I-Disorder efana ne-Parkinson's kodwa With Differences
Lapho umlingisi waseBrithani nomculi uDudley Moore bafa ngo-Mashi 27, 2002, imbangela esemthethweni yokufa yayibhalwe njenge-pneumonia. Kodwa, eqinisweni, Moore wayelokhu elwa nesimo esingavamile esaziwa ngokuqhubekayo kwe-supranuclear palsy (PSP) eyenza ukuwohloka kancane kancane kwezinxenye zobuchopho ezilawula ukulinganisela, ukulawula imisipha, umsebenzi wokuqonda, nokunyakaza okuzithandela nokuzithandela njengokugwinya nesiso ukunyakaza.
Izimbangela Zokuqhuma Kwesifo Sokushisa Okuphakeme Okuqhubekayo
Ngenkathi imbangela ye-palsy yokuhamba phambili ye-supranuclear engaziwa kakhulu, icabanga ukuthi ihlotshaniswa nokuguquguquka kwengxenye ethile yegesi eyaziwa ngokuthi i-chromosome 17.
Ngeshwa, akuyona yonke into engavamile ukuguquka. Nakuba cishe wonke umuntu one-PSP unalezi zakhi zofuzo, ngakho-ke, yizinxenye ezimbili kwezintathu zabantu abaningi. Ngenxa yalokho, ukuguqulwa kwezinto kubonakala sengathi kunomthelela esikhundleni sokuphela kwesici se-disorder. Izinhlayiya zemvelo nezinye izingqinamba zofuzo zingase futhi zidlale ingxenye.
Ososayensi abakakaqiniseki ngokuphelele ukuthi izinga le-PSP lihlotshaniswa nesifo sika-Parkinson noma se-Alzheimer lapho sinazo izimpawu ezithile zesici.
I-PSP itholakala ukuthi ithinte umuntu oyedwa kubantu abangu-100 000 kungakhathaliseki ukuthi uhlanga, geography, noma umsebenzi. Amadoda athambekele ekuthintweni kancane kunabesifazane. Izimpawu zivame ukuvela phakathi kweminyaka engama-50 no-60.
Izimpawu ze-PSP
Esinye sezici eziningi kakhulu, izimpawu ze-PSP zihlanganisa ukulawula ukunyakaza kwamehlo, ikakhulukazi ikhono lokubuka phansi. Lesi simo, esaziwa ngokuthi i-ophthalmoparesis, senza ukukhubazeka noma ukukhubazeka kwemisipha ethile eduze kwe-eyeball. Ukunyakaza okuqondile kwamehlo nakho kuthinteka kakhulu.
Njengoba isimo siqhubeka, ukubuka phezulu kungahle kuthinteke.
Ngenxa yokuntuleka kokulawula okubalulekile, abantu ababhekana ne-ophthalmoparesis bazohlale bekhononda ngemibono kabili , umbono obonakalayo, nokuzwela okukhanya. Ukulawulwa kobuchopho obubi kungase kwenzeke futhi.
Njengoba ezinye izingxenye zobuchopho zithinteka, i-PSP izobonakala ngezinhlobo eziningi zezibonakaliso ezivamile ezivame ukwedlula isikhathi. Lokhu kufaka:
- Ukungaqiniseki nokulahlekelwa kwesilinganiso
- Ngokujwayelekile ukunciphisa ukunyakaza
- Ukukhipha amagama
- Kunzima ukugwinya (dysphagia)
- Ukulahlekelwa kwememori
- Ama-spasms ebusweni buso
- Ukujikijela emuva kwekhanda ngenxa yokuqina kwentamo yezintamo
- Ukungabikho kwe-Urinary
- Izinguquko ekuziphatheni, kufaka phakathi ukulahlekelwa kokuvimbela kanye nokuqhuma okungazelelwe
- Ukunciphisa umcabango onzima futhi ongaqondakali
- Ukulahlekelwa amakhono enhlangano noma okuhlela (njengokuphatha imali, ukulahlekelwa, ukuhambisana nokuzibophezela komsebenzi)
Ukuxilongwa kwe-PSP
I-PSP ivame ukungaqondakali kahle ngezigaba zakudala zesifo futhi ivame ukungena ematheni ekungeneni kwezindlebe zangaphakathi, inkinga ye-thyroid, isifo noma isifo se-Alzheimer (ikakhulukazi asebekhulile).
Ukuxilongwa kwenziwa ngokusekelwe ngokubukeza izimpawu. Kuyindlela abadokotela abadingeka ngayo ukukhipha ezinye izimbangela ezikhona. Ukuskena kwe- imagination ye-resonance imaging (MRI) ye-brainstem ingasetshenziswa ukusekela ukuxilongwa.
