Isifo Sokuzibulala Ngokwemvelo
I-Sjogren's syndrome ebizwa ngokuthi udokotela waseSweden, u-Henrik Sjögren, owathola ekuqaleni kwawo-1900- isifo esizimele , esiyisifo sokuvuvukala esingase sibe njengesimiso sokuqala esingenaso esinye isifo se-rheumatic noma njengesimo sesibili kanye nesinye isimo se-rheumatic. Amaphesenti angaba ngu-50 eSjogren's syndrome kwenzeka njengesimo esisodwa.
Amanye amaphesenti angu-50 we-Sjogren's syndrome kwenzeka njengesimo sesibili, cishe kunesifo samathambo , i-systemic lupus erythematosus, i- scleroderma , i- polymyositis , noma i-dermatomyositis.
Ngokusho kwe-Sjogren's Syndrome Foundation, i-Sjogren's syndrome ingenye yezimo ezivame kakhulu ezizimele futhi kuthinta abaningi abangaba izigidi ezingu-4 baseMelika. Amaphesenti angamashumi ayisishiyagalolunye ama-Sjogren's syndrome abafazi. Isilinganiso seminyaka yokuqala sineminyaka engaphezu kwengu-40 ubudala-kodwa amadoda, abesifazane nabantwana bangathuthukisa isifo se-Sjogren sika kunoma yisiphi ubudala.
Isizathu
Isizathu se-Sjogren's syndrome asiziwa. Ngokusho kwe-American College of Rheumatology, izici zofuzo kanye nezifo ezibangelwa igciwane kungakhuphula ingozi yokuthuthukisa i-syndrome. Amahomori angase abe yisici.
Izimpawu
Ngokusho kwe-Sjogren's Syndrome Foundation, izimpawu zingafaka:
- Amehlo anomile angase abe nomuzwa wokuthokoza noma uvutha
- Umlomo omile
- Kunzima ukuhlafuna, ukugwinya nokukhuluma
- Uphukile noma ukhuluma ulimi olubi
- Omile, ovuthayo umphimbo
- Umehluko ukunambitha noma iphunga
- Ukubola kwamazinyo
- I-Oral imvu yesifo
- Ubuhlungu obuhlangene
- Izinkinga zokugaya
- Ikhala elimile nomkhumbi
- Ukuvuvukala kwama-glands azungeze ubuso
- Ukomisa kwamagagasi
- Ukukhathala
- Ama-lymph nodes ekhulisiwe
Izinkinga ezinzima ezihlobene neSjogren's syndrome zihlanganisa:
- Ukuhlambalaza ngezingalo nemilenze ehlobene ne- vasculitis
- Ukuvuvukala emaphashini, isibindi, nezinso
- Izinkinga ze-neurological ezibangelwa ukunganaki, ukugubha, nokubuthakathaka
- I-Lymphoma inamba encane yeziguli
Ukuxilongwa
Kanye nezibonakaliso, imiphumela yokuhlolwa komzimba kanye nokuhlolwa okuhloswe ngayo ukusiza ukuhlonza isifo sikaSjogren's syndrome. Akukho ukuhlolwa okulodwa okungaqinisekisa ukuthi ukuxilongwa ngokwayo. Izivivinyo ezisiza ukudala ukuxilongwa zibandakanya:
- I-anti-nuclear antibody (ukuhlolwa kwe-ANA) - amaphesenti angu-70 weziguli zika-Sjogren zivivinya i-ANA, kepha i-antibody ingase ibe khona nabantu abanempilo.
- I-SSA (anti-Ro) ne-SSB (anti-La) - Ama-antibodies ngokuvamile atholakala kubantu abane-primary syndrome's syndrome. Akuzona zonke iziguli zikaSjogren ezivivinya nge-SSA ne-SSB.
- Isisindo se-rheumatoid - amaphesenti angama-60 kuya kwangu-70 abantu abathintekayo abane-syndrome kaSjogren anemiphumela emihle yesifo se-rheumatoid.
- Ama-immunoglobulins - Amaprotheni egazi ajwayelekile aphakanyisiwe ku-Sjogren's syndrome.
