Izifo zikaPick and Corticobasal Degeneration zithinta ama-Circadian Rhythms
I- dementias ye-frontotemporal efana nesifo sika-Pick nesifo se- corticobasal sithinta kanjani ukulala? Funda ngalezi zimo, kufaka phakathi izimpawu zabo ezivame kakhulu, nokuthi ukucindezeleka okuthinta kanjani lobes yangaphambili nangokwesimo sobuchopho kuthinta imibuthano yokulala neyemvelo.
Kuyini Ukudemeza Kwama-Frontotemporal?
I-Dementia ihlanganisa ukuphazamiseka okuhlukahlukene okuthinta kancane kancane ubuchopho futhi kungathinta inkumbulo, ukunakekelwa, ubuntu, ulimi, ukuxazulula izinkinga, nokusebenza kwansuku zonke.
Kulesi sigaba esibanzi, kunezimo ezithinta izindawo ezithile zobuchopho futhi ziholele ekusebenzeni okungasebenzi. Enye yalezi zinhlobo ezithize yi-frontotemporal dementia (FTD), isifo esithinta i-lobes yangaphambili neyesimo sobuchopho (etholakala emaceleni nangaphambili). Ithinta amaphesenti angu-5 kuya kwangu-15 abantu abane-dementia.
Ukuwohloka komqondo kwe-frontotemporal kufaka izimo ezimbili ezihlukile: isifo sikaPickk kanye nesifo se-corticobasal. Le yangaphambili ibhekene nokuthola okungavamile okubizwa ngokuthi imizimba ye-Pick, etholakala ngaphakathi kwe-neurons yobuchopho equkethe inani elingavamile noma uhlobo lweprotheyini okuthiwa i-tau. Kunezakhi zofuzo ezibonakala zifaka isandla esihlokweni saleso sifo, kodwa isizathu esiqondile sisaziwa. Isifo sika Pick yisimo esingavamile esivame ukuvela kubantu abaneminyaka engama-40 kuya kwengu-60 ubudala.
Ngokuphambene, i-corticobasal degeneration (i-CBD) ibonakala ngokulahlekelwa kancane kwe-neurons ku-cortex ye-cerebral ne-basal ganglia, izindawo ezimbili zobuchopho ezibalulekile ekucabangeni nasekuhambeni.
Le-atrophy ingathinta uhlangothi olulodwa lomzimba ekuqaleni, kodwa njengoba lesi sifo siqhubeka, izinhlangothi zombili zomzimba zingase zihileleke. I-CBD ingaqala cishe uneminyaka engama-60.
Ziyini Izimpawu Zengqondo Ye-Frontotemporal Dementia?
Indawo yobuchopho ethintekayo ekuhloleni komqondo kwe-frontotemporal kuholela esimweni esithile sezimpawu.
Nge-Pick's disease, ubuntu bokuqala kanye nezinguquko zokuziphatha kungenzeka. Lokhu kungabonakala njengokunzima kuzilungiselelo zomphakathi ngokuziphatha okungavamile, okuphoqelekile, noma okungalungile. Ngokuphambene nalokho, isifo se-Alzheimer ngokuvamile sibonakala ngokulahlekelwa inkumbulo njengesibonakaliso esiyinhloko. Abantu abanezifo zika-Pick bangase babe nezinguquko eziphuthumayo noma babonakale bengakhathazeki (kungakhathaleli), futhi kungase kube nezinkinga ezihlobene nenkulumo (ebizwa nge-aphasia) nokucabanga okungafanelekile. Ngokuhamba kwesikhathi, ubuthakathaka noma ukutholakala kungase kuthuthuke. Ngokusemthethweni, lezi zimpawu zizoqhubeka ziba zimbi nakakhulu.
Ukuguqulwa kwama-Corticobasal kunezimpawu ezengeziwe ngenxa yemiphumela kwi-basal ganglia. Lokhu kungabangela izimpawu ezifana nesifo sikaParkinson, kuhlanganise nokuqina, ukuhamba kancane, nokungalingani. Abantu abane-CBD bazophinde bahlakulele i-apraxia, okungukuthi abakwazi ukuhamba ngenhloso naphezu kokuthi amandla namandla nokusebenza kukhona. Isibonelo, umuntu ophethe i-CBD angeke akwazi ukulinganisa ukunyakaza kwamazinyo, ukubhema ugwayi, ukuhlamba izinwele, noma ukudla isobho kusuka ku-spoon. Lezi zinkinga ekugcineni zenza kube nzima ukuhamba. Inkulumo ingase iyanqamuka, futhi kunzima ukugwinya kungase kwenzeke.
