Lolu hlobo lwe-Frontotemporal Degeneration Luyaziwa nangokuthi Izifo zikaPickk
Ukungafani komqondo we-frontotemporal (bvFTD) okuhlukile kokuziphatha kuyomunye wezinhlobo eziningana ze-dementias eziwela esigabeni "sokuguga kwangaphambili". Lesi sigaba sithinta cishe ama-50,000 kuya ku-60,000 aseMelika. Njengoba igama libonisa, lolu hlobo lokudemeka kwengqondo luyithinta kakhulu i-lobes yangaphambili neyesimweni sobuchopho. I-dementias ye-frontotemporal ejwayelekile kunazo zonke ziyizinhlobo zokuziphatha ezihlukile.
Ukuguquka komqondo kwangaphambili kwe-frontotemporal ngezinye izikhathi kuthiwa yi- Pick's disease .
Yini Ebangelwa Izifo Zika Pick?
Isifo sika Pick sicatshangwa ukuthi sibangelwa ukuhlanganiswa okungavamile kwamaprotheni we-tau ku-lobes yangaphambili neyesimweni sobuchopho. Lezi ziqhumane zeprotheyini ziyaziwa ngokuthi imizimba ye-Pick. Njengoba zibutha kulezi zinwele, amangqamuzana obuchopho aqala ukufa, okwenza izinguquko ezingokomzwelo, zokuziphatha nezokuqonda ekusebenzeni kwakho.
Izimpawu
Izimpawu ezivame kakhulu ze-bvFTD yizinselele zokuziphatha noma zomzwelo , kuhlanganise nokudla ngokweqile, ukuziphatha ngendlela engavumelani nomzwelo , ukwenza izimpendulo ezingalungile zenhlalo, nokubonisa izingxoxo nezenzo zocansi , kanye nokucasula, ukukhathazeka , ukunganakwa nokuzidla.
Abantu abane-bvFTD bangase babe nobunzima bokugcina umsebenzi, babonise ukwehla kokuhlanzeka kwabo, bagcine izinto ezithile, benze izinqumo ezimbi zezezimali, namalungu omndeni wabangane nabangani ngezimvo zabo ezingacabangi nokuziphatha.
Abanye abantu abane-bvFTD nabo babhekene nezinkinga zokunyakaza ezifana nesifo sikaPasinson , kuhlanganise nokuncipha kwesimo sobuso, ukuqina komfutho, ubuthakathaka nokuqina.
Ngokungafani ne- Alzheimer's , ukulahlekelwa inkumbulo akuvami ukukhula ku-bvFTD, futhi uma kuyenzeka, akuze kube yilesi sifo izigaba zayo kamuva.
Njengomnakekeli, ungase ubone izinkinga zememori, kanye nezinselelo ngokuhlela noma ukunakwa (okuhlobene nokusebenza okuphezulu ).
Nge-bvFTD enzima, ulimi luyabathinteka, okwenza kube nzima ukuxhumana .
Izifo Zama-Pick Zihluke Kanjani Ku-Alzheimer's?
Ukuhluka kwesimo sengqondo se-frontotemporal (Isifo sikaPick) sinezimpawu ezithintekayo ngesifo se-Alzheimer ngoba izifo zombili ziyakuthinta ukuqonda, imizwelo nokuziphatha.Izibonakaliso zangaphambili zesifo sika Pick, noma kunjalo, zihlanganisa ikakhulukazi ushintsho emoyeni, isahlulelo , ukusebenza okuphezulu nokuziphatha, ngenkathi e-Alzheimer's disease, inkumbulo, ukujwayela kanye nokunciphisa ukuxhumana sekuvamile kakhulu ekuqaleni.
