Imizamo Ejwayelekile Yokuhlola Nokuthi Kungani Ukuthola Ukuxilonga Kunzima
Njengoba izimpawu ze-idiopathic pulmonary fibrosis (i- IPF ) zilinganisa lezo zinhliziyo eziningana nezinhlobo zamaphaphu, ngokuvamile kuthatha isikhathi esithile sokuthola lesi sifo. Phakathi nalesi sikhathi, ngokuvamile unyaka noma amabili, iziguli zivame ukubona odokotela abaningi bezama ukuthola isizathu sezimpawu zabo.
Izimpawu ezivamile ze-IPF
Njengezinye izifo zamaphaphu, njenge-COPD, kunomonakalo omkhulu emaphashini ngaphambi kokuba izimpawu zivele.
Lezi zimpawu zingabandakanya:
- Ukuphefumula , ikakhulukazi ngomsebenzi, ngokuvamile kuyisibonakaliso sokuqala. Ngokuhamba kwesikhathi lobunzima bokuphefumula bubuhlungu kangangokuthi ukuphefumula kufinyeleleke ngisho nokuphumula.
- Ukukhwehlela okuqhubekayo ngokuvamile okumile (okungewona okhiqizayo)
- Okuncane, ukuphefumula okusheshayo
- Ukukhathala
- Ukulahlekelwa isisindo ngaphandle kokuzama ( ukulahlekelwa kwesisindo esingachazwanga )
- I-Clubbing - I-Clubbing yisimo lapho iminwe nezinzwani zanda khona ekugcineni, kufana nesipuni esiphezulu.
- Ama-muscle nama-joint aches
Ukuhlolwa kwe-IPF
Njengamanje, akukhona ukuhlolwa kokuhlolwa kwe-IPF, futhi ukuxilongwa kusekelwe kubantu abanikeza izimpawu. Inqubo yokuhlola umdlavuza wamaphaphu , noma kunjalo, ingathatha i-IPF kubantu ukuthi ngubani ohlolwayo avunyelwe futhi anconywa.
Ukuxilongwa nokuThuthukisa
Ukuxilongwa kwe-IPF kuvame ukuthatha isikhathi esithile, nabantu abaningi abahamba unyaka noma amabili futhi bebona odokotela abaningi ngaphambi kokuba kutholakale ukuxilongwa.
Isizathu salokhu ukuthi izimpawu zokuqala ze-IPF zilinganisa kakhulu lezi ezinye izimo eziningi, kuhlanganise nesifo senhliziyo. Abantu abaningi baphuthunyiswa inhliziyo ngaphambi kokuba bathole ukuthi basekelwe ezimpawu ezivamile zokuqala.
Okunye okuvivinywa udokotela wakho angayenza umyalelo kufaka phakathi:
- I-CT High-resolution CT Scan: I- IPF ivame ukuxilongwa ngokusekelwe ekutholeni okujwayelekile okubonwe esitokisini esiphezulu se-CT yesibindi. Ku-CT scan, i-fibrosis ibonakala kunoma iyiphi i-radiologist ebhekisela njengephethini lezinyosi.
- I-lung biopsy: Kunezikhathi lapho ukuhlolwa kwe-CT kuphela kungenza kuqinisekiswe ukutholakala kwe-IPF, kodwa uma kutholakala ukuthi ukuxilongwa kubhekene ne- lung biopsy kunganconywa . Lokhu kungenziwa njengengxenye ye-bronchoscopy, nge-incision encane esifubeni (thoracoscopy) noma nge-thoracotomy. I-biopsy yenzeka ngokuyinhloko ukulawula ezinye izimbangela zamaphaphu njengesifo somdlavuza wamaphaphu noma i-sarcoidosis.
- Ezinye izivivinyo ezisiza ekuxilongweni nasezikhundleni: Ukuhlanganiswa kokuhlolwa kanye nezinye izivivinyo ngokuvamile kwenziwa kokubili ukusiza ekuxilongweni, ukunquma ukuthi amaphaphu asebenza kahle kangakanani, futhi ukuthola ukuthi isifo sifinyelele kangakanani. Ezinye zazo zihlanganisa:
- Ukuhlolwa komlando kanye nomzimba.
- I-Spirometry - I-Spirometry yinto ehlolwayo ebheke ukuthi umoya ukhululeka kangakanani esikhathini esingesigamu esisodwa, futhi uyisibonakaliso somsebenzi wamaphaphu.
- Okunye ukuhlolwa komsebenzi wamapulmoni
- Oximetry
- Amagesi egazini egazi - Zombili ama-oxyetri ne-ABG zenziwa ukuhlola okuqukethwe kwe-oksijini yegazi.
- Ukuhlola isifo sofuba
- Ukuhlolwa kwegazi - Ucwaningo lubheka ama-biomarker azosiza ekutholeni lesi sifo esikhathini esizayo.
I-Genetic Predisposition: I-fibrosis ye-Idiopathic yamapayipi ingase isebenze emindenini kanye nezinguquko ezithile (nge-chromosome 11) zitholakale zivamile kwi-IPF yomndeni.
Izwi elivela
Kungakhathaliseki ukuthi i-IPF yakho yithatha isikhathi esithile ukuxilonga, uma utholakala ukuthi uyazi ukuthi unezinketho zokwelapha ezitholakalayo, futhi ngaphezulu kuphandwa futhi kuthuthukiswe . Kanye nokulawula izinto ezithile zokuphila, ungaqhubeka uphila kahle nge-fibrosis ye-idiopathic pulmonary .
> Imithombo:
Antoniou, K., Tomassetti, S., Tsitoura, E., noCancheri. Umdlavuza we-Idiopathic pulmonary ne-lung lung: isibuyekezo somtholampilo nesipathogenesis. Ama-Opinions amanje ku-Pulmonary Medicine . 2015 Sep 18. (Epub ngaphambi kokuphrinta).
de Boer, K., noJee Lee. Ukuncintisana okungaziwa ngaphansi kwe-fibrosis ye-idiopathic pulmonary: ukubuyekezwa. I-Respirology . 2015 Sep 13. (Epub ngaphambi kokuphrinta).
Oldham, J. et al. I-TOLLIP, i-MUC5B ne-Response ku-N-acetylcystein Phakathi Kwabantu abane-Idiopathic Pulmonary Fibrosis. I-American Journal of Respiratory and Critical Care Medicine . 2015 Sep 2. (Epub ngaphambi kokuphrinta).
O'Riordan, T., Smith, V., noG. Raghu. Ukuthuthukiswa kwama-Novel Agents for Idiopathic Pulmonary Fibrosis: ukuqhubekela phambili ekukhethweni kwelitshe kanye nokuklanywa kwesilingo somtholampilo. Isifuba . 2015 Meyi 8. (Epub ngaphambi kokuphrinta).
Raghu, G. et al. Ukuhlolisisa i-idiopathic pulmonary pulmonary fibrosis nge-CT-high-resolution CT ezigulini ezinobumbalwa obuncane noma obungenabuzwayo obuhle bokuthi u-honeycombing: ukuhlaziywa kwesibili kokulingwa okungahleliwe nokulawulwa. I-Lancet Imithi Yokuphefumula . 2014. 2 (4): 277-84.