Iyini i-IPF nokuthi Iyini Eyibangela?
Uma wena noma othandekayo uthola ukuthi une-idiopathic pulmonary fibrosis (i-IPF), yazi ukuthi bambalwa kakhulu abantu abajwayele lesi sifo. Uma uqala ukucinga imininingwane endala ku-IPF, awukwazi ukuthola izindaba ezinhle kakhulu. Kuze kube-2014 kwakungekho ngempela imithi etholakalayo eyenza umehluko omkhulu kubantu abaphila nalesi sifo. Ngesibindi, lokho kuyashintsha-manje kukhona ukwelashwa kwalesi sifo esithuthukisa izimpilo.
Iyini i-Idiopathic Pulmonary Fibrosis (IPF)?
I-IPF iyindlela ejwayelekile kakhulu yeqembu lezifo ezibizwa ngokuthi i-idiopathic interstitial pneumonia. Igama elithi interstitial lisho ukuthi isimo uma sikhona ezindaweni zamapayipi phakathi kwe-alveoli (ama -sac amancane emoyeni ekupheleni komuthi wokuphefumula lapho kwenzeka khona ukushintshaniswa kwe-oksijeni ne-carbon dioxide) nase-linings alveolar. I-Fibrosis isho ukusho okuncane. Lokhu kukhishwa ezindongeni ze-alveolar kanye nezicubu eziphakathi kwazo eziphazamisa ikhono le-oksijeni ukuba lidlule ezindongeni ze-alveoli kanye negazi.
Esikhathini esidlule, kwakucatshangwa ukuthi i-IPF yinkqubo yokuvuvukala. Manje kucatshangwa ukuthi kuqala ngomonakalo emaphashini kusukela ekuhlanganiseni kwemithombo, kulandelwa ukuphulukiswa okungavamile-fibrosis.
Ukuze ucabange ukuthi lokhu kuyinjani, cabanga ukuthi unqunywe esikhumbeni sakho esiphila ngesibalo. Kubantu abaningi, ukusika kunophilisa ngomugqa omuhle obomvu ophenduka umhlophe ngesikhatsi.
Kwamanye abantu, isikhumba siyasiphilisa ngendlela engavamile, eshiya uketshezi olumile nolunqabile lwe-keloid . I-fibrosis e-IPF ifana nalolu hlobo lokusila, kodwa alubonakali ngaphandle komzimba.
Ngaphandle kokuba yisifo esiqhubekayo, amaphesenti ayishumi abantu abane-IPF kulindeleke ukuba bakhe umdlavuza wamaphaphu.
I-IPF evamile kangakanani?
Izinombolo ziyahluka uma zibuka izigameko ze-fibrosis ye-idiopathic pulmonary, kodwa kuvumelana ukuthi isimo asihloliswanga; abantu abaningi banesipiliyoni se-IPF futhi batholakala ukuthi banesimo esithile, noma badlula ngaphambi kokuba kutholakale ukuxilongwa okufanele.
Ngokusekelwe kokuhlaziywa okunye e-United States, kutholakale ukuthi lesi sigameko (inani labantu abaxilongwa ngonyaka) we-IPF kwakungu-58.7 kubantu abayi-100,000. Kwesinye isifundo se-2011, kwatholakala ukuthi ukusabalalisa (inani labantu abaphila nalesi sifo) se-IPF kwakungama-495.5 amacala kubantu abayizigidi ezingama-100 000 abahlinzeka ngemithi. (Isifo esingavamile sichazwa njengomuntu ongaphansi kuka-1 kubantu abangu-50,000 abanalo izifo, ngakho-ke i-IPF ayinjwayelo, kodwa ayivamile.)
Ukubheka ukushona kwezilinganiso ze-IPF kwabikezela ukuthi abantu abangu-13 000 kuya ku-17 000 bazofa nge-IPF e-United States ngo-2014 futhi phakathi kwabantu abangu-28 000 no-65 000 bazofa eYurophu. Ukuze ubeke lokhu ngombono, cishe abantu abangu-40 000 bafa ngomdlavuza wesikhumba minyaka yonke e-United States, okwenza i-IPF ibe imbangela enkulu yokugula nokufa.
