 / nmt.13.74.