Ezimweni ze-PSP, kuzoba nezibonakaliso zokuqeda (atrophy) engxenyeni yobuchopho obuxhumanisa ubuchopho emthonjeni womgogodla. Ku-MRI, umbono ohlangothini lobu buchopho buzobonisa ukuthi yini abanye ababiza ngokuthi "i-penguin" noma "isibonakaliso se-hummingbird" (esibizwa kanjalo ngoba isimo sayo sinjengeyenyoni).
Lokhu, kanye nezimpawu, uphenyo oluhlukile, kanye nokuhlolwa kofuzo, kunganikeza ubufakazi obudingekayo ukuze kutholakale ukuxilongwa.
Indlela i-PSP eyahlukana ngayo nezifo ze-Parkinson
Ukuze ahlukanise i-PSP evela ku-Parkinson, odokotela bazocabangela izinto ezifana nokuhlelwa komlando nomlando wezokwelapha.
Isibonelo, abantu abane-PSP bazogcina ngokuhlelekile noma ukusekelwa okuxhaswe emuva, ngenkathi abantu abane-intanethi ka-Parkinson bevame ukuba nesimo esiphezulu esiphezulu.
Ngaphezu kwalokho, abantu abane-PSP bajwayele ukuwa ngenxa yokuntuleka kokulinganisela okuqhubekayo. Ngenkathi abantu abane-Parkinson nabo besengozini enkulu yokuwa, labo abane-PSP bavame ukwenza kanjalo emuva ngenxa yokuqina kobunzima bezintambo nokuhlehliswa emuva.
Ngalokho kuthiwa, i-PSP ibhekwa njengengxenye yeqembu lezifo ezingenayo i-neurodegenerative ebizwa nge- Parkinson-plus syndrome lapho abanye befaka khona i-Alzheimer's.
Izinketho zokwelapha
Ayikho ukwelashwa okuqondile kwe-PSP. Ezinye iziguli zingase ziphendule izidakamizwa ezifanayo ezisetshenziselwa ukuphatha i-Parkinson, njenge- levodopa , nakuba impendulo iba yinto empofu (okunye ukuhlukana okusetshenziselwa ukuxilonga lesi sifo).
Imithi ethile yokucindezeleka, njenge-Prozac, i-Elavil neTofranil, ingasiza ngezinye izimpawu zokucabanga noma zokuziphatha umuntu angase abe nakho. Ngaphandle kwemithi, izibuko ezikhethekile (ama-bifocals, ama-prisms) angasiza ngezinkinga ezibukwayo, kuyilapho ukuhamba ngezinsiza nezinye izinto eziguquguqukayo kungathuthukisa ukuhamba nokuvimbela ukuwa.
Ngenkathi ukwelapha ngokomzimba kungavamile ukuthuthukisa izinkinga zezimoto, zingasiza ukugcina amakhemikhali womjovo nokuvimbela ukuwohloka kwemisipha ngenxa yokungasebenzi. Ezimweni ze-dysphagia ezinzima, ithubhu yokudla ingadingeka.
Ama-electrode asetshenziselwa ukukhiqiza kanye nama-generators we-pulse asetshenziselwa ukwelashwa okujulile kokuvuselela ubuchopho ama-Parkinson akazange aqinisekiswe ukuthi aphumelele ekuphatheni i-PSP.
Izwi elivela
Naphezu kokungaqondi ngokuphathelene ne-PSP kanye nezinketho zokwelashwa okulinganiselwe, kubalulekile ukukhumbula ukuthi lesi sifo asinayo inkambo ebekiwe futhi ingahluka ngokuphawulekayo kumuntu nomuntu. Ngokunakekelwa kwezempilo okuqhubekayo nokudla okunempilo okuhle, umuntu ophethe i-PSP, empeleni, angaphila iminyaka, ngisho nangamashumi eminyaka, ngemva kokuxilongwa.
Kubantu ngabanye kanye nemindeni ephila nalesi sifo, kubalulekile ukufuna ukwesekwa ukugwema ukuzihlukanisa kanye nokuthola ulwazi olungcono olubhekene nesiguli kanye nokudluliselwa. Lezi zinhlangano zihlanganisa izinhlangano ezifana ne-New York City-Based CurePSP ezinikezela ngamaqembu omuntu kanye namasevisi e-intanethi, isiqondisi sodokotela ochwepheshe, nenethiwekhi yabaxhasi abaqeqeshiwe abaqeqeshiwe.
> Umthombo:
> Ling, H. "Indlela Yomtholampilo Yokuthuthukiswa Kwesifo Sokushisa Isikhulu Sokuhamba Kwesifo Esiphakeme." I-Journal ye-Disvement Disorders. 2016; 9 (1): 3-13.