I-Mycosis fungoides (MF) yiyona ejwayelekile kakhulu kwi- T-cell lymphomas , iqoqo legazi elingavamile elikhula esikhumbeni. I-Sezary syndrome, ifomu elingavamile kakhulu, livela cishe ku-5% kuwo wonke amacala we-mycosis fungoides. E-United States, amacala angaba ngu-1000 amasha we-mycosis fungoides okwenzeka ngonyaka.
I-MF ithinta amadoda kabili kaningi njengabesifazane, futhi ivame kakhulu kubantu abamnyama kunabantu abamhlophe.
I-Mycosis fungoides ingaqala nganoma yisiphi isikhathi, kodwa iminyaka ejwayelekile kakhulu ineminyaka engu-50 ubudala. Isizathu sesifo asikwazi.
Izimpawu ze-Mycosis Fungoides
I-Mycosis fungoides iqhubeka ngezigaba, ezichazwa izimpawu zesikhumba, ezifaka:
- Isigaba se-Patch - Isikhumba sakha ama-flat, abomvu obomvu; kubantu abanobumnyama abangase babonakale sengathi bangabonakaliswa kakhulu noma abomvu kakhulu. Lezi zimpawu zesikhumba zinzima kakhulu. Ezinye izindawo zingase zikhuliswe futhi zikhuni, futhi ziyaziwa njengezigcawu. Ama-patches nama-plaque ngokuvamile avela emagodini, ubuhlungu, izinqulu, ngaphansi kwezikhali, nasezibelethweni / esifubeni.
- Isigaba sezinambuzane zesikhumba - Ama-red-violet aphakanyisiwe (ama-nodules) avela futhi angase ahlolwe njengama-mushroom noma abe nesilonda.
- Isibindi sokubomvu (i-erythroderma) esiteji - Ngaphandle kwamagqabhezana nama-tumor, isikhumba somuntu singase sikhule izindawo ezinkulu ezibomvu ezibucayi kakhulu ne-scaly. Izikhumba ebusweni zingase zikhuni, futhi isikhumba sezintende zezandla nemigqa singase sigxume futhi siphume.
- I-lymph node stage - Kulesi sigaba, i-mycosis fungoides iqala ukuthuthela kwezinye izingxenye zomzimba. Izindawo zokuqala ezithintekile yizakhi zamakhansela, ezingaba zivuthayo, futhi ngokuvamile ziba nomdlavuza. Umdlavuza we-MF ungase usakaze nesibindi, amaphaphu, noma umnkantsha wamathambo.
Ukuhlonza Isimo
Lesi simo saziwa nangokuthi i-Alibert-Bazin syndrome noma i-granuloma fungoides.
Ngokujwayelekile, kuneminyaka engaba ngu-6 ubude kusukela ngesikhathi izimpawu ziqala kuze kutholakale ukuthi i-mycosis fungoides ixilongwa. Ngalesi sifo, ukudideka nezinye izimo kuvamile njengoba izigaba zokuqala zesifo ngokuvamile zifana ne-eczema noma i-psoriasis.
Ukuze kutholakale kahle i-mycosis fungoides, isampula yesikhumba singathathwa ( isikhumba se-biopsy ) futhi sihlolwe lesi sifo. Ukuhlolwa kwelabhuzi kungenziwa ukuze kunqume ukuqhubeka komdlavuza.
Ukuze uqonde izigaba ezahlukene zesifo, ukuhlolwa okuhlukahlukene kwenziwa ukuhlola i-lymph nodes, igazi kanye nezitho zangaphakathi. Iningi leziguli libonisa izimpawu ezigcinwe kuphela esikhumbeni, njengama-patches (izindawo eziphambili) nama-plaques (izindawo eziphakanyisiwe noma 'ezinamathele').
Ukwelashwa kwe-MF
Uma i-mycosis fungoides isesiteji sokuqala, ukwelashwa okunjengama-steroid creams, ukwelashwa okulula, ukwelashwa kwamakhemikhali okusetshenziselwa isikhumba, noma imisebe ye-electron ibhaliswe. Umgomo ukubeka umdlavuza weMF ekuxoxweni, okungahlala isikhathi eside.
Uma isifo somuntu singaphenduli ukwelashwa kwesikhumba, noma lesi sifo siphumelele esigabeni sesisu, izindlela zokwelapha ezifana ne-recombinant alfa interferon noma i- chemotherapy zingasetshenziswa. Ngeshwa, akekho ukwelashwa kwe-mycosis fungoides, ngakho-ke isikhathi esiningi umuntu asinda ngayo lesi sifo sincike ekutheni sisakaze kangakanani ngesikhathi sitholwa futhi ukwelashwa kuqala.
Umthombo:
I-Pinter-Brown, i-LC (2002). Mycosis fungoides. eMedicine.