- Izivivinyo ezikhethekile ze-ophthalmologic noma zamazinyo zingalawulwa ukuhlola ukuma okungavamile noma ezinye izinto ezingavamile. Uvivinyo lungabandakanya: Ukuhlola kukaSchirmer kwamehlo omile (udokotela ubeka amapheshana ephepha ngaphansi kwamajwabu angaphansi aphansi kanye nezinyathelo zokumanzi ephepheni emva kwemizuzu emihlanu); slit ukuhlolwa isibani (eyenziwa ophthalmologist besebenzisa imishini ukukhulisa nokuhlola iso, ukuhlola okomile nokuvuvukala); ukubola ngamadayimenzi abalulekile (ukuhlola umonakalo ebusweni beso); ukuhlolwa komlomo (udokotela uhlola ukungajwayelekile futhi angathola isampula somathele wokuhlola isici); i-lip biopsy (udokotela ususa izinhlayiyana ezincane ezivela emlonyeni ophansi ukuze kuhlolwe amancane).
Ukwelapha
Ukwelashwa kwesifo sikaSjogren sikahluke kumuntu ngamunye, kuye ngokuthi yiziphi izingxenye zomzimba ezithintekayo. Nakuba kungekho ukwelashwa kwe-Sjogren's syndrome, ukuhlanza emanzini, ama-saliva substitutes, sprays, ama-gel, kanye ne-gomamu kunganciphisa izimpawu zomlomo. Imithi kanye nokukhethwa kwezidakamizwa emlonyeni owomile ohlobene neSjogren's syndrome kungase kuhlanganise amathe kanye nama-mucus okuvuselela izidakamizwa, njenge:
- I-Salagen (i-Pilocarpine hydrochloride)
- I-Evoxac (i-Cevimeline HCI)
Izinyembezi zokufakelwa namafutha okugcoba amehlo angasiza ekunciphiseni amehlo anomile angapheli. Imithi kanye nokukhethwa kwezidakamizwa zokwelashwa kweso elomile elihlobene neSjogren's syndrome kungafaka:
- I-Restasis (i-Cyclosporine Ophthalmic Emulsion)
- I-Hydroxypropyl Cellulose (Amaconsi Ezilonda Nama-Pellets)
Izinkinga ezingaphezulu, ezifana nobuhlungu obuhlangene noma ukubandakanya ubuhlungu be-muscle, zivame ukuphathwa nge- NSAID (izidakamizwa ezingezona izifo ezingezona ukuvuvukala). Ukubola, izinso, isitsha segazi, noma izinkinga zesistimu zezinzwa zingaphathwa nge:
- Corticosteroids
- Ama-DMARD (izidakamizwa zokuguqula izifo) noma ama-immunosuppressives
Izwi elivela
Isikhathi esiphezulu kusukela ekuqaleni kwezimpawu ukuxilongwa kwe-Sjogren's syndrome kuthiwa sekuyiminyaka engaphezu kwengu-6. Emva kwakho konke, kunezimbangela eziningi zamehlo owomile nomlomo owomile okudingeka ukhishwe ngaphandle. Amehlo omlomo omile futhi omile yizimpawu ezivame kakhulu ezihlobene neSjogren's syndrome, kodwa izimpawu azizona kuphela. Imithi ethile, ethathwe kwezinye izimo, ingabangela ukomisa. Ngisho nokuphuma esikhathini kuhlotshaniswa nezimpawu zokomisa. Kubalulekile ukuthi ungagxila eziphethweni ngoba unamehlo owomile noma umlomo owomile. Uma unayo lezi zimpawu, bheka udokotela ukuthola ukuhlolwa okuphelele nokuxilongwa. I-Rheumatologists ilawula iziguli ze-Sjogren's syndrome, kuyilapho odokotela bamazinyo nabadokotela bezilwane bangase baphathe izimpawu ezithile. I-Sjogren's syndrome yinkinga ephathekayo. Ngokwelashwa okuphumelelayo, iningi labantu lingaphila kahle.
Sizobe singakhulumi ukukhuluma ngemithi elula yamehlo omile. Blink amehlo akho ukuwahambisa. Blink 5 noma izikhathi 6 ngomzuzu. Vikela amehlo akho kusuka emoyeni nasezingxenyeni. Qiniseka ukuthi usebenzisa i-humidifier ekhaya lakho. Gwema ukubhema, futhi ugweme ukwakheka kweso okungabacasula. Ngokufanayo, kunezeluleko ezivamile zokulawula umlomo owomile. Chew i-sugar free sugar noma ususe on candy hard candy. Sip amanzi emini. Sebenzisa i-lip balm ukuze unciphise izindebe ezomile.
> Imithombo:
> Mayelana neSjogren's Syndrome. I-Sjogren's Syndrome Foundation.
> Imibuzo nezimpendulo Mayelana neSjogren's Syndrome, i-NIAMS, ibuyekezwe ngo-September 2016.
> Udell, James, MD. I-Sjogren's Syndrome. I-American College of Rheumatology. Kubuyekezwe ngoMashi 2017.