I-pulmonary arterial hypertension isifo esibi kakhulu lapho kukhona khona ukwelashwa kodwa akukho ukwelashwa, ngokweNational Heart, Lung, ne-Blood Institute. Ukuphefumula kwesifo se-pulmary secondary kungabangela noma kwenzeka ngenxa yesinye isimo sesibili.
Izimbangela ze-Hypertension Pulmonary
Ukucindezeleka okubangelwa yi-pulmonary arterial hypertension (noma ukucindezeleka kwegazi emaphashini) yisimo esingavamile kodwa esibi kakhulu sezokwelapha.
Le nkinga, engahambisani nokwanda komfutho wegazi (isisindo somfutho wegazi), ibangelwa ukulahlekelwa kwevolumu yamapayipi kanye nokulahleka kokuguquguquka (ukuqina) komshini wepulmonary umsebenzi wayo ukubuyisela igazi emaphashini okuphefumula.
Izifo Zama-Rheumatic Associated With Hypertension Pulmonary
Umfutho wegazi ophezulu we-pulmonary uhlotshaniswa nemibandela eminingi. Ezigulini ezinezinkinga ezinkulu zamaphaphu (i-fibrosis njengoba ibonakala ku- scleroderma futhi ngezinye izikhathi i- arthritis ye-rheumatoid ), kukhona amandla amaphaphu anciphile ukuze inhliziyo ikhulise ukucindezela okudingekayo ukuqhuma igazi ngokusebenzisa umthambo wamapayipi emaphashini. Ezinye iziguli zithuthukisa ukucindezela komthamo wamapayipi ngenxa yokunciphisa umshini. Lokhu kungabonakala ezimweni ezifana ne-scleroderma (ngokuvamile efonini elinganiselwe elibizwa ngokuthi i-CREST) noma ngaphansi kwe-lupus (systemic lupus erythematosus) ejwayelekile. Muva nje lolu hlobo lwegazi lomfutho wegazi luyatholakala ukuthi luhlotshaniswa nezidakamizwa zokudla ezingasemakethe.
Izimpawu
Izimpawu zalesi simo zihlanganisa ukuphefumula kokuphefumula nokuhlungu kwesifuba. Ukuxilonga kungaphakanyiswa yi-ultrasound ye-non-invasive yenhliziyo (i-echocardiogram). I-catheterization ye-cardiac (i-catheterization ye-heart) enezinye izingozi zezokwelapha ngokuvamile kuvame ukuqinisekisa ukuxilongwa.
Ukwelapha
Esikhathini esedlule, kwakungekho ukwelashwa okuncane okutholakala kule nkinga eyenza ukuhlushwa okubi.
Ngenhlanhla, kunezindlela zokwelapha ezintsha ezitholakalayo ukusiza iziguli ezinezimo zabo kufaka:
- i-epoprostenol (isidakamizwa esifushane esidinga ukumnika okuqhubekayo nge-IV enkulu)
- i-treprostinil (elawulwa ukufakwa okuncane okuqhubekayo)
- i-bosentan (enikezwe ngomlomo)
- i-sildenafil (inikezwe ngomlomo)
- iloprost (inhaled)
Izindlela zokwelapha ezengeziwe zifaka oksijeni, abambalwa begazi, izidakamizwa kanye nokuvuselelwa kwe-cardiopulmonary. Uma kutholakala nale nkinga, kungcono ukubona udokotela wamaphaphu onolwazi kule nkinga.
Impendulo eyanikezwa nguScott J. Zashin, MD, uprofesa wothisha wezempilo e-University of Texas Southwestern Medical School, Division of Rheumatology, eDallas, eTexas. UDkt. Zashin ungudokotela ozofika esibhedlela sasePresbyterian yaseDallas nasePlano. Ungumunye we-American College of Physicians kanye ne-American College of Rheumatology kanye nelungu le-American Medical Association. UDkt. Zashin ungumbhali we- arthritis ngaphandle kwemizwa - Isimangaliso se-anti-TNF Blockers kanye nombhali-mbhali we- Natural Arthritis Treatment .