Ukuxilongwa
Ukuxilongwa kwe-BvFTD kuvame ukulibaziseka ngoba okokuqala kungacatshangwa ukuthi umuntu othintekile uvele nje ehlukumezayo, egoqela, ecindezelekile noma esebenzayo. Njengoba izimpawu ziqhubeka, noma kunjalo, imindeni ngokuvamile ifuna usizo lomhlengikazi lokuxilongwa nokuphathwa. Ukuxilongwa kuxhomeke ekubeni khona kwezimpawu eziningi ezichazwe ngenhla, kanye nekhono lokulawula enye i-dementias efana ne-Alzheimer's noma i- mental dementia . Ukubukeza izimiso ezisemthethweni zokuziphatha okuhlukile kwe-FTD kungase kube usizo kumalungu omndeni uma i-BvFTD itholakale noma ihlolwe udokotela.
I-MRI ingasiza ekuhloleni i-bvFTD ngoba izovame ukubonisa ezinye i- atrophy (shrinkage) ye- lobe yangaphambili yobuchopho. Njengoba lesi sifo siqhubeka, i-atrophy izokhula futhi isakaze ezindaweni zendawo, kanye ne-basal ganglia.
Ukubikezela nokulindela Ukuphila (I-Long-Term Outlook)
Isilinganiso seminyaka yokuphila kusukela ekuqaleni kwezimpawu cishe iminyaka eyisishiyagalombili kuya kweyisishiyagalolunye, nakuba abanye abantu bangaphila iminyaka engu-20 noma ngaphezulu ngesifo. Njengawo wonke umqondo we-dementia, kungaba yisifo esiyinselele kulabo abanakekeli, kanye nalabo abakutholayo.
Ukwelapha
Ukwelashwa kungase kube nokuzama ukusebenzisa amasu okuziphatha okungewona izidakamizwa ukuvimbela ukuziphatha okuqondile.
Abanye odokotela banikeze izidakamizwa ezibizwa ngokuthi i-serotonin reuptake inhibitors (i-SSRIs) ekhethiwe, engasiza ngamanye okuziphatha okucindezelayo okuphoqeleka njengokugcoba noma ukudla ngokweqile.
Izwi kusuka
Kungokwemvelo ukuzizwa ukhululekile ngezinye izikhathi njengoba ubhekana nezinselelo zokuziphatha okungafani kokucindezeleka kwe-frontotemporal. Yeka isilingo sokuzama ukwenza konke wena; esikhundleni salokho, funa ukusekela kulabo abakuzungezile, kungakhathaliseki ukuthi kusetshenziswa uhlelo lokusekela umphakathi, ingxoxo ye-intanethi mayelana ne-BvFTD noma umngane ozimisele ukukukhipha ikhofi noma uhlale ekhaya nomthandekayo wakho ngenkathi ulala.
Ukwengeza, i-Association for Frontotemporal Dementia ibhala amaqembu asekelayo asekhaya kanye nezinsiza ze-intanethi kanye nomugqa wocingo ozosiza.
Imithombo:
Ama-Annal of Neurology. Ukuguquka nokuguquka kwe-hypothalamus ekuziphatheni komqondo okuphambene nokuziphatha komqondo kwangaphambili. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3084499
Inhlangano ye-Frontotemporal Degeneration. Imikhawulo yokuvumelana yamazwe ngamazwe nge-FTD ehlukile yokuziphatha. http://www.theaftd.org/wp-content/uploads/2009/02/Table-3-International-consensus-criteria-for-behavioural-variant-FTD.pdf
Amabhange, S., Weintraub, S. Journal of Geriatric Psychiatry kanye Neurology. Izimpawu Ze-Neuropsychiatric Ngokuhlukahluka Kwama-Frontotemporal Dementia ne-Primary Aphasia Ehamba phambili .. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2892801/
I-Neurology. Ukuzwela kwezinqubo zamanje zokuxilongwa kokuziphatha kokuhluka komqondo kwangaphambili kwe-frontotemporal. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2821829/
IYunivesithi yaseCalifornia, eSan Francisco. Ukunyuka kwezifo: Ukuhluka okuhlukile kwe-FTD. http://memory.ucsf.edu/ftd/overview/ftd/progression/multiple