Ubani othola i-IPF? Izimbangela Nezici Zengozi
Akukwazi ukuthi yini eyenza i-IPF, ngakho-ke, igama elithi "idiopathic," elisho ukuthi "asazi imbangela." Lokho kusho ukuthi kunezici ezinobungozi ezingase zibeke abantu esibhedlela.
Ezinye zazo zihlanganisa:
- Ubudala - I-IPF ivame ukutholwa kubantu asebekhulile nabakudala.
- Ukubhema - Abantu abangamaphesenti angama-60 abakha i-IPF banomlando wokubhema.
- Izifo ezinjenge -Virus njengegciwane le-Epstein-Barr , elibangela i-mononucleosis esithathelwanayo.
- Ukuvezwa kwemvelo nokusebenza.
- Isifo se-reflux se-gastroesophageal (GERD) - Iningi labantu abathintekayo abane-IPF banomlando we-GERD ngenhliziyo.
- Umlando womndeni (i- genetic predisposition ) - I-IPF isebenza emindenini futhi ukushintshashintsha kwezakhi zofuzo kubonakala kwandisa ingozi.
Kunezimbangela eziningana eziyaziwayo ze-fibrosis ye-pulmonary, njenge-radiation nemithi, kodwa lezi ngencazelo ngeke zihlukaniswe ngaphansi kwe-fibrosis ye-idiopathic pulmonary.
Izwi elivela
Ngenxa yezizathu ezingaziwa, ukufa okuvela ku-IPF kubonakala sengathi kuyanda emhlabeni wonke. Ngesikhathi esifanayo, kuthuthukiswa ukwelashwa okusha nokuthuthukiswa njengoba ucwaningo oluqhubekayo kulesi sifo luqhubeka . Emva kokuxilongwa , nodokotela wakho kufanele asebenze ndawonye ukuze athole ukhetho lwezokwelapha olusebenza ngecala lakho elilodwa. Kunezinhlobo ezihlukahlukene zemithi etholakalayo, kanti ezinye iziguli zingase zikhethwe ukufakelwa kwamaphaphu. Ukwengeza, amaqembu okusekela ayatholakala lapho ungaxhuma khona nabanye futhi ufunde amasu okuphila kangcono naphezu kokuba ne-IPF. Ekugcineni, indima yakho esebenzayo ekunakekelweni kwezempilo ingenza umehluko, futhi.
> Imithombo:
Antoniou, K., Tomassetti, S., Tsitoura, E., noCancheri. Umdlavuza we-Idiopathic pulmonary ne-lung lung: isibuyekezo somtholampilo nesipathogenesis. Ama-Opinions amanje ku-Pulmonary Medicine . 2015 Sep 18. (Epub ngaphambi kokuphrinta).
Ghebremariam, Y. et al. Umphumela we-pleiotropic we-proton pump inhibitor esomeprazole eholela ekususweni kwe-lung inflammation ne-fibrosis. Journal of Medicine Medicine . 2015. 13: 249.
UHutchinson, J., McKeever, T., Fogarty, A., Navaratnam, V., no R. Hubbard. Ukwandisa ukufa kwezwe emhlabeni kusuka ku-fibrois ye-idiopathic yamaphaphu ekhulwini lama-20 leminyaka. Amanothi we-American Thoracic Society . 2014. 11 (8): 1176-85.
Idiopathic Pulmonary Fibrosis Research Clinic Network, uMartinez, F., deAndrade, J., Anstrom, K., King, T., noG. Raghu. Ukuhlolwa okungahleliwe kwe-acetylcysteine ku-fibrosis ye-idiopathic pulmonary pulmonary. I-New England Journal of Medicine . 2014. 370 (22): 2093-101.
IsiSpanishi, uP., Maher, T., noL. Richeldi. I-fibrosis ye-Idiopathic pulmonary: Ukuthuthukiswa kwakamuva kwindlela yokwelashwa kwemithi. I-Pharmacology & Therapeutics . 2015. 152: 18-27.