Dementia Frontotemporal kanye nemiphumela yokulala
Ukulala kwabantu abane-dementia ye-frontotemporal kungashintsha, futhi empeleni, iphethini lokulala nokuvuka liguqulwa.
Isigqi esivamile se-circadian sihlukana kakhulu, ngenhlanganisela yalezi zombili zenzeka kokubili imini nobusuku. Lokhu kubonakala kudluliselwa ngaphezu kwezinguquko ezingenzeka uma uhlala endaweni yokuhlala esizwa njengendlu yokuhlengikaza. Abantu abathintekayo bavame ukuba nesigaba sokulala esiphezulu , belele futhi bavuke ngaphambi kokujwayelekile.
Uma kugcinwa nge- electroencephalogram (i-EEG) , isigqi samagagasi obuchopho asivamile: kuhamba kancane ngesikhathi sokuvuka. Noma kunjalo, kungase kube okujwayelekile kubantu abangaba yingxenye yesithathu yabantu, ngakho akusivivinyo oluphelele ukuxilonga lesi simo.
Okunye ukuphazamiseka kokulala kungahle kwenzeke ku-dementia ye-frontotemporal ngezizathu ezifanayo ezenzeka kuwo wonke umuntu, kufaka phakathi i- apnea yokulala .
Lezi zingadinga ukuhlolwa okungaphezulu kanye nezinga elifanele lokwelashwa, kuye ngokuthi ukukhubazeka okungaphansi kokungena komqondo.
Ukwelashwa nokubikezelwa kwe-Frontotemporal Dementia
Azikho zokwelapha eziqondile ezinganciphisa noma eziguqula inkambo yale-dementias. Ukwelashwa, kuhlanganise nokusetshenziswa kwemithi, kungase kuhloswe ukunciphisa izimpawu ezithile, kodwa ngeshwa, lezi zingase zibe nokumelene nokungenelela. Ukunakekelwa okusekelayo kuyadingeka, kubandakanya ukuhlinzeka indawo ephephile ngezinga elidingekayo losizo.
Ukuchazwa kwesifo sengqondo se-frontotemporal ngokwemvelo kuvamisile, ngenkambo eqhubekayo futhi ikhula - nokukhubazeka kuyisici esivamile sezifo. Isifo sikaPick sizoholela ekufeni eminyakeni emibili kuya kwengu-10, ikakhulukazi kusuka ekutheleleni (njengokungenwa kwe-pneumonia noma ukutheleleka kwamagciwane), noma enye inkinga yokukhubazeka okunzima. Ukuhlukunyezwa kwe-Corticobasal kulandela isikhathi esifanayo, kuqhubeka iminyaka engaphezu kuka-6 kuya kwengu-8 futhi kuholela ekufeni ngendlela efanako.
Kubalulekile ukuthi abanakekeli nabathandekayo babantu abane-dementia ye-frontotemporal balondoloze inethiwekhi yokusekela futhi bathole usizo njengoba kudingeka. Ukuphazamiseka ubuthongo kungaba ingxenye encane kumongo wezinye izinkinga, kodwa ukuphazanyiswa kwamaphethini okulala kusalokhu kuthatha umonakalo kumuntu othintekile kanye nabanakekeli bakhe. Ngakho ukuphatha ukulala ukuphazamiseka kungase kuzuze ukungenelela futhi unciphise umthwalo wokunakekelwa.
Uma uthola ukuthi udinga usizo olungeziwe ekulawuleni lesi simo, ungazuza ngokubonisana nodokotela wezinzwa, ongasiza ekuxhumaniseni ukunakekelwa nokuhlinzeka ngokudluliselwa kwezinsiza emphakathini wakho.
Imithombo
Kryger, MH et al . "Izimiso Nemikhuba Yokulala Imithi." Elsevier , edition 5, iphe. 1042.
"Isifo sika Pick." I-PubMed Health . Kufinyelelwe: Januwari 30, 2013.
"I-NINDS Corticobasal Degeneration Information Page." I-National Institute of Neurological Disorders and Stroke . Kufinyelelwe: Januwari 30